المؤلفون: Pérot, Jean-Baptiste, Niewiadomska-Cimicka, Anna, Brouillet, Emmanuel, Trottier, Yvon, Flament, Julien

المساهمون: Laboratoire des Maladies Neurodégénératives - UMR 9199 (LMN), Molecular Imaging Research Center Fontenay-aux-Roses (MIRCEN), Université Paris-Saclay-Centre National de la Recherche Scientifique (CNRS)-Institut de Biologie François JACOB (JACOB), Direction de Recherche Fondamentale (CEA) (DRF (CEA)), Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Direction de Recherche Fondamentale (CEA) (DRF (CEA)), Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Université Paris-Saclay-Centre National de la Recherche Scientifique (CNRS)-Institut de Biologie François JACOB (JACOB), Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Centre National de la Recherche Scientifique (CNRS)

المصدر: ISSN: 1932-6203.

مصطلحات موضوعية: [SDV]Life Sciences [q-bio]

العلاقة: hal-04400325; https://hal.science/hal-04400325Test; https://hal.science/hal-04400325/documentTest; https://hal.science/hal-04400325/file/journal.pone.0296790.pdfTest

الإتاحة: https://doi.org/10.1371/journal.pone.0296790Test
https://hal.science/hal-04400325Test
https://hal.science/hal-04400325/documentTest
https://hal.science/hal-04400325/file/journal.pone.0296790.pdfTest

المؤلفون: Ciancia, Marion, Rataj-Baniowska, Monika, Zinter, Nicolas, Baldassarro, Vito Antonio, Fraulob, Valérie, Charles, Anne-Laure, Alvarez, Rosana, Muramatsu, Shin-Ichi, de Lera, Angel R, Geny, Bernard, Dollé, Pascal, Niewiadomska-Cimicka, Anna, Krężel, Wojciech

المساهمون: Ciancia, Marion, Rataj-Baniowska, Monika, Zinter, Nicola, Baldassarro, Vito Antonio, Fraulob, Valérie, Charles, Anne-Laure, Alvarez, Rosana, Muramatsu, Shin-Ichi, de Lera, Angel R, Geny, Bernard, Dollé, Pascal, Niewiadomska-Cimicka, Anna, Krężel, Wojciech

مصطلحات موضوعية: Huntington’s disease, Medium spiny neuron, Mice models of movement disorder, Mitochondria, Motor behavior, Nuclear hormone receptor, Retinoic acid receptor, Striatum, Animal, Glutamic Acid, Mice, Receptors, Retinoic Acid, Huntington Disease, Neurons

وصف الملف: STAMPA

العلاقة: info:eu-repo/semantics/altIdentifier/pmid/35151792; info:eu-repo/semantics/altIdentifier/wos/WOS:000782349700004; volume:212; firstpage:1; lastpage:20; numberofpages:20; journal:PROGRESS IN NEUROBIOLOGY; https://hdl.handle.net/11585/904832Test; info:eu-repo/semantics/altIdentifier/scopus/2-s2.0-85125265074

الإتاحة: https://doi.org/10.1016/j.pneurobio.2022.102246Test
https://hdl.handle.net/11585/904832Test

المؤلفون: Niewiadomska-Cimicka, Anna¹ (AUTHOR) lorraine.fievet@hotmail.fr, Fievet, Lorraine¹ (AUTHOR) keime@igbmc.fr, Surdyka, Magdalena² (AUTHOR) msurdyka@ibch.poznan.pl, Jesion, Ewelina² (AUTHOR) jesion.ewelina@gmail.com, Keime, Céline¹ (AUTHOR) virly@igbmc.fr, Singer, Elisabeth^3,4,5 (AUTHOR) elisabeth.singer@med.uni-tuebingen.de, Eisenmann, Aurélie¹ (AUTHOR), Kalinowska-Poska, Zaneta² (AUTHOR) zkalinowska@ibch.poznan.pl, Nguyen, Hoa Huu Phuc⁵ (AUTHOR), Fiszer, Agnieszka⁶ (AUTHOR) agnieszka.fiszer@ibch.poznan.pl, Figiel, Maciej² (AUTHOR) mfigiel@ibch.poznan.pl, Trottier, Yvon¹ (AUTHOR) ania.niewiadomska@gmail.com

المصدر: International Journal of Molecular Sciences. Apr2024, Vol. 25 Issue 8, p4354. 21p.

مصطلحات موضوعية: *SPINOCEREBELLAR ataxia, *PHENOTYPES, *LABORATORY mice, *ANIMAL disease models, *SMALL interfering RNA, *CEREBELLAR cortex, *BLOOD-brain barrier

المؤلفون: Niewiadomska-Cimicka, Anna, Hache, Antoine, Le Gras, Stéphanie, Keime, Céline, Ye, Tao, Eisenmann, Aurelie, Harichane, Imen, Roux, Michel, Messaddeq, Nadia, Clérin, Emmanuelle, Léveillard, Thierry, Trottier, Yvon

المساهمون: Institut de Génétique et de Biologie Moléculaire et Cellulaire (IGBMC), Université de Strasbourg (UNISTRA)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Institut de la Vision, Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU)-Centre National de la Recherche Scientifique (CNRS), ANR-18-CE12-0026,SAGA-Retina,Rôle du complexe co-activateur SAGA dans la transcription au cours de la différenciation cellulaire chez les mammifères(2018), ANR-15-JPWG-0008,ModelPolyQ,Advanced models of polyglutamine disorders -HD, SCA2, SCA3, SCA7-(2015), ANR-10-LABX-0030,INRT,Integrative Biology : Nuclear dynamics- Regenerative medicine - Translational medicine(2010), ANR-10-IDEX-0002,UNISTRA,Par-delà les frontières, l'Université de Strasbourg(2010), European Project: 643417,H2020,H2020-HCO-2014,JPco-fuND(2015)

المصدر: ISSN: 1021-7770.

مصطلحات موضوعية: [SDV.BBM.GTP]Life Sciences [q-bio]/Biochemistry, Molecular Biology/Genomics [q-bio.GN], [SDV.NEU.NB]Life Sciences [q-bio]/Neurons and Cognition [q-bio.NC]/Neurobiology, [SDV.MHEP.OS]Life Sciences [q-bio]/Human health and pathology/Sensory Organs

العلاقة: info:eu-repo/grantAgreement//643417/EU/ERA-NET for establishing synergies between the Joint Programming on Neurodegenerative Diseases Research and Horizon 2020/JPco-fuND; hal-03935562; https://hal.science/hal-03935562Test; https://hal.science/hal-03935562/documentTest; https://hal.science/hal-03935562/file/islandora_158686.pdfTest

الإتاحة: https://doi.org/10.1186/s12929-022-00892-1Test
https://hal.science/hal-03935562Test
https://hal.science/hal-03935562/documentTest
https://hal.science/hal-03935562/file/islandora_158686.pdfTest

المؤلفون: Surdyka, Magdalena, Jesion, Ewelina, Niewiadomska-Cimicka, Anna, Trottier, Yvon, Kalinowska-Pośka, Żaneta, Figiel, Maciej

المساهمون: Institute of Bioorganic Chemistry Poznań, Polska Akademia Nauk = Polish Academy of Sciences = Académie polonaise des sciences (PAN), Institut de Génétique et de Biologie Moléculaire et Cellulaire (IGBMC), Université de Strasbourg (UNISTRA)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS)

المصدر: ISSN: 1662-5099 ; Frontiers in Molecular Neuroscience ; https://hal.science/hal-04018712Test ; Frontiers in Molecular Neuroscience, 2022, 15, ⟨10.3389/fnmol.2022.947490⟩.

مصطلحات موضوعية: AAV-PHP.eB, AAVrh10, Purkinje cells, adeno-associated virus (AAV), cerebellum, deep cerebellar nuclei, granule cells, retrograde, [SDV.BBM]Life Sciences [q-bio]/Biochemistry, Molecular Biology

العلاقة: info:eu-repo/semantics/altIdentifier/pmid/36176957; hal-04018712; https://hal.science/hal-04018712Test; https://hal.science/hal-04018712/documentTest; https://hal.science/hal-04018712/file/islandora_160360.pdfTest; PUBMED: 36176957; PUBMEDCENTRAL: PMC9513253

الإتاحة: https://doi.org/10.3389/fnmol.2022.947490Test
https://hal.science/hal-04018712Test
https://hal.science/hal-04018712/documentTest
https://hal.science/hal-04018712/file/islandora_160360.pdfTest

المؤلفون: Pérot, Jean-Baptiste^1,2 (AUTHOR), Niewiadomska-Cimicka, Anna^3,4,5,6 (AUTHOR), Brouillet, Emmanuel¹ (AUTHOR), Trottier, Yvon^3,4,5,6 (AUTHOR), Flament, Julien¹ (AUTHOR) julien.flament@cea.fr

المصدر: PLoS ONE. 1/16/2024, Vol. 19 Issue 1, p1-12. 12p.

مصطلحات موضوعية: *CEREBRAL atrophy, *PROSENCEPHALON, *BRAIN stem, *MAGNETIC resonance imaging, *BRAIN degeneration

المؤلفون: Niewiadomska-Cimicka, Anna, Doussau, Frédéric, Perot, Jean-Baptiste, Roux, Michel, Keime, Celine, Hache, Antoine, Piguet, Françoise, Novati, Ariana, Weber, Chantal, Yalcin, Binnaz, Meziane, Hamid, Champy, Marie-France, Grandgirard, Erwan, Karam, Alice, Messaddeq, Nadia, Eisenmann, Aurélie, Brouillet, Emmanuel, Nguyen, Hoa Huu Phuc, Flament, Julien, Isope, Philippe, Trottier, Yvon

المساهمون: Institut de Génétique et de Biologie Moléculaire et Cellulaire (IGBMC), Université de Strasbourg (UNISTRA)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Institut des Neurosciences Cellulaires et Intégratives (INCI), Université de Strasbourg (UNISTRA)-Centre National de la Recherche Scientifique (CNRS), Commissariat à l'énergie atomique et aux énergies alternatives (CEA), Institute of Medical Genetics and Applied Genomics Tübingen, University of Tübingen, Institut Clinique de la Souris (ICS), ANR-15-JPWG-0008,ModelPolyQ,Advanced models of polyglutamine disorders -HD, SCA2, SCA3, SCA7-(2015), ANR-17-RAR3-0008,TreatPolyQ,Allele-specific lowering of mutant polyQ proteins as treatment for Huntington disease, spinocerebellar ataxia type 3 and spinocerebellar ataxia type 7(2017), ANR-18-CE12-0026,SAGA-Retina,Rôle du complexe co-activateur SAGA dans la transcription au cours de la différenciation cellulaire chez les mammifères(2018), ANR-15-CE37-0001,CeMod,Traitement modulaire de l'information dans le cervelet et mouvements anormaux(2015), ANR-10-LABX-0030,INRT,Integrative Biology : Nuclear dynamics- Regenerative medicine - Translational medicine(2010), ANR-10-IDEX-0002,UNISTRA,Par-delà les frontières, l'Université de Strasbourg(2010), ANR-11-INBS-0011,NeurATRIS,Infrastructure de Recherche Translationnelle pour les Biothérapies en Neurosciences(2011), ANR-10-INBS-0009,France Génomique,Organisation et montée en puissance d'une Infrastructure Nationale de Génomique(2010), European Project: 643417,H2020,H2020-HCO-2014,JPco-fuND(2015)

المصدر: ISSN: 0270-6474.

مصطلحات موضوعية: [SDV.NEU.NB]Life Sciences [q-bio]/Neurons and Cognition [q-bio.NC]/Neurobiology

العلاقة: info:eu-repo/grantAgreement//643417/EU/ERA-NET for establishing synergies between the Joint Programming on Neurodegenerative Diseases Research and Horizon 2020/JPco-fuND; hal-03378998; https://hal.science/hal-03378998Test; https://hal.science/hal-03378998/documentTest; https://hal.science/hal-03378998/file/Version%20soumise%20-%20NiewiadomskaTest-Cimicka%20et%20al.%20-%202021%20-%20SCA7%20Mouse%20Cerebellar%20Pathology%20Reveals%20Preferenti.pdf

الإتاحة: https://doi.org/10.1523/JNEUROSCI.1882-20.2021Test
https://hal.science/hal-03378998Test
https://hal.science/hal-03378998/documentTest
https://hal.science/hal-03378998/file/Version%20soumise%20-%20NiewiadomskaTest-Cimicka%20et%20al.%20-%202021%20-%20SCA7%20Mouse%20Cerebellar%20Pathology%20Reveals%20Preferenti.pdf

المؤلفون: Niewiadomska-Cimicka, Anna, Hache, Antoine, Trottier, Yvon

المساهمون: Institut de Génétique et de Biologie Moléculaire et Cellulaire (IGBMC), Université de Strasbourg (UNISTRA)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), ANR-18-CE12-0026,SAGA-Retina,Rôle du complexe co-activateur SAGA dans la transcription au cours de la différenciation cellulaire chez les mammifères(2018)

المصدر: ISSN: 1662-4548.

مصطلحات موضوعية: polyglutamine, spinocerebellar ataxia, SCA, epigenetic, transcriptional dysregulation, Purkinje cells, [SDV.NEU.NB]Life Sciences [q-bio]/Neurons and Cognition [q-bio.NC]/Neurobiology, [SDV.BBM.GTP]Life Sciences [q-bio]/Biochemistry, Molecular Biology/Genomics [q-bio.GN]

العلاقة: hal-03665604; https://hal.science/hal-03665604Test; https://hal.science/hal-03665604/documentTest; https://hal.science/hal-03665604/file/islandora_151097.pdfTest

الإتاحة: https://doi.org/10.3389/fnins.2020.00571Test
https://hal.science/hal-03665604Test
https://hal.science/hal-03665604/documentTest
https://hal.science/hal-03665604/file/islandora_151097.pdfTest

المؤلفون: Niewiadomska-Cimicka, Anna, Trottier, Yvon

المساهمون: Agence Nationale de la recherche, Fondation pour la Recherche Médicale, Association RETINA-FRANCE, Connaître les Syndrômes Cérébelleux

المصدر: Neurotherapeutics ; volume 16, issue 4, page 1074-1096 ; ISSN 1878-7479

مصطلحات موضوعية: Pharmacology (medical), Neurology (clinical), Pharmacology

الإتاحة: https://doi.org/10.1007/s13311-019-00778-5Test
https://api.elsevier.com/content/article/PII:S1878747923009686?httpAccept=text/xmlTest
https://api.elsevier.com/content/article/PII:S1878747923009686?httpAccept=text/plainTest

المؤلفون: Surdyka, Magdalena, Niewiadomska-Cimicka, Anna, Kalinowska-Poska, Zaneta, Jesion, Ewelina, Singer-Mikosch, Elisabeth, Fievet, Lorraine, Fiszer, Agnieszka, Caron, Nicholas S, Hayden, Michael R, Nguyen, Huu Phuc, Trottier, Yvon, Figiel, Maciej

المصدر: I: Experimental therapeutics – preclinical

الإتاحة: https://doi.org/10.1136/jnnp-2022-ehdn.229Test