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1دورية أكاديمية
المؤلفون: Vazquez-Sanchez, Sonia, Tilkin, Britt, Gasset-Rosa, Fatima, Zhang, Sitao, Piol, Diana, McAlonis-Downes, Melissa, Artates, Jonathan, Govea-Perez, Noe, Verresen, Yana, Guo, Lin, Cleveland, Don, Shorter, James, Da Cruz, Sandrine
المصدر: Department of Biochemistry and Molecular Biology Faculty Papers
مصطلحات موضوعية: animals, humans, mice, amyotrophic lateral sclerosis, brain, disease models, animal, disease progression, frontotemporal dementia, transgenic, protein aggregation, pathological, RNA-binding protein FUS, Biochemistry, Medical Sciences, Molecular Biology, Nervous System Diseases
وصف الملف: application/pdf
العلاقة: https://jdc.jefferson.edu/bmpfp/258Test; https://jdc.jefferson.edu/context/bmpfp/article/1259/viewcontent/Frontotemporal_dementia_like_disease_progression_elicited_by_seeded_aggregation_and_spread_of_FUS.pdfTest; https://jdc.jefferson.edu/context/bmpfp/article/1259/filename/0/type/additional/viewcontent/Supplementary_Material_1.pdfTest
الإتاحة: https://jdc.jefferson.edu/bmpfp/258Test
https://jdc.jefferson.edu/context/bmpfp/article/1259/viewcontent/Frontotemporal_dementia_like_disease_progression_elicited_by_seeded_aggregation_and_spread_of_FUS.pdfTest
https://jdc.jefferson.edu/context/bmpfp/article/1259/filename/0/type/additional/viewcontent/Supplementary_Material_1.pdfTest -
2دورية أكاديمية
المؤلفون: Maimon, Roy, Chillon-Marinas, Carlos, Snethlage, Cedric E, Singhal, Sarthak M, McAlonis-Downes, Melissa, Ling, Karen, Rigo, Frank, Bennett, C Frank, Da Cruz, Sandrine, Hnasko, Thomas S, Muotri, Alysson R, Cleveland, Don W
المصدر: Nature Neuroscience. 24(8)
مصطلحات موضوعية: Biomedical and Clinical Sciences, Neurosciences, Neurodegenerative, Biotechnology, Stem Cell Research - Nonembryonic - Non-Human, Stem Cell Research, Aging, Brain Disorders, 1.1 Normal biological development and functioning, Underpinning research, Neurological, Animals, Cellular Reprogramming, Dentate Gyrus, Ependymoglial Cells, Mice, Neurogenesis, Neurons, Oligonucleotides, Antisense, Polypyrimidine Tract-Binding Protein, Psychology, Cognitive Sciences, Neurology & Neurosurgery, Biological psychology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/84x4q7zgTest
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3دورية أكاديمية
المؤلفون: Yu, Haiyang, Lu, Shan, Gasior, Kelsey, Singh, Digvijay, Vazquez-Sanchez, Sonia, Tapia, Olga, Toprani, Divek, Beccari, Melinda S, Yates, John R, Da Cruz, Sandrine, Newby, Jay M, Lafarga, Miguel, Gladfelter, Amy S, Villa, Elizabeth, Cleveland, Don W
المصدر: Science. 371(6529)
مصطلحات موضوعية: Neurosciences, Neurodegenerative, Aetiology, 2.1 Biological and endogenous factors, Aging, Animals, Anisotropy, Cryoelectron Microscopy, DNA-Binding Proteins, HEK293 Cells, HSP70 Heat-Shock Proteins, Histone Deacetylases, Humans, Liquid Crystals, Mice, Mice, Inbred C57BL, Mutation, Neurodegenerative Diseases, Neurons, Proteasome Endopeptidase Complex, Proteasome Inhibitors, Protein Aggregates, Protein Domains, RNA-Binding Proteins, Rats, Rats, Sprague-Dawley, General Science & Technology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/8598b09mTest
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4دورية أكاديمية
المؤلفون: Zhu, Qiang, Jiang, Jie, Gendron, Tania F, McAlonis-Downes, Melissa, Jiang, Lulin, Taylor, Amy, Diaz Garcia, Sandra, Ghosh Dastidar, Somasish, Rodriguez, Maria J, King, Patrick, Zhang, Yongjie, La Spada, Albert R, Xu, Huaxi, Petrucelli, Leonard, Ravits, John, Da Cruz, Sandrine, Lagier-Tourenne, Clotilde, Cleveland, Don W
المصدر: Nature Neuroscience. 23(5)
مصطلحات موضوعية: Genetics, Neurosciences, Neurodegenerative, Aging, Orphan Drug, Dementia, Rare Diseases, Alzheimer's Disease including Alzheimer's Disease Related Dementias (AD/ADRD), Brain Disorders, Alzheimer's Disease Related Dementias (ADRD), Frontotemporal Dementia (FTD), ALS, Acquired Cognitive Impairment, 2.1 Biological and endogenous factors, Aetiology, Neurological, Amyotrophic Lateral Sclerosis, Animals, C9orf72 Protein, DNA Repeat Expansion, Female, Frontotemporal Dementia, Male, Mice, Mice, Inbred C57BL, Mice, Transgenic, Psychology, Cognitive Sciences, Neurology & Neurosurgery
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/8gr0980rTest
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5دورية أكاديمية
المؤلفون: Bravo-Hernandez, Mariana, Tadokoro, Takahiro, Navarro, Michael R, Platoshyn, Oleksandr, Kobayashi, Yoshiomi, Marsala, Silvia, Miyanohara, Atsushi, Juhas, Stefan, Juhasova, Jana, Skalnikova, Helena, Tomori, Zoltan, Vanicky, Ivo, Studenovska, Hana, Proks, Vladimir, Chen, PeiXi, Govea-Perez, Noe, Ditsworth, Dara, Ciacci, Joseph D, Gao, Shang, Zhu, Wenlian, Ahrens, Eric T, Driscoll, Shawn P, Glenn, Thomas D, McAlonis-Downes, Melissa, Da Cruz, Sandrine, Pfaff, Samuel L, Kaspar, Brian K, Cleveland, Don W, Marsala, Martin
المصدر: Nature Medicine. 26(1)
مصطلحات موضوعية: Medical Biotechnology, Biomedical and Clinical Sciences, Neurosciences, Gene Therapy, Brain Disorders, Traumatic Head and Spine Injury, ALS, Genetics, Spinal Cord Injury, Rare Diseases, Biotechnology, Neurodegenerative, Physical Injury - Accidents and Adverse Effects, Neurological, Amyotrophic Lateral Sclerosis, Animals, Atrophy, Dependovirus, Disease Progression, Evoked Potentials, Motor, Female, Gene Expression Regulation, Gene Silencing, Gene Transfer Techniques, Humans, Inflammation, Interneurons, Male, Mice, Inbred C57BL, Mice, Transgenic, Motor Neurons, Muscle Development, Nerve Degeneration, Pia Mater, Primates, Protein Folding, RNA, Messenger, RNA, Small Interfering, Spinal Cord, Superoxide Dismutase-1, Swine, Medical and Health Sciences, Immunology, Biomedical and clinical sciences, Health sciences
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/2vg510sdTest
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6دورية أكاديمية
المؤلفون: Jiang, Lu-Lin, Zhu, Bing, Zhao, Yingjun, Li, Xiaoguang, Liu, Tongfei, Pina-Crespo, Juan, Zhou, Lisa, Xu, Wenxi, Rodriguez, Maria J, Yu, Haiyang, Cleveland, Don W, Ravits, John, Da Cruz, Sandrine, Long, Tao, Zhang, Dongxian, Huang, Timothy Y, Xu, Huaxi
المصدر: Journal of Clinical Investigation. 129(8)
مصطلحات موضوعية: Neurosciences, ALS, Genetics, Rare Diseases, Brain Disorders, Neurodegenerative, Aetiology, 2.1 Biological and endogenous factors, Neurological, Amyotrophic Lateral Sclerosis, Animals, Astrocytes, Down-Regulation, Excitatory Amino Acid Transporter 2, Glutamic Acid, Humans, Mice, Mice, Knockout, Motor Cortex, Nerve Tissue Proteins, Receptors, Tumor Necrosis Factor, Type I, Superoxide Dismutase, Transcription, Genetic, Up-Regulation, Cell Biology, Neurodegeneration, Neuroscience, Medical and Health Sciences, Immunology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/3np9p571Test
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7دورية أكاديمية
المؤلفون: Gasset-Rosa, Fatima, Lu, Shan, Yu, Haiyang, Chen, Cong, Melamed, Ze'ev, Guo, Lin, Shorter, James, Da Cruz, Sandrine, Cleveland, Don W
المصدر: Neuron. 102(2)
مصطلحات موضوعية: Acquired Cognitive Impairment, Neurodegenerative, Brain Disorders, Rare Diseases, Dementia, Active Transport, Cell Nucleus, Amyotrophic Lateral Sclerosis, Animals, Cell Death, Cell Line, Tumor, Cytoplasmic Granules, DNA-Binding Proteins, Frontotemporal Dementia, GTPase-Activating Proteins, HEK293 Cells, Humans, Membrane Glycoproteins, Mice, Neurons, Nuclear Pore Complex Proteins, Phase Transition, Stress, Physiological, alpha Karyopherins, ran GTP-Binding Protein, ALS/FTD, RNA-binding proteins, TDP-43, TDP-43 de-mixing, iPSCs, liquid-liquid phase separation, low complexity domains, motor neurons, neurodegeneration, nucleocytoplasmic transport, stress granules, Neurosciences, Psychology, Cognitive Sciences, Neurology & Neurosurgery
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/3rv1f882Test
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8دورية أكاديمية
المؤلفون: Ling, Shuo-Chien, Dastidar, Somasish Ghosh, Tokunaga, Seiya, Ho, Wan Yun, Lim, Kenneth, Ilieva, Hristelina, Parone, Philippe A, Tyan, Sheue-Houy, Tse, Tsemay M, Chang, Jer-Cherng, Platoshyn, Oleksandr, Bui, Ngoc B, Bui, Anh, Vetto, Anne, Sun, Shuying, McAlonis-Downes, Melissa, Han, Joo Seok, Swing, Debbie, Kapeli, Katannya, Yeo, Gene W, Tessarollo, Lino, Marsala, Martin, Shaw, Christopher E, Tucker-Kellogg, Greg, La Spada, Albert R, Lagier-Tourenne, Clotilde, Da Cruz, Sandrine, Cleveland, Don W
مصطلحات موضوعية: Lysosomes, Animals, Mice, Inbred C57BL, Humans, RNA-Binding Protein FUS, RNA, Gene Expression Profiling, Homeostasis, Autophagy, Mutant Proteins, FUS, RNA metabolism, amyotrophic lateral sclerosis, autophagy-lysosome, frontotemporal degeneration, homeostasis, mouse, neuroscience, Mice, Inbred C57BL, Biochemistry and Cell Biology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/5w2862f9Test
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9دورية أكاديمية
المؤلفون: Melamed, Ze’ev, López-Erauskin, Jone, Baughn, Michael W, Zhang, Ouyang, Drenner, Kevin, Sun, Ying, Freyermuth, Fernande, McMahon, Moira A, Beccari, Melinda S, Artates, Jon W, Ohkubo, Takuya, Rodriguez, Maria, Lin, Nianwei, Wu, Dongmei, Bennett, C Frank, Rigo, Frank, Da Cruz, Sandrine, Ravits, John, Lagier-Tourenne, Clotilde, Cleveland, Don W
المصدر: Nature Neuroscience. 22(2)
مصطلحات موضوعية: Biomedical and Clinical Sciences, Neurosciences, Dementia, Regenerative Medicine, Brain Disorders, Neurodegenerative, Genetics, Rare Diseases, ALS, Stem Cell Research - Induced Pluripotent Stem Cell, Stem Cell Research, Orphan Drug, Acquired Cognitive Impairment, 2.1 Biological and endogenous factors, Aetiology, Neurological, Amyotrophic Lateral Sclerosis, DNA-Binding Proteins, Female, Humans, Membrane Proteins, Motor Cortex, Motor Neurons, Nerve Degeneration, Polyadenylation, Spinal Cord, Stathmin, Psychology, Cognitive Sciences, Neurology & Neurosurgery, Biological psychology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/0hr574czTest
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10دورية أكاديمية
المؤلفون: López-Erauskin, Jone, Tadokoro, Takahiro, Baughn, Michael W, Myers, Brian, McAlonis-Downes, Melissa, Chillon-Marinas, Carlos, Asiaban, Joshua N, Artates, Jonathan, Bui, Anh T, Vetto, Anne P, Lee, Sandra K, Le, Ai Vy, Sun, Ying, Jambeau, Mélanie, Boubaker, Jihane, Swing, Deborah, Qiu, Jinsong, Hicks, Geoffrey G, Ouyang, Zhengyu, Fu, Xiang-Dong, Tessarollo, Lino, Ling, Shuo-Chien, Parone, Philippe A, Shaw, Christopher E, Marsala, Martin, Lagier-Tourenne, Clotilde, Cleveland, Don W, Da Cruz, Sandrine
المصدر: Neuron. 100(4)
مصطلحات موضوعية: Hippocampus, Axons, Cells, Cultured, Animals, Mice, Inbred C57BL, Mice, Transgenic, Humans, Mice, Amyotrophic Lateral Sclerosis, RNA-Binding Protein FUS, Protein Biosynthesis, Pregnancy, Female, Male, Frontotemporal Dementia, Loss of Function Mutation, ALS, FTD, FUS, Frontotemporal dementia, RNA-binding proteins, TLS, axonal translation, neurodegenerative disease, protein synthesis, Neurodegenerative, Alzheimer's Disease including Alzheimer's Disease Related Dementias (AD/ADRD), Neurosciences, Dementia, Genetics, Alzheimer's Disease Related Dementias (ADRD), Behavioral and Social Science, Brain Disorders, Aging, Frontotemporal Dementia (FTD), Acquired Cognitive Impairment, Rare Diseases, Aetiology, 2.1 Biological and endogenous factors, Neurological, Psychology, Cognitive Sciences, Neurology & Neurosurgery
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/1xc9h7bmTest