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المؤلفون: Margarita Gerou, Benjamin A. Hall, Scott P. Allen, Kathrin Meyer, Pamela J. Shaw, Ryan Woof, Jessica Allsop, Stephen J. Kolb
المصدر: Neurobiology of Aging
مصطلحات موضوعية: 0301 basic medicine, Male, Aging, AGEs, advanced glycation end products, SOD1, superoxide dismutase 1, DHAP, dihydroxyacetone phosphate, chemistry.chemical_compound, 0302 clinical medicine, FALS, familial amyotrophic lateral sclerosis, PGM, phosphoglucomutase, Glycolysis, Amyotrophic lateral sclerosis, SALS, sporadic amyotrophic lateral sclerosis, Glycogen, General Neuroscience, Middle Aged, ALS, amyotrophic lateral sclerosis, Aging, ALS, iNPC, induced neuronal progenitor cell, Disease Progression, Ketoglutaric Acids, Female, medicine.drug, Adult, medicine.medical_specialty, C9ORF72, chromosome 9 open reading frame 72, ETC, electron transport chain, Citric Acid Cycle, TCA, tricarboxylic acid, Context (language use), Biology, Article, 03 medical and health sciences, iPSC, induced pluripotent stem cells, ROS, reactive oxygen species, Internal medicine, medicine, Humans, LDHA, lactate dehydrogenase A, Progenitor cell, Inosine, Aged, G3P, glyceraldehyde 3-phosphate, GP, glycogen phosphorylase, NADH, nicotinamide adenine dinucleotide, reduced form, Amyotrophic Lateral Sclerosis, ChREBP, carbohydrate response element binding protein, Metabolism, Fibroblasts, iAstrocytes, induced astrocytes, medicine.disease, NAD, mtDNA, mitochondrial DNA, AMPK, AMP-activated protein kinase, 030104 developmental biology, Endocrinology, chemistry, Neurology (clinical), Geriatrics and Gerontology, Age of onset, TDP-43, TAR DNA-binding protein 43, Energy Metabolism, 030217 neurology & neurosurgery, Developmental Biology
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::fa322bad33369b41380c3947538e1343Test
http://europepmc.org/articles/PMC8346650Test -
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المؤلفون: Peter, St George-Hyslop, Julie Qiaojin, Lin, Akinori, Miyashita, Emma C, Phillips, Seema, Qamar, Suzanne J, Randle, GuoZhen, Wang
المصدر: Brain Research
مصطلحات موضوعية: PY-NLS, proline tyrosine nuclear localisation signal, PTM, post-translational modification, TNPO1, transportin 1/karyopherin β2, Biophysics, TAF15, TATA box binding protein 15, Phase separation, SMN, survival motor neuron, fALS, familial amyotrophic lateral sclerosis, Cytoplasmic Granules, Article, FUS, fused in sarcoma protein, Protein Domains, RRM, RNA recognition Motif, FTLD, frontotemporal lobar degeneration, Arginine methylation, Humans, QGSY, glutamine glycine serine and tyrosine repeats motif, DDX4, DEAD box helicase 4, RGG, arginine glycine glycine repeat motif, CHOP, C/EBP homologous protein gene, Cation-pi interactions, EWS, Ewing sarcoma protein, ComputingMethodologies_COMPUTERGRAPHICS, Amyotrophic Lateral Sclerosis, RNA-Binding Proteins, Neurodegenerative Diseases, Temporal Lobe, DNA-Binding Proteins, Frontotemporal Dementia, Mutation, hnRNP, heterogeneous nuclear ribonucleoprotein, RNA-Binding Protein FUS, ADMA FUS, asymmetrically di-methylated arginine FUS, TDP-43, transactive response DNA binding protein 43, RNA binding proteins, Frontotemporal Lobar Degeneration, Protein Processing, Post-Translational
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=pmid________::d7c33cdb5ca19f9cf1f4a371dcd4e851Test
https://pubmed.ncbi.nlm.nih.gov/29723523Test -
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المؤلفون: Naoyuki Taniguchi, Noriko Fujiwara, Yoshiki Yamaguchi, Keiichiro Suzuki, Hidetaka Torigoe, Soichi Wakatsuki, Kentaro Ihara
المصدر: Bioscience Reports
Bioscience Reports, Vol 32, Iss 6 (2012)مصطلحات موضوعية: Models, Molecular, amyotrophic lateral sclerosis (ALS), Alkylation, Protein Conformation, Dimer, 2-ME, 2-mercaptoethanol, lcsh:Life, lcsh:QR1-502, SOD1, superoxide dismutase 1, Crystallography, X-Ray, Biochemistry, lcsh:Microbiology, Protein Structure, Secondary, chemistry.chemical_compound, Protein structure, Superoxide Dismutase-1, superoxide dismutase 1 (SOD1), FALS, familial amyotrophic lateral sclerosis, PDB, protein data bank, biology, Hydrogen bond, Protein Stability, computer.file_format, ALS, amyotrophic lateral sclerosis, Protein folding, Oxidation-Reduction, crystal structure, Stereochemistry, SOD1, Biophysics, S2, Superoxide dismutase, Humans, Amino Acid Sequence, Cysteine, Molecular Biology, Mercaptoethanol, Original Paper, Superoxide Dismutase, asymmetric configuration, Amyotrophic Lateral Sclerosis, Hydrogen Bonding, Cell Biology, Protein Data Bank, WT, wild-type, lcsh:QH501-531, chemistry, biology.protein, Protein Multimerization, computer, Sequence Alignment
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d4f8b02545d12a056f9d7501444ec093Test
http://europepmc.org/articles/PMC3497728Test -
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المؤلفون: Sabate R, Rousseau F, Schymkowitz J, Batlle C, Ventura S
المصدر: Prion
r-FSJD. Repositorio Institucional de Producción Científica de la Fundació Sant Joan de Déu
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r-FSJD: Repositorio Institucional de Producción Científica de la Fundació Sant Joan de Déu
Fundació Sant Joan de Déuمصطلحات موضوعية: PFD, prion forming domain, CJD, Creutzfeldt-Jakob disease, TSE, transmissible spongiform encephalopathy, neurodegenerative diseases, AD, Alzheimer's disease, Q/N-rich domains, amyloids, fALS, familial amyotrophic lateral sclerosis, prions, yeast, protein intrinsic disorder, PD, Parkinson's disease
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=dedup_wf_001::241d23df4b619a9cf1d0b23103318fecTest
http://fundanet.fsjd.org/Publicaciones/ProdCientif/PublicacionFrw.aspx?id=18905Test -
5دورية أكاديميةBioenergetic Defects and Oxidative Damage in Transgenic Mouse Models of Neurodegenerative Disorders.
المؤلفون: Brown, Susan
المساهمون: MASSACHUSETTS GENERAL HOSPITAL BOSTON
المصدر: DTIC AND NTIS
مصطلحات موضوعية: Anatomy and Physiology, Medicine and Medical Research, OXIDATION, ETIOLOGY, NERVE CELLS, NEUROLOGY, CEREBRAL CORTEX, CEREBELLUM, STRESSES, DAMAGE, ENZYMES, AGING(PHYSIOLOGY), METABOLISM, DEOXYRIBONUCLEIC ACIDS, MUTATIONS, PATHOLOGY, MICE, IN VIVO ANALYSIS, UTILIZATION, WILDLIFE, ASSAYING, GLUCOSE, SPINAL CORD, CEREBRUM, NEUROTOXINS, SPECTROPHOTOMETRY, &HUNTINGTON'S DISEASE, BIOENERGETIC DYSFUNCTION, HE(HUNTINGTON'S DISEASE), FALS(FAMILIAL AMYOTROPHIC LATERAL SCLEROSIS)
وصف الملف: text/html
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6مورد إلكترونيBioenergetic Defects and Oxidative Damage in Transgenic Mouse Models of Neurodegenerative Disorders.
المصدر: DTIC AND NTIS
مصطلحات الفهرس: Anatomy and Physiology, Medicine and Medical Research, OXIDATION, ETIOLOGY, NERVE CELLS, NEUROLOGY, CEREBRAL CORTEX, CEREBELLUM, STRESSES, DAMAGE, ENZYMES, AGING(PHYSIOLOGY), METABOLISM, DEOXYRIBONUCLEIC ACIDS, MUTATIONS, PATHOLOGY, MICE, IN VIVO ANALYSIS, UTILIZATION, WILDLIFE, ASSAYING, GLUCOSE, SPINAL CORD, CEREBRUM, NEUROTOXINS, SPECTROPHOTOMETRY., &HUNTINGTON'S DISEASE, BIOENERGETIC DYSFUNCTION, HE(HUNTINGTON'S DISEASE), FALS(FAMILIAL AMYOTROPHIC LATERAL SCLEROSIS), NEURODEGENERATION, Text
