دورية أكاديمية
Envolvimento pulmonar na síndrome de Sweet paraneoplásica Pulmonary involvement in paraneoplastic Sweet's syndrome
العنوان: | Envolvimento pulmonar na síndrome de Sweet paraneoplásica Pulmonary involvement in paraneoplastic Sweet's syndrome |
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المؤلفون: | Marcelo Pavesi, Chiara S. Tessmer, Victor M. B. Garcia Neto, Jean Carlo Miller, Gilca Natchigal, Hiram L. Almeida Júnior |
المصدر: | Revista Brasileira de Hematologia e Hemoterapia, Vol 28, Iss 4, Pp 307-309 (2006) |
بيانات النشر: | Elsevier, 2006. |
سنة النشر: | 2006 |
المجموعة: | LCC:Diseases of the blood and blood-forming organs |
مصطلحات موضوعية: | Síndrome de Sweet, acometimento pulmonar, dermatose neutrofílica febril aguda, Sweet's syndrome, pulmonary involvement, acute febrile neutrophilic dermatosis, Diseases of the blood and blood-forming organs, RC633-647.5 |
الوصف: | Síndrome de Sweet (dermatose neutrofílica febril aguda) é caracterizada por lesões cutâneas inflamatórias acompanhadas por febre, leucocitose e mal-estar, devendo ser reconhecida por hematologistas, já que freqüentemente é paraneoplásica. O envolvimento sistêmico pode estar presente e o comprometimento pulmonar, apesar de raro, tem sido reportado na forma de infiltração pulmonar bilateral, bronquiolite obliterante e derrame pleural. Há infiltração neutrofílica densa na histologia. Apresentamos o caso de uma paciente com leucemia mielóide crônica que desenvolveu a síndrome de Sweet com infiltrações pulmonares não infecciosas, as quais não foram responsivas à antibioticoterapia, porém mostraram melhora clínica com a corticoterapia.Sweet's syndrome (acute febrile neutrophilic dermatosis) is characterized by inflammatory skin lesions accompanied by fever, leukocytosis and malaise, it should be recognized by hematologists, because it can be a paraneoplastic manifestation. Systemic involvement may be present and lung lesions, despite of the rarity, have been reported in the form of bilateral pulmonary infiltrations, bronchiolitis obliterans and pleural effusion. Histopathology shows dense neutrophilic infiltrates. We present a patient with chronic myeloid leukemia who developed Sweet's syndrome with bilateral pulmonary infiltrations, which were non-responsive to antibiotics but showed clinical improvement on steroid therapy. |
نوع الوثيقة: | article |
وصف الملف: | electronic resource |
اللغة: | English |
تدمد: | 1516-8484 1806-0870 |
العلاقة: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842006000400019Test; https://doaj.org/toc/1516-8484Test; https://doaj.org/toc/1806-0870Test |
DOI: | 10.1590/S1516-84842006000400019 |
الوصول الحر: | https://doaj.org/article/7ffa254c0cda4dbda1c3ac96ee93edd7Test |
رقم الانضمام: | edsdoj.7ffa254c0cda4dbda1c3ac96ee93edd7 |
قاعدة البيانات: | Directory of Open Access Journals |
تدمد: | 15168484 18060870 |
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DOI: | 10.1590/S1516-84842006000400019 |