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1دورية أكاديمية
المؤلفون: Lucile Hoch, Nathalie Bourg, Fanny Degrugillier, Céline Bruge, Manon Benabides, Emilie Pellier, Johana Tournois, Gurvan Mahé, Nicolas Maignan, Jack Dawe, Maxime Georges, David Papazian, Nik Subramanian, Stéphanie Simon, Pascale Fanen, Cédric Delevoye, Isabelle Richard, Xavier Nissan
المصدر: Frontiers in Pharmacology, Vol 13 (2022)
مصطلحات موضوعية: misfolded protein, drug repurposing, givinostat, HDAC inhibitor, autophagy, Therapeutics. Pharmacology, RM1-950
وصف الملف: electronic resource
العلاقة: https://www.frontiersin.org/articles/10.3389/fphar.2022.856804/fullTest; https://doaj.org/toc/1663-9812Test
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2دورية أكاديمية
المؤلفون: Fanny Degrugillier, Stéphanie Simon, Abdel Aissat, Natascha Remus, Chadia Mekki, Xavier Decrouy, Aurélie Hatton, Alexandre Hinzpeter, Brice Hoffmann, Isabelle Sermet‐Gaudelus, Isabelle Callebaut, Pascale Fanen, Virginie Prulière‐Escabasse
المصدر: Clinical Case Reports, Vol 7, Iss 11, Pp 2128-2134 (2019)
مصطلحات موضوعية: CFTR, chronic rhinosinusitis, cystic fibrosis, functional studies, Medicine, Medicine (General), R5-920
وصف الملف: electronic resource
العلاقة: https://doaj.org/toc/2050-0904Test
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3دورية أكاديمية
المؤلفون: Stéphanie Simon, Abdel Aissat, Fanny Degrugillier, Benjamin Simonneau, Pascale Fanen, André-Patrick Arrigo
المصدر: International Journal of Molecular Sciences, Vol 22, Iss 8, p 4252 (2021)
مصطلحات موضوعية: cystic fibrosis, CFTR, sHsps, HspB1, HspB4, HspB5, Biology (General), QH301-705.5, Chemistry, QD1-999
وصف الملف: electronic resource
العلاقة: https://www.mdpi.com/1422-0067/22/8/4252Test; https://doaj.org/toc/1661-6596Test; https://doaj.org/toc/1422-0067Test
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4دورية أكاديمية
المؤلفون: Fanny Degrugillier, Abdel Aissat, Virginie Prulière-Escabasse, Lucie Bizard, Benjamin Simonneau, Xavier Decrouy, Chong Jiang, Daniela Rotin, Pascale Fanen, Stéphanie Simon
المصدر: International Journal of Molecular Sciences, Vol 21, Iss 14, p 4844 (2020)
مصطلحات موضوعية: cystic fibrosis, CFTR, HspB5, alpha B-crystallin, CRYAB, phosphorylation, Biology (General), QH301-705.5, Chemistry, QD1-999
وصف الملف: electronic resource
العلاقة: https://www.mdpi.com/1422-0067/21/14/4844Test; https://doaj.org/toc/1661-6596Test; https://doaj.org/toc/1422-0067Test
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5
المؤلفون: Lucile Hoch, Nathalie Bourg, Fanny Degrugillier, Céline Bruge, Manon Benabides, Emilie Pellier, Johana Tournois, Gurvan Mahe, Nicolas Maignan, Jack Dawe, Maxime Georges, David Papazian, Nik Subramanian, Stéphanie Simon, Pascale Fanen, Cédric Delevoye, Isabelle Richard, Xavier Nissan
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_________::5146663409df1ffa0518c68f53590e2bTest
https://doi.org/10.22541/au.163956865.51404833/v1Test -
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المؤلفون: Aurélie Hatton, Isabelle Callebaut, Xavier Decrouy, Stéphanie Simon, Chadia Mekki, Natascha Remus, Abdel Aissat, Fanny Degrugillier, Brice Hoffmann, Alexandre Hinzpeter, Isabelle Sermet-Gaudelus, Pascale Fanen, Virginie Prulière-Escabasse
المصدر: Clinical Case Reports
Clinical Case Reports, Vol 7, Iss 11, Pp 2128-2134 (2019)مصطلحات موضوعية: congenital, hereditary, and neonatal diseases and abnormalities, Chronic rhinosinusitis, lcsh:Medicine, Pulmonary infection, Case Report, macromolecular substances, Case Reports, 030204 cardiovascular system & hematology, Cystic fibrosis, cystic fibrosis, 03 medical and health sciences, 0302 clinical medicine, Rare mutations, Medicine, Functional studies, CFTR, Genotyping, lcsh:R5-920, business.industry, chronic rhinosinusitis, lcsh:R, General Medicine, respiratory system, medicine.disease, 030220 oncology & carcinogenesis, Immunology, functional studies, lcsh:Medicine (General), business
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::93d4433a8202d90eb53d8c930323c04bTest
http://europepmc.org/articles/PMC6878083Test -
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المؤلفون: Pascale Fanen, Stéphanie Simon, Abdel Aissat, Fanny Degrugillier, Benjamin Simonneau, Xavier Decrouy, Chong Jiang, Lucie Bizard, Virginie Prulière-Escabasse, Daniela Rotin
المساهمون: Institut Mondor de Recherche Biomédicale (IMRB), Institut National de la Santé et de la Recherche Médicale (INSERM)-IFR10-Université Paris-Est Créteil Val-de-Marne - Paris 12 (UPEC UP12), Hôpital Henri Mondor, Service d'ORL [Créteil], Centre Hospitalier Intercommunal de Créteil (CHIC), The Hospital for sick children [Toronto] (SickKids), Simon, Stéphanie, Institut National de la Santé et de la Recherche Médicale (INSERM)-Université Paris-Est Créteil Val-de-Marne - Paris 12 (UPEC UP12)-IFR10
المصدر: International Journal of Molecular Sciences
International Journal of Molecular Sciences, MDPI, 2020, 21 (14), pp.4844. ⟨10.3390/ijms21144844⟩
International Journal of Molecular Sciences, Vol 21, Iss 4844, p 4844 (2020)
Volume 21
Issue 14مصطلحات موضوعية: Male, phosphorylation, [SDV]Life Sciences [q-bio], CRYAB, Aminopyridines, Cystic Fibrosis Transmembrane Conductance Regulator, Quinolones, Aminophenols, Cystic fibrosis, Ivacaftor, lcsh:Chemistry, cystic fibrosis, Mice, 0302 clinical medicine, CFTR, lcsh:QH301-705.5, Heat-Shock Proteins, Spectroscopy, 0303 health sciences, biology, Chemistry, General Medicine, Cystic fibrosis transmembrane conductance regulator, 3. Good health, Computer Science Applications, Cell biology, [SDV] Life Sciences [q-bio], Drug Combinations, Protein Transport, 030220 oncology & carcinogenesis, HspB5, Phosphorylation, medicine.drug, Proteasome Endopeptidase Complex, congenital, hereditary, and neonatal diseases and abnormalities, Phenylalanine, Article, Catalysis, Cell Line, Inorganic Chemistry, 03 medical and health sciences, alpha B-crystallin, Heat shock protein, medicine, Animals, Humans, Benzodioxoles, Physical and Theoretical Chemistry, Molecular Biology, 030304 developmental biology, Endoplasmic reticulum, Cell Membrane, Organic Chemistry, medicine.disease, Crystallins, HEK293 Cells, Proteasome, lcsh:Biology (General), lcsh:QD1-999, Chaperone (protein), Mutation, biology.protein, Molecular Chaperones
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::30bf87afa4aa91a5e13ad3449ad99f86Test
https://www.hal.inserm.fr/inserm-03235062/documentTest -
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المؤلفون: Fanny Degrugillier
المساهمون: Institut Mondor de Recherche Biomédicale (IMRB), Institut National de la Santé et de la Recherche Médicale (INSERM)-IFR10-Université Paris-Est Créteil Val-de-Marne - Paris 12 (UPEC UP12), Université Paris-Est, Pascale Fanen, STAR, ABES
المصدر: Médecine humaine et pathologie. Université Paris-Est, 2019. Français. ⟨NNT : 2019PESC0068⟩
HALمصطلحات موضوعية: [SDV.MHEP] Life Sciences [q-bio]/Human health and pathology, Cystic Fibrosis, HspB5, Cftr, F508del mutation, Small Heat Shock Proteins, Petites Protéines de Choc Thermiques / de Stress, Mucoviscidose, Mutation F508del, [SDV.MHEP]Life Sciences [q-bio]/Human health and pathology
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=dedup_wf_001::ca5057c8f5b09682ceeea25c86537751Test
https://tel.archives-ouvertes.fr/tel-03441507/file/TH2019PESC0068.pdfTest -
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المؤلفون: Stéphanie Simon, Xavier Decrouy, Chong Jiang, Daniela Rotin, Virginie Prulière-Escabasse, Pascale Fanen, Fanny Degrugillier
المصدر: Cystic fibrosis.
مصطلحات موضوعية: Pathology, medicine.medical_specialty, business.industry, medicine, medicine.disease, business, Cystic fibrosis
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_________::ca6d156a65267eda30f4fb4298501c7dTest
https://doi.org/10.1183/13993003.congress-2018.pa3421Test