دورية أكاديمية

Pleomorphic dermal sarcoma presenting in a child with Li‐Fraumeni syndrome: A case report and review of the literature.

التفاصيل البيبلوغرافية
العنوان: Pleomorphic dermal sarcoma presenting in a child with Li‐Fraumeni syndrome: A case report and review of the literature.
المؤلفون: Kim, Heeyeon1 (AUTHOR), Noh, Hyungrye1 (AUTHOR), Shim, Joonho1 (AUTHOR), Oh, Se Jin1 (AUTHOR), Lee, Jong Hee1,2 (AUTHOR), Lee, Dong‐Youn1 (AUTHOR), Park, Ji Hye1 (AUTHOR) jh1204.park@samsung.com
المصدر: Pediatric Dermatology. Mar2024, Vol. 41 Issue 2, p311-314. 4p.
مصطلحات موضوعية: *LITERATURE reviews, *LI-Fraumeni syndrome, *SARCOMA, *CHILD patients, *OLDER patients
مستخلص: Pleomorphic dermal sarcoma (PDS) is an uncommon malignant soft‐tissue tumor that occurs mostly in elderly patients, with only 5% of cases occurring in children. However, pediatric patients with Li‐Fraumeni syndrome (LFS) can develop several types of cancer, particularly sarcomas. Here, we describe a young LFS patient who presented with early‐onset PDS and review the literature. [ABSTRACT FROM AUTHOR]
قاعدة البيانات: Academic Search Index
الوصف
تدمد:07368046
DOI:10.1111/pde.15452