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1
المؤلفون: Sara Lopes, Thorsten Schmidt, Clévio Nóbrega, Miguel Monteiro Lopes, Dineke S. Verbeek, Diana Lobo, Dina Pereira, Ana Vasconcelos-Ferreira, Luís Pereira de Almeida, Inês Morgado Martins, Rosário Faro
المساهمون: Movement Disorder (MD), Molecular Neuroscience and Ageing Research (MOLAR)
المصدر: Molecular Therapy, 30(1), 370-387. CELL PRESS
Mol Therمصطلحات موضوعية: congenital, hereditary, and neonatal diseases and abnormalities, Ataxia, Intranuclear Inclusions, Neuropathology, Mutant Huntingt, Biology, Neuroprotection, Mice, Cerebellar-Aaxiagene-Productcell-Lines, Drug Discovery, Genetics, medicine, Transcriptional regulation, Nuclear-Localization, Autophagy, Animals, Ataxin-3, Molecular Biology, Pharmacology, ULK2, Machado-Joseph Disease, ULK1, Dependovirus, medicine.disease, Cell biology, Disease Models, Animal, Molecular Medicine, Original Article, Polyglutamine-Expanded Ataxin-3, Rat Modelin-Vitro, medicine.symptom, Machado–Joseph disease
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::b6624ead970bd32025df3f2fed67eab6Test
https://hdl.handle.net/11370/6e7d478b-8917-4de9-ba98-76e5ef115fc2Test -
2دورية أكاديمية
المؤلفون: Matos, C, Nóbrega, C, Louros, S, Almeida, B, Ferreiro, E, Valero, J, Almeida, L, Macedo-Ribeiro, S, Carvalho, A
المساهمون: Instituto de Investigação e Inovação em Saúde
مصطلحات موضوعية: Machado-joseph-disease, Protein ataxin-3, Polyglutamine disease, Mutant ataxin-3, Rat model, Huntingtin phosphorylation, Clinical-features, Expanded ataxin-3, Repeat expansion, Transgenic mice
وصف الملف: application/pdf; text/plain
العلاقة: info:eu-repo/grantAgreement/FCT/SFRH/SFRH/BD/47160/2008/PT; info:eu-repo/grantAgreement/FCT/SFRH/SFRH/BPD/70783/2010/PT; Journal of Cell Biology, vol. 212 (4), p. 465-480; http://jcb.rupress.org/content/212/4/465Test; http://hdl.handle.net/10216/108249Test
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3دورية أكاديمية
المؤلفون: An-Hsun Chou, Si-Ying Chen, Tu-Hsueh Yeh, Yi-Hsin Weng, Hung-Li Wang
المصدر: Neurobiology of Disease, Vol 41, Iss 2, Pp 481-488 (2011)
مصطلحات موضوعية: Spinocerebellar ataxia type 3, Ataxin-3, Polyglutamine-expanded ataxin-3, SCA3 transgenic mice, Cerebellum, Histone deacetylase, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
العلاقة: http://www.sciencedirect.com/science/article/pii/S0969996110003530Test; https://doaj.org/toc/1095-953XTest
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4دورية أكاديمية
المؤلفون: An-Hsun Chou, Tu-Hsueh Yeh, Pin Ouyang, Ying-Ling Chen, Si-Ying Chen, Hung-Li Wang
المصدر: Neurobiology of Disease, Vol 31, Iss 1, Pp 89-101 (2008)
مصطلحات موضوعية: Spinocerebellar ataxia type 3, Ataxin-3, Polyglutamine-expanded ataxin-3, SCA3 transgenic mice, Cerebellum, Microarray analysis, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
العلاقة: http://www.sciencedirect.com/science/article/pii/S0969996108000673Test; https://doaj.org/toc/1095-953XTest
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5دورية أكاديمية
المؤلفون: An-Hsun Chou, Tu-Hsueh Yeh, Yu-Li Kuo, Yu-Cheng Kao, Mei-Jie Jou, Chia-Yu Hsu, Shu-Ru Tsai, Akira Kakizuka, Hung-Li Wang
المصدر: Neurobiology of Disease, Vol 21, Iss 2, Pp 333-345 (2006)
مصطلحات موضوعية: Spinocerebellar ataxia type 3, Ataxin-3, Polyglutamine-expanded ataxin-3, Apoptosis, Polyglutamine neurodegenerative disorders, Bax, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
العلاقة: http://www.sciencedirect.com/science/article/pii/S0969996105002123Test; https://doaj.org/toc/1095-953XTest
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6
المؤلفون: Contessotto, Miriam Gisele Gasparotto, 1972, Garcia, Maria Cristina Cabral, Oliveira, Cristiano Luis Pinto de, 1975, Torriani, Iris Concepcion Linares de, 1934, Lopes-Cendes, Íscia Teresinha, 1964, Murai, Marcelo Jun, 1978
المساهمون: UNIVERSIDADE ESTADUAL DE CAMPINAS
المصدر: Repositório Institucional da Unicamp
Universidade Estadual de Campinas (UNICAMP)
instacron:UNICAMP
Repositório da Produção Científica e Intelectual da Unicampمصطلحات موضوعية: Doença de Machado-Joseph, Expanded ataxin-3, Machado-Joseph disease, Small-angle X-ray scattering, Artigo original, Ataxia, Raios X - Espalhamento a baixo ângulo
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=dedup_wf_001::3888209f15dcce4c49e8bbf2e03113caTest
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7دورية أكاديمية
المؤلفون: Vasconcelos-Ferreira, Ana, Martins, Inês Morgado, Lobo, Diana, Pereira, Dina, Lopes, Miguel M., Faro, Rosário, Lopes, Sara M., Verbeek, Dineke, Schmidt, Thorsten, Nóbrega, Clévio, Pereira de Almeida, Luís
المساهمون: Sapientia
مصطلحات موضوعية: Polyglutamine-Expanded Ataxin-3, Mutant Huntingt, Intranuclear Inclusions, Nuclear-Localization, Cerebellar-Aaxiagene-Productcell-Lines, Rat Modelin-Vitro, Autophagy
وصف الملف: application/pdf
العلاقة: 1525-0024
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8
المؤلفون: Sandra Macedo-Ribeiro, Luís Pereira de Almeida, Bruno Almeida, Clévio Nóbrega, Susana R. Louros, Ana Luísa Carvalho, Elisabete Ferreiro, Jorge Valero, Carlos A. Matos
المساهمون: Instituto de Investigação e Inovação em Saúde
المصدر: Repositório Científico de Acesso Aberto de Portugal
Repositório Científico de Acesso Aberto de Portugal (RCAAP)
instacron:RCAAP
The Journal of Cell Biology
Europe PubMed Centralمصطلحات موضوعية: Male, 0301 basic medicine, Time Factors, medicine.disease_cause, Synapse, Serine, 0302 clinical medicine, Transgenic mice, Phosphorylation, Ataxin-3, Mutant ataxin-3, Research Articles, Cerebral Cortex, Neurons, Mutation, Machado-Joseph Disease, Cell biology, Expanded ataxin-3, Biochemistry, Spinocerebellar ataxia, Rat model, RNA Interference, Protein ataxin-3, Machado–Joseph disease, Signal Transduction, congenital, hereditary, and neonatal diseases and abnormalities, Molecular Sequence Data, Gestational Age, Biology, Transfection, Neuroprotection, Article, 03 medical and health sciences, medicine, Animals, Humans, Amino Acid Sequence, Rats, Wistar, Cell Biology, Repeat expansion, Fibroblasts, medicine.disease, Clinical-features, Repressor Proteins, Disease Models, Animal, Polyglutamine disease, HEK293 Cells, 030104 developmental biology, nervous system, Ataxin, Machado-joseph-disease, Nerve Degeneration, Synapses, Huntingtin phosphorylation, Peptides, 030217 neurology & neurosurgery
وصف الملف: application/pdf; text/plain
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::caa8599ef81658f39793e775da0d11fcTest
https://hdl.handle.net/10216/108249Test -
9
المؤلفون: Yi Hsin Weng, Tu Hsueh Yeh, Hung Li Wang, Si Ying Chen, An Hsun Chou
المصدر: Neurobiology of Disease, Vol 41, Iss 2, Pp 481-488 (2011)
مصطلحات موضوعية: Transcriptional Activation, Genetically modified mouse, Cerebellum, congenital, hereditary, and neonatal diseases and abnormalities, Transgene, Down-Regulation, Mice, Transgenic, Nerve Tissue Proteins, Histone Deacetylases, lcsh:RC321-571, Mice, chemistry.chemical_compound, Downregulation and upregulation, Spinocerebellar ataxia type 3, medicine, Animals, Histone deacetylase, Enzyme Inhibitors, Polyglutamine-expanded ataxin-3, Ataxin-3, lcsh:Neurosciences. Biological psychiatry. Neuropsychiatry, Ataxin-1, biology, Nuclear Proteins, Acetylation, Sodium butyrate, Machado-Joseph Disease, Histone acetyltransferase, Molecular biology, Cell biology, Repressor Proteins, Phenotype, Histone, medicine.anatomical_structure, Ataxins, Neurology, chemistry, SCA3 transgenic mice, biology.protein, Butyric Acid
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::764adb266c7489328157913970c7d266Test
http://www.sciencedirect.com/science/article/pii/S0969996110003530Test -
10
المؤلفون: Tu Hsueh Yeh, Hung Li Wang, Pin Ouyang, Ying Ling Chen, Si Ying Chen, An Hsun Chou
المصدر: Neurobiology of Disease, Vol 31, Iss 1, Pp 89-101 (2008)
مصطلحات موضوعية: Genetically modified mouse, Cerebellum, Ataxia, Transcription, Genetic, Transgene, Blotting, Western, Gene Expression, Mice, Transgenic, Substantia nigra, Biology, lcsh:RC321-571, Mice, Spinocerebellar ataxia type 3, Heat shock protein, medicine, Animals, Humans, RNA, Messenger, Polyglutamine-expanded ataxin-3, Ataxin-3, lcsh:Neurosciences. Biological psychiatry. Neuropsychiatry, Oligonucleotide Array Sequence Analysis, Reverse Transcriptase Polymerase Chain Reaction, Neurodegeneration, Nuclear Proteins, Microarray analysis, Machado-Joseph Disease, medicine.disease, Immunohistochemistry, Molecular biology, Cell biology, Blotting, Southern, Disease Models, Animal, medicine.anatomical_structure, Neurology, nervous system, Ataxin, SCA3 transgenic mice, medicine.symptom, Peptides, Trinucleotide Repeat Expansion, Transcription Factors
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::e9fdf1f8f122593d4685fa8d75ff9efdTest
http://www.sciencedirect.com/science/article/pii/S0969996108000673Test