Xanthogranuloma of the sellar region is rare. It typically causes symptoms of pituitary dysfunction or visual change due to compression of the optic chiasm. However, to the best of our knowledge, no case of xanthogranuloma-associated hydrocephalus has been documented in the literature. This study describes a 32-year-old man afflicted with xanthogranuloma of the sellar region who presented with acute change in consciousness and associated obstructive hydrocephalus. A literature review and discussion regarding therapeutic options for this condition are presented.
