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1دورية أكاديمية
المؤلفون: Lijun Zhou, Meng Xie, Xinxin Wang, Renshi Xu
المصدر: Frontiers in Neuroscience, Vol 18 (2024)
مصطلحات موضوعية: amyotrophic lateral sclerosis, animal models, motor neuron degeneration, pathology, pathogenesis, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
العلاقة: https://www.frontiersin.org/articles/10.3389/fnins.2024.1341109/fullTest; https://doaj.org/toc/1662-453XTest
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2دورية أكاديمية
المؤلفون: Hilal Cihankaya, Verian Bader, Konstanze F. Winklhofer, Matthias Vorgerd, Johann Matschke, Sarah Stahlke, Carsten Theiss, Veronika Matschke
المصدر: Cells, Vol 13, Iss 12, p 995 (2024)
مصطلحات موضوعية: amyotrophic lateral sclerosis, motor neuron degeneration, NLRP3 inflammasome, miR-223-3p, pyroptotic cell death, wobbler mouse, Cytology, QH573-671
وصف الملف: electronic resource
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3دورية أكاديمية
المصدر: Proceedings of the National Academy of Sciences of the United States of America. 118(39)
مصطلحات موضوعية: Genetics, Neurosciences, Aetiology, 2.1 Biological and endogenous factors, Neurological, Animals, Cerebellar Diseases, Disease Models, Animal, Female, Gene Expression Regulation, Male, Mice, Mice, Inbred C57BL, Mice, Knockout, Mutation, Neurodegenerative Diseases, Polyadenylation, RNA Precursors, RNA Processing, Post-Transcriptional, RNA, Messenger, RNA, Transfer, RNA-Binding Proteins, Transcription Factors, motor neuron degeneration, tRNA splicing, clevage factor II, deep cerebellar nuclei, alternative polyadenylation, cleavage factor II
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/7md9m52rTest
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4دورية أكاديمية
المؤلفون: Ting-Jung Lin, Kuang-Chao Cheng, Luo-Yun Wu, Wei-Yu Lai, Thai-Yen Ling, Yung-Che Kuo, Yen-Hua Huang
المصدر: Frontiers in Cell and Developmental Biology, Vol 11 (2023)
مصطلحات موضوعية: ALS, mesenchymal stem cell, motor neuron degeneration, precision medicine, cellular therapy, Biology (General), QH301-705.5
وصف الملف: electronic resource
العلاقة: https://www.frontiersin.org/articles/10.3389/fcell.2023.1292681/fullTest; https://doaj.org/toc/2296-634XTest
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5دورية أكاديمية
المؤلفون: Huang, Shih-Ling, Wu, Lien-Szu, Lee, Min, Chang, Chin-Wen, Cheng, Wei-Cheng, Fang, Yu-Sheng, Chen, Yun-Ru, Cheng, Pei-Lin, Shen, Che-Kun James
المصدر: Acta Neuropathologica Communications. 8(1)
مصطلحات موضوعية: Biological Sciences, Biomedical and Clinical Sciences, Neurosciences, Genetics, Rare Diseases, Stem Cell Research, Brain Disorders, Neurodegenerative, ALS, 2.1 Biological and endogenous factors, Aetiology, Neurological, Amyotrophic Lateral Sclerosis, Animals, Autophagy, Cell Line, DNA-Binding Proteins, Disease Models, Animal, Embryonic Stem Cells, Female, Gene Knock-In Techniques, Male, Mice, Transgenic, Motor Neurons, Muscle, Skeletal, Protein Aggregation, Pathological, Spinal Cord, ALS-TDP pathogenesis, Amyotrophic lateral sclerosis, Autonomous spinal cord motor neuron degeneration, Homologous knock-in mouse models with ALS-associated TDP-43 mutations, Mis-splicing of Bcl-2 pre-mRNA, TAR DNA-binding protein 43, Biochemistry and Cell Biology, Clinical Sciences, Biochemistry and cell biology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/2732x3nvTest
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6دورية أكاديمية
المؤلفون: Teresa Cunha-Oliveira, Liliana Montezinho, Rui F. Simões, Marcelo Carvalho, Elisabete Ferreiro, Filomena S. G. Silva
المصدر: Cells, Vol 13, Iss 3, p 248 (2024)
مصطلحات موضوعية: amyotrophic lateral sclerosis, mitochondrial dysfunction, neurodegeneration, pathological mechanisms, motor neuron degeneration, mitochondria-targeted therapies, Cytology, QH573-671
وصف الملف: electronic resource
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7دورية أكاديمية
المؤلفون: Franco Espín, Julio, Gatius, Alaó, Armengol, José Ángel, Arumugam, Saravanan, Moradi, Mehri, Sendtner, Michael, Calderó, Jordi, Tabares, Lucía
المساهمون: Universidad de Sevilla. Departamento de Fisiología Médica y Biofísica, Agencia Estatal de Investigación. España, Ministerio de Ciencia e Innovacion, European Commission (EC). Fondo Europeo de Desarrollo Regional (FEDER), TV3 Foundation, Deutsche Forschungsgemeinschaft / German Research Foundation (DFG)
مصطلحات موضوعية: spinal muscular atrophy, motor neuron degeneration, SMN granules, neuromuscular junction, β-actin mRNA, MAP1B, neurofilaments
وصف الملف: application/pdf
العلاقة: Biomolecules, 12 (10), 1524.; PID2019-110272RB-100/AEI/10.13039/501100011033; PID2021-122785OB-I00; 202005; Se 697/7-1; https://www.mdpi.com/2218-273X/12/10/1524Test; https://idus.us.es/handle//11441/145418Test
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8دورية أكاديمية
المؤلفون: Sansa Zaragoza, Alba, Miralles, Maria P., Beltran Perelló, Maria, Celma Nos, Ferran, Calderó i Pardo, Jordi, Garcera, Ana, Soler i Tatché, Rosa Ma.
مصطلحات موضوعية: Spinal muscular atrophy, Motor neuron degeneration, ERK, MAPK, Autophagy
وصف الملف: application/pdf
العلاقة: info:eu-repo/grantAgreement/AEI/Plan Estatal de Investigación Científica, Técnica y de Innovación 2021-2023/PID2021-122785OB-I00/ES/; Reproducció del document publicat a: https://doi.org/10.1038/s41420-023-01409-xTest; Cell Death Discovery, 2023, vol. 9, num. 113; https://doi.org/10.1038/s41420-023-01409-xTest; https://repositori.udl.cat/handle/10459.1/463354Test
الإتاحة: https://doi.org/10.1038/s41420-023-01409-xTest
https://repositori.udl.cat/handle/10459.1/463354Test -
9دورية أكاديمية
المؤلفون: Nicolas James Ho, Xiao Chen, Yong Lei, Shen Gu
المصدر: Zoological Research, Vol 44, Iss 3, Pp 650-662 (2023)
مصطلحات موضوعية: hereditary spastic paraplegia, motor neuron degeneration, disease pathogenicity, transcriptome analysis, single-cell rna sequencing, Zoology, QL1-991
العلاقة: http://www.zoores.ac.cn/EN/10.24272/j.issn.2095-8137.2022.281Test; https://doaj.org/toc/2095-8137Test; https://doaj.org/article/ae0aaba3673342ed96221137a82b5c4fTest
الإتاحة: https://doi.org/10.24272/j.issn.2095-8137.2022.281Test
https://doaj.org/article/ae0aaba3673342ed96221137a82b5c4fTest -
10دورية أكاديمية
المؤلفون: Bridget Martinez, Philip V Peplow
المصدر: Neural Regeneration Research, Vol 17, Iss 4, Pp 728-740 (2022)
مصطلحات موضوعية: amyotrophic lateral sclerosis, animal model, brain, brainstem, microrna, motor neuron degeneration, spinal cord, therapeutic approaches, Neurology. Diseases of the nervous system, RC346-429
وصف الملف: electronic resource
العلاقة: http://www.nrronline.org/article.asp?issn=1673-5374;year=2022;volume=17;issue=4;spage=728;epage=740;aulastTest=; https://doaj.org/toc/1673-5374Test