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المؤلفون: Chiung Yu Huang, Meghan E. McGarry, Dennis W. Nielson, Ngoc P. Ly
المصدر: J Cyst Fibros
Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, vol 20, iss 3مصطلحات موضوعية: Male, 0301 basic medicine, Pulmonary and Respiratory Medicine, medicine.medical_specialty, Longitudinal study, Younger age, Adolescent, Cystic Fibrosis, Clinical Sciences, Respiratory System, medicine.disease_cause, Cystic fibrosis, Article, Congenital, Young Adult, 03 medical and health sciences, Rare Diseases, 0302 clinical medicine, Clinical Research, Internal medicine, Humans, Medicine, Pseudomonas Infections, Longitudinal Studies, Registries, Preschool, Child, Lung, Survival analysis, Pediatric, Patient registry, business.industry, Pseudomonas aeruginosa, Hazard ratio, Infant, Newborn, Infant, Hispanic or Latino, Newborn, medicine.disease, United States, 030104 developmental biology, Increased risk, 030228 respiratory system, Child, Preschool, Pediatrics, Perinatology and Child Health, Health disparities, business
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::707afb2559bf0aa255d078a44c4d9628Test
https://doi.org/10.1016/j.jcf.2020.10.002Test -
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المؤلفون: Meghan E. McGarry, Ngoc P. Ly, John Neuhaus, Dennis W. Nielson
المصدر: Pediatr Pulmonol
Pediatric pulmonology, vol 54, iss 9مصطلحات موضوعية: Adult, Male, Pulmonary and Respiratory Medicine, Vital capacity, medicine.medical_specialty, Adolescent, Cystic Fibrosis, Respiratory System, Vital Capacity, Ethnic group, Cystic fibrosis, Article, White People, Pulmonary function testing, Paediatrics and Reproductive Medicine, Young Adult, 03 medical and health sciences, FEV1/FVC ratio, Rare Diseases, 0302 clinical medicine, Clinical Research, Forced Expiratory Volume, 030225 pediatrics, Epidemiology, medicine, Humans, Child, Lung, Retrospective Studies, pulmonary function testing, Patient registry, business.industry, Retrospective cohort study, Hispanic or Latino, respiratory system, medicine.disease, social dimensions of pulmonary medicine, United States, Respiratory Function Tests, Good Health and Well Being, 030228 respiratory system, Pediatrics, Perinatology and Child Health, Linear Models, epidemiology, Female, business, Demography
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::cd7e62a3f91bef08989af10ab86fcf13Test
https://doi.org/10.1002/ppul.24377Test -
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المؤلفون: Peter M. Haggie, Walter E. Finkbeiner, Joseph-Anthony Tan, Alan S. Verkman, Dennis W. Nielson, Jung-Ho Son, Luis J. V. Galietta, Mark J. Kurth, Lorna Zlock, Puay-Wah Phuan, Ilaria Musante, Clarabella J. Li
المساهمون: Phuan, Puay-Wah, Son, Jung-Ho, Tan, Joseph-Anthony, Li, Clarabella, Musante, Ilaria, Zlock, Lorna, Nielson, Dennis W., Finkbeiner, Walter E., Kurth, Mark J., Galietta, Luis J., Haggie, Peter M., Verkman, Alan S.
المصدر: Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, vol 17, iss 5
مصطلحات موضوعية: 0301 basic medicine, Cystic Fibrosis, High-throughput screen, Respiratory System, Mutant, Cystic Fibrosis Transmembrane Conductance Regulator, Quinolones, Pharmacology, Aminophenols, medicine.disease_cause, Cystic fibrosis, Congenital, 0302 clinical medicine, CFTR, Lung, Sulfonamides, Mutation, Cultured, Drug Synergism, respiratory system, Small molecule, Potentiator, Cystic fibrosi, N1303K, Ion Channel Gating, Pulmonary and Respiratory Medicine, Agonist, congenital, hereditary, and neonatal diseases and abnormalities, medicine.drug_class, Cells, Clinical Sciences, Article, Cell Line, Structure-Activity Relationship, 03 medical and health sciences, Rare Diseases, medicine, Animals, Humans, Structure–activity relationship, business.industry, medicine.disease, 030104 developmental biology, 030228 respiratory system, Cell culture, Pediatrics, Perinatology and Child Health, Mutant Proteins, business
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::ff281dd2963975887cc2ef3535c3e964Test
https://doi.org/10.1016/j.jcf.2018.05.010Test -
4دورية أكاديمية
المؤلفون: Mutation Sn, Meghan E. Mcgarry, Dennis W. Nielson
المساهمون: The Pennsylvania State University CiteSeerX Archives
المصدر: http://journal.publications.chestnet.org/pdfaccess.ashx?PDFSource%3D13%26ResourceID%3D6008271Test.
العلاقة: http://citeseerx.ist.psu.edu/viewdoc/summary?doi=10.1.1.673.9232Test; http://journal.publications.chestnet.org/pdfaccess.ashx?PDFSource%3D13%26ResourceID%3D6008271Test
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المؤلفون: Alan S. Verkman, Amber A. Rivera, Lorna Zlock, Dennis W. Nielson, Puay-Wah Phuan, Walter E. Finkbeiner, Peter M. Haggie, Joseph-Anthony Tan
المصدر: Scientific Reports
Scientific reports, vol 9, iss 1
Scientific Reports, Vol 9, Iss 1, Pp 1-12 (2019)مصطلحات موضوعية: 0301 basic medicine, congenital, hereditary, and neonatal diseases and abnormalities, Cystic Fibrosis, Mutant, Nonsense mutation, lcsh:Medicine, Cystic Fibrosis Transmembrane Conductance Regulator, medicine.disease_cause, Cystic fibrosis, Article, Congenital, 03 medical and health sciences, Structure-Activity Relationship, Rare Diseases, 0302 clinical medicine, Piperidines, Drug Discovery, medicine, Missense mutation, Humans, lcsh:Science, Lung, Chloride channels, Mutation, Multidisciplinary, biology, Chemistry, Drug discovery, lcsh:R, Drug Synergism, Potentiator, respiratory system, medicine.disease, Molecular biology, Cystic fibrosis transmembrane conductance regulator, 3. Good health, respiratory tract diseases, High-Throughput Screening Assays, 030104 developmental biology, 5.1 Pharmaceuticals, 030220 oncology & carcinogenesis, Chloride channel, biology.protein, Pyrazoles, lcsh:Q, Development of treatments and therapeutic interventions
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::f64b46f7be6481fe2a050f58427d89b7Test
https://pubmed.ncbi.nlm.nih.gov/31776420Test -
6دورية أكاديمية
المؤلفون: Benjamin L Schulz, Andrew J Sloane, J Robinson, Sindhu S Prasad, Robyn A Lindner, Michael Robinson, Peter T Bye, Dennis W Nielson, Jenny L Harry, Nicolle H Packer, Niclas G Karlsson
المساهمون: The Pennsylvania State University CiteSeerX Archives
وصف الملف: application/pdf
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المصدر: Pediatric pulmonology, vol 52, iss 12
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Adult, Male, Pediatrics, medicine.medical_specialty, Heterozygote, Adolescent, Cystic Fibrosis, hispanic latino, Respiratory System, Cystic Fibrosis Transmembrane Conductance Regulator, Cystic fibrosis, Article, Pulmonary function testing, Paediatrics and Reproductive Medicine, Cohort Studies, Congenital, 03 medical and health sciences, Young Adult, Rare Diseases, 0302 clinical medicine, Clinical Research, Forced Expiratory Volume, Epidemiology, medicine, Humans, 030212 general & internal medicine, Young adult, Child, Lung, pulmonary function testing, Patient registry, business.industry, Homozygote, Hispanic or Latino, medicine.disease, healthcare disparities, social dimensions of pulmonary medicine, Good Health and Well Being, medicine.anatomical_structure, 030228 respiratory system, Pediatrics, Perinatology and Child Health, Life expectancy, epidemiology, Female, business, Cohort study
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::a484ffe9f8991cc41a719044e3077acfTest
https://europepmc.org/articles/PMC5693693Test/ -
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المؤلفون: Carol J. Blaisdell, James Troendle, Anne Zajicek, Claire Chougnet, James M. Greenberg, William Hardie, Alan H. Jobe, Karen McDowell, Thomas Ferkol, Mark R. Holland, James Kemp, Philip T. Levy, Phillip Tarr, Gautam K. Singh, Barbara Warner, Aaron Hamvas, Philip L. Ballard, Roberta A. Ballard, Roberta L. Keller, Amir M. Khan, Leslie Lusk, Dennis W. Nielson, Elizabeth E. Rogers, David J. Durand, Jeffrey D. Merrill, Eric C. Eichenwald, Candice Fike, Tina Hartert, Paul Moore, Judy Aschner, Scott Guthrie, Nathalie Maitre, Marshall Summar, Carl D'Angio, Vasanth Kumar, Tom Mariani, Gloria Pryhuber, Anne Marie Reynolds, Kristin Scheible, Timothy Stevens, Clement Ren, Rita M. Ryan, C. Michael Cotten, Kim Fisher, Jack Sharp, Judith A. Voynow, Stephanie Davis, Brenda Poindexter, Jonas Ellenberg, Rui Feng, Melissa Fernando, Howard Panitch, Barbara Schmidt, Pamela Shaw, Scarlett Bellamy, Lynn M. Taussig
المصدر: The Journal of pediatrics. 197
مصطلحات موضوعية: Male, Pediatrics, medicine.medical_specialty, Neonatal intensive care unit, medicine.medical_treatment, Birth weight, Gestational Age, Article, Cohort Studies, 03 medical and health sciences, 0302 clinical medicine, 030225 pediatrics, Intensive care, Intensive Care Units, Neonatal, Medicine, Humans, 030212 general & internal medicine, Airway Management, Diuretics, Respiratory Distress Syndrome, Newborn, Respiratory distress, business.industry, Respiration, Postmenstrual Age, Infant, Newborn, Gestational age, United States, Infant, Extremely Premature, Pediatrics, Perinatology and Child Health, Female, Diuretic, business, Cohort study
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::f2d4ad6659c91ac8579951ecd32a8dddTest
https://pubmed.ncbi.nlm.nih.gov/30029857Test -
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المؤلفون: Claire D. Brindis, Thida Ong, Diana Dawson, Mary Ellen Kleinhenz, Dennis W. Nielson, Nancy Lewis, Megumi J. Okumura, Martha Richards
المصدر: Okumura, MJ; Ong, T; Dawson, D; Nielson, D; Lewis, N; Richards, M; et al.(2014). Improving transition from paediatric to adult cystic fibrosis care: Programme implementation and evaluation. BMJ Quality and Safety, 23(SUPPL1). doi: 10.1136/bmjqs-2013-002364. UCSF: Retrieved from: http://www.escholarship.org/uc/item/6zv2w1xkTest
BMJ quality & safety, vol 23 Suppl 1, iss SUPPL1مصطلحات موضوعية: Adult, Program evaluation, Transition to Adult Care, medicine.medical_specialty, Quality management, Adolescent, Cystic Fibrosis, Patient Education, Clinical Sciences, 8.1 Organisation and delivery of services, Cystic fibrosis, Transitions in Care, Article, Congenital, Young Adult, Rare Diseases, 7.1 Individual care needs, Clinical Research, Health care, Congenital Disorders, medicine, Humans, Program Development, Young adult, Preschool, Child, Intensive care medicine, Lung, Curriculum, Quality of Health Care, Patient Care Team, business.industry, Health Policy, Programme implementation, medicine.disease, Quality Improvement, United States, Child, Preschool, Public Health and Health Services, Health Policy & Services, Management of diseases and conditions, Patient Care, business, Curriculum and Pedagogy, Health and social care services research, Program Evaluation, Patient education
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::fea2037a380974d259181141ab02e055Test
https://doi.org/10.1136/bmjqs-2013-002364Test -
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المؤلفون: Puay-Wah Phuan, Walter E. Finkbeiner, Radu G. Avramescu, Doranda Perdomo, Gergely L. Lukacs, Peter M. Haggie, Dennis W. Nielson, Haijin Xu, Alan S. Verkman, Lorna Zlock, Joseph-Anthony Tan
المصدر: The Journal of biological chemistry, vol 292, iss 3
مصطلحات موضوعية: 0301 basic medicine, Cystic Fibrosis, Regulator, Cystic Fibrosis Transmembrane Conductance Regulator, Quinolones, medicine.disease_cause, Aminophenols, Biochemistry, Cystic fibrosis, Medical and Health Sciences, Piperazines, 0302 clinical medicine, Lung, Cells, Cultured, Mutation, Inbred F344, Cultured, Transfection, Biological Sciences, Transmembrane protein, Cell biology, 5.1 Pharmaceuticals, Development of treatments and therapeutic interventions, Biochemistry & Molecular Biology, Cells, small molecule, Mutation, Missense, Biology, drug discovery, 03 medical and health sciences, Rare Diseases, medicine, Animals, Humans, Editors' Picks, drug screening, ΔF508, Molecular Biology, Wild type, Cell Biology, Potentiator, medicine.disease, Rats, Inbred F344, Rats, 030104 developmental biology, Orphan Drug, 030228 respiratory system, Amino Acid Substitution, Chemical Sciences, Missense
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::f9ee1b4b68959eb31aadd51eb37112dcTest
https://europepmc.org/articles/PMC5247652Test/