دورية أكاديمية

BASCULE syndrome: Additional evidence for the association with autonomic dysfunction.

التفاصيل البيبلوغرافية
العنوان: BASCULE syndrome: Additional evidence for the association with autonomic dysfunction.
المؤلفون: Bessis, Didier, Devoye, Céline, Molinari, Nicolas, Quéré, Isabelle, de La Villéon, Grégoire, Jeziorski, Éric
المصدر: Pediatric Dermatology; Mar2024, Vol. 41 Issue 2, p377-378, 2p
مصطلحات موضوعية: ORTHOSTATIC intolerance, DYSAUTONOMIA, POSTURAL orthostatic tachycardia syndrome, SYNDROMES
مستخلص: This article discusses the BASCULE syndrome, a condition characterized by Bier anemic spots, cyanosis, and urticaria-like eruption. The authors conducted a retrospective study of 33 adolescents and adults with BASCULE syndrome, finding a female predominance and a median age of symptom onset at 13 years. The syndrome was triggered by orthostatism and involved the lower limbs and upper limbs. The study also found associations with autonomic dysfunction, including postural orthostatic tachycardia syndrome (POTS) and orthostatic hypotension, as well as electrocardiographic abnormalities. However, no significant clinical improvement was observed with treatment. The authors suggest further research on the potential efficacy of propranolol for BASCULE syndrome. [Extracted from the article]
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قاعدة البيانات: Complementary Index
الوصف
تدمد:07368046
DOI:10.1111/pde.15522