دورية أكاديمية

Envolvimento pulmonar na síndrome de Sweet paraneoplásica Pulmonary involvement in paraneoplastic Sweet's syndrome

التفاصيل البيبلوغرافية
العنوان: Envolvimento pulmonar na síndrome de Sweet paraneoplásica Pulmonary involvement in paraneoplastic Sweet's syndrome
المؤلفون: Marcelo Pavesi, Chiara S. Tessmer, Victor M. B. Garcia Neto, Jean Carlo Miller, Gilca Natchigal, Hiram L. Almeida Júnior
المصدر: Revista Brasileira de Hematologia e Hemoterapia, Vol 28, Iss 4, Pp 307-309 (2006)
بيانات النشر: Elsevier, 2006.
سنة النشر: 2006
المجموعة: LCC:Diseases of the blood and blood-forming organs
مصطلحات موضوعية: Síndrome de Sweet, acometimento pulmonar, dermatose neutrofílica febril aguda, Sweet's syndrome, pulmonary involvement, acute febrile neutrophilic dermatosis, Diseases of the blood and blood-forming organs, RC633-647.5
الوصف: Síndrome de Sweet (dermatose neutrofílica febril aguda) é caracterizada por lesões cutâneas inflamatórias acompanhadas por febre, leucocitose e mal-estar, devendo ser reconhecida por hematologistas, já que freqüentemente é paraneoplásica. O envolvimento sistêmico pode estar presente e o comprometimento pulmonar, apesar de raro, tem sido reportado na forma de infiltração pulmonar bilateral, bronquiolite obliterante e derrame pleural. Há infiltração neutrofílica densa na histologia. Apresentamos o caso de uma paciente com leucemia mielóide crônica que desenvolveu a síndrome de Sweet com infiltrações pulmonares não infecciosas, as quais não foram responsivas à antibioticoterapia, porém mostraram melhora clínica com a corticoterapia.Sweet's syndrome (acute febrile neutrophilic dermatosis) is characterized by inflammatory skin lesions accompanied by fever, leukocytosis and malaise, it should be recognized by hematologists, because it can be a paraneoplastic manifestation. Systemic involvement may be present and lung lesions, despite of the rarity, have been reported in the form of bilateral pulmonary infiltrations, bronchiolitis obliterans and pleural effusion. Histopathology shows dense neutrophilic infiltrates. We present a patient with chronic myeloid leukemia who developed Sweet's syndrome with bilateral pulmonary infiltrations, which were non-responsive to antibiotics but showed clinical improvement on steroid therapy.
نوع الوثيقة: article
وصف الملف: electronic resource
اللغة: English
تدمد: 1516-8484
1806-0870
العلاقة: http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842006000400019Test; https://doaj.org/toc/1516-8484Test; https://doaj.org/toc/1806-0870Test
DOI: 10.1590/S1516-84842006000400019
الوصول الحر: https://doaj.org/article/7ffa254c0cda4dbda1c3ac96ee93edd7Test
رقم الانضمام: edsdoj.7ffa254c0cda4dbda1c3ac96ee93edd7
قاعدة البيانات: Directory of Open Access Journals
الوصف
تدمد:15168484
18060870
DOI:10.1590/S1516-84842006000400019