Spontaneous Hemopericardium Complicated by Tamponade in a Child With Moderate Hemophilia A: Case-Based Review
| العنوان: | Spontaneous Hemopericardium Complicated by Tamponade in a Child With Moderate Hemophilia A: Case-Based Review |
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| المؤلفون: | Seyfeddine Zayani, Farah Thabet, Majdi Ben Massoud, Chokri Chouchane, Habib Gamra, Slaheddine Chouchane |
| المصدر: | World Journal for Pediatric and Congenital Heart Surgery. :215013512311688 |
| بيانات النشر: | SAGE Publications, 2023. |
| سنة النشر: | 2023 |
| مصطلحات موضوعية: | Pediatrics, Perinatology and Child Health, Surgery, General Medicine, Cardiology and Cardiovascular Medicine |
| الوصف: | Hemophilia A is the most common severe innate bleeding disorder. It is an X-linked recessive inherited bleeding disorder characterized by a qualitative and/or quantitative deficiency of factor VIII. The clinical manifestation of this disease is hemorrhaging that can affect every organ, in particular joints (hemarthrosis) and muscles (hematoma). Some serious but rare hemorrhages can be life-threatening, in particular hemorrhage of the central nervous system and hemopericardium. We report a rare case of spontaneous hemopericardium complicated by tamponade in a child with moderate hemophilia A treated with Factor VIII replacement infusion and pericardial drainage, with a favorable outcome. To our knowledge, this is the second case described in the literature of spontaneous hemopericardium occurring in a child with hemophilia A. Our case suggests that a dose of 50 IU/kg/8 h of factor VIII maintained for up to one day after removal of the pericardial drain seems to be sufficient to ensure correct hemostasis, though further evidence is needed to confirm this impression. |
| تدمد: | 2150-136X 2150-1351 |
| الوصول الحر: | https://explore.openaire.eu/search/publication?articleId=doi_________::0824b0c0fa27ea0ce23d7b913addf542Test https://doi.org/10.1177/21501351231168868Test |
| حقوق: | CLOSED |
| رقم الانضمام: | edsair.doi...........0824b0c0fa27ea0ce23d7b913addf542 |
| قاعدة البيانات: | OpenAIRE |
| تدمد: | 2150136X 21501351 |
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