دورية أكاديمية

Characteristics of Adult Patients with Idiopathic Retroperitoneal Fibrosis and Assessment of Risk of Relapse at Diagnosis

التفاصيل البيبلوغرافية
العنوان: Characteristics of Adult Patients with Idiopathic Retroperitoneal Fibrosis and Assessment of Risk of Relapse at Diagnosis
المؤلفون: Jerome Razanamahery, Bastien Bouldoires, Sebastien Humbert, Philip Bielefeld, Veronique Fournier, Bernard Bonnotte, Gilles Blaison, Nadine Magy-Bertrand
المصدر: Journal of Clinical Medicine; Volume 10; Issue 7; Pages: 1380
بيانات النشر: Multidisciplinary Digital Publishing Institute
سنة النشر: 2021
المجموعة: MDPI Open Access Publishing
مصطلحات موضوعية: idiopathic retroperitoneal fibrosis, risk of relapse, smoking cessation
الوصف: Objectives: To compare adult patients’ characteristics suffering from idiopathic retroperitoneal fibrosis between “relapse-free” and relapsing patients at the diagnosis and identify factors associated with relapse at initial presentation. Methods: We conducted a retrospective multicentric study in four hospitals in Eastern France, from 1993 to 2020, of adult patients suffering from idiopathic retroperitoneal fibrosis. We analyzed clinical, biological, and radiological features at diagnosis and during a forty-month follow-up. Results: Of 47 patients suffering from retroperitoneal fibrosis, 21 patients had idiopathic retroperitoneal fibrosis. Among them, 13 experienced one or more relapses during follow-up. At diagnosis, clinical characteristics, relevant comorbidities, biological and radiological features were similar between groups. Smoking cessation seems associated with decreased relapse risk (p: 0.0624). A total of 8 patients developed chronic renal failure during follow-up. Ureteral infiltration at diagnosis was associated with evolution to chronic renal failure (p: 0.0091). Conclusion: No clinical, biological, or radiological features could predict relapse at retroperitoneal fibrosis diagnosis, but smoking cessation may prevent relapse.
نوع الوثيقة: text
وصف الملف: application/pdf
اللغة: English
العلاقة: Immunology; https://dx.doi.org/10.3390/jcm10071380Test
DOI: 10.3390/jcm10071380
الإتاحة: https://doi.org/10.3390/jcm10071380Test
حقوق: https://creativecommons.org/licenses/by/4.0Test/
رقم الانضمام: edsbas.28E49206
قاعدة البيانات: BASE