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المؤلفون: C.N. Gambelli, J. Bredin, A.-C.M. Doix, J. Garcia, V. Tanant, M. Fournier-Mehouas, C. Desnuelle, S. Sacconi, S.S. Colson
المصدر: SSRN Electronic Journal.
مصطلحات موضوعية: History, Polymers and Plastics, Biophysics, Orthopedics and Sports Medicine, Business and International Management, Industrial and Manufacturing Engineering
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::f49641d6d4d60ff80f365be2591d4cb3Test
https://doi.org/10.2139/ssrn.4200000Test -
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المؤلفون: M.-H. Soriani, C. Desnuelle
المصدر: Revue Neurologique. 173:288-299
مصطلحات موضوعية: Weakness, medicine.medical_specialty, Physical disability, Palliative care, Disease, 03 medical and health sciences, 0302 clinical medicine, Physical medicine and rehabilitation, Quality of life (healthcare), Multidisciplinary approach, medicine, Humans, Respiratory function, 030212 general & internal medicine, Amyotrophic lateral sclerosis, Patient Care Team, Nutritional Support, business.industry, Amyotrophic Lateral Sclerosis, Palliative Care, medicine.disease, Respiration, Artificial, Patient Care Management, Neurology, Neurology (clinical), medicine.symptom, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::ff103b4edf3578a457c0b726d616fbeaTest
https://doi.org/10.1016/j.neurol.2017.03.031Test -
3دورية أكاديمية
المؤلفون: A. Al chalabi, P. M. Andersen, S. Chandran, A. Chio, P. Corcia, P. Couratier, O. Danielsson, M. De Carvalho, C. Desnuelle, T. Grehl, J. Grosskreutz, T. Holmã ̧y, C. Ingre, M. Karlsborg, G. Kleveland, J. Christoph Koch, B. Koritnik, M. Kuzmakozakiewicz, H. Laaksovirta, A. Ludolph, C. Mcdermott, T. Meyer, B. Mitre Ropero, J. Mora Pardina, I. Nygren, S. Petri, M. Povedano Panades, F. Salachas, P. Shaw, V. Silani, G. Staaf, K. Svenstrup, K. Talbot, O. Tysnes, P. Van Damme, A. Van Der Kooi, M. Weber, P. Weydt, J. Wolf, O. Hardiman, L. H. Van Den Berg
المساهمون: A. Al chalabi, P.M. Andersen, S. Chandran, A. Chio, P. Corcia, P. Couratier, O. Danielsson, M. De Carvalho, C. Desnuelle, T. Grehl, J. Grosskreutz, T. Holmã ̧y, C. Ingre, M. Karlsborg, G. Kleveland, J. Christoph Koch, B. Koritnik, M. Kuzmakozakiewicz, H. Laaksovirta, A. Ludolph, C. Mcdermott, T. Meyer, B. Mitre Ropero, J. Mora Pardina, I. Nygren, S. Petri, M. Povedano Panade, F. Salacha, P. Shaw, V. Silani, G. Staaf, K. Svenstrup, K. Talbot, O. Tysne, P. Van Damme, A. Van Der Kooi, M. Weber, P. Weydt, J. Wolf, O. Hardiman, L.H. Van Den Berg
مصطلحات موضوعية: Neurology, Neurology (clinical), Settore MED/26 - Neurologia
العلاقة: info:eu-repo/semantics/altIdentifier/pmid/28975816; info:eu-repo/semantics/altIdentifier/wos/WOS:000415817900001; volume:18; issue:7-8; firstpage:471; lastpage:474; numberofpages:4; journal:AMYOTROPHIC LATERAL SCLEROSIS AND FRONTOTEMPORAL DEGENERATION; http://hdl.handle.net/2434/526534Test; info:eu-repo/semantics/altIdentifier/scopus/2-s2.0-85030548661
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المؤلفون: Constantinos Papadopoulos, David Orlikowski, Hélène Prigent, Arnaud Lacour, Céline Tard, Alain Furby, Julien Praline, Guilhem Solé, Jean-Yves Hogrel, Marie De Antonio, Claudio Semplicini, Joelle Deibener-Kaminsky, Pierre Kaminsky, Bruno Eymard, Nadjib Taouagh, Barbara Perniconi, Dalil Hamroun, Pascal Laforêt, G. Bassez, A.-L. Bedat-Millet, A. Behin, B. Eymard, S. Leonard-Louis, T. Stojkovic, A. Canal, V. Decostre, F. Bouhour, F. Boyer, C. Caillaud, Y. Castaing, F. Chapon, P. Cintas, I. Durieu, A. Echaniz-Laguna, L. Feasson, X. Ferrer, R. Froissart, M. Piraud, D. Germain, K. Benistan, N. Guffon-Fouilhoux, H. Journel, P. Labauge, A. Levy, A. Magot, Y. Péréon, M.-C. Minot-Myhié, A. Nadaj-Pakleza, C. Nathier, N. Pellegrini, P. Petiot, F. Lofaso, A. Dutry, D. Renard, S. Sacconi, C. Desnuelle, E. Salort-Campana, J. Pouget, V. Tiffreau, D. Vincent, F. Zagnoli
المساهمون: Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Troubles cognitifs dégénératifs et vasculaires - U 1171 - EA 1046 (TCDV), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Lille, Droit et Santé-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Unité de Recherche Pluridisciplinaire Sport, Santé, Société (URePSSS) - ULR 7369 - ULR 4488 (URePSSS), Université d'Artois (UA)-Université du Littoral Côte d'Opale (ULCO)-Université de Lille, Troubles cognitifs dégénératifs et vasculaires - U 1171 (TCDV), Université de Lille-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille)-Institut National de la Santé et de la Recherche Médicale (INSERM), Université d'Artois (UA)-Université de Lille-Université du Littoral Côte d'Opale (ULCO)
المصدر: Molecular Genetics and Metabolism
Molecular Genetics and Metabolism, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩
Molecular Genetics and Metabolism, Elsevier, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩مصطلحات موضوعية: 0301 basic medicine, Male, Pediatrics, Endocrinology, Diabetes and Metabolism, [SDV]Life Sciences [q-bio], Mesh:Walking, Walking, Mesh:Adult, Respiratory failure, Biochemistry, Late Onset Disorders, Cohort Studies, 0302 clinical medicine, Endocrinology, Mesh:alpha-Glucosidases/therapeutic use, Glycogen Storage Disease Type II, Respiration, Pompe disease, Enzyme replacement therapy, Middle Aged, 3. Good health, Diabetes and Metabolism, Mesh:Late Onset Disorders/drug therapy, Cohort, Breathing, Female, France, Mesh:Respiration, Mesh:alpha-Glucosidases/administration & dosage, Mesh:Enzyme Replacement Therapy*/adverse effects, medicine.drug, Adult, Mesh:Female, medicine.medical_specialty, congenital, hereditary, and neonatal diseases and abnormalities, Mesh:Glycogen Storage Disease Type II/drug therapy, Mesh:Male, Late onset, 03 medical and health sciences, FEV1/FVC ratio, Mesh:alpha-Glucosidases/adverse effects, Mesh:Middle Aged, Mesh:Glycogen Storage Disease Type II/physiopathology, Genetics, medicine, Humans, Mesh:Cohort Studies, Adverse effect, Molecular Biology, Alglucosidase alfa, Mesh:France, Advanced, business.industry, nutritional and metabolic diseases, alpha-Glucosidases, Surgery, Mesh:Humans, 030104 developmental biology, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::2eca040ef3e520953509b66aeb672813Test
https://hal.univ-lille.fr/hal-02369159Test -
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المؤلفون: E. Delmont, C. Desnuelle
المصدر: Pratique Neurologique - FMC. 4:233-239
مصطلحات موضوعية: Neurology (clinical)
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_________::9015e325fbedd257a7c67ff362d20be9Test
https://doi.org/10.1016/j.praneu.2013.10.003Test -
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المؤلفون: P, Laforêt, K, Laloui, B, Granger, D, Hamroun, N, Taouagh, J-Y, Hogrel, D, Orlikowski, F, Bouhour, A, Lacour, E, Salort-Campana, I, Penisson-Besnier, S, Sacconi, F, Zagnoli, F, Chapon, B, Eymard, C, Desnuelle, J, Pouget, D, Vincent
المصدر: Revue Neurologique. 169:595-602
مصطلحات موضوعية: Adult, Male, medicine.medical_specialty, Weakness, Pediatrics, Biopsy, Cohort Studies, Age Distribution, Glycogen storage disease type II, medicine, Humans, Registries, Prospective cohort study, Alglucosidase alfa, Glycogen Storage Disease Type II, business.industry, Muscles, Muscle weakness, alpha-Glucosidases, Enzyme replacement therapy, Middle Aged, medicine.disease, Surgery, Natural history, Neurology, Cohort, Female, France, Neurology (clinical), medicine.symptom, business, medicine.drug
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::168b913bde13165fa65af14534581b91Test
https://doi.org/10.1016/j.neurol.2013.07.002Test -
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المؤلفون: Jésus Gonzalez-Bermejo, C. Desnuelle, C. Tromeur, Frédéric Gagnadoux
المصدر: Revue des Maladies Respiratoires Actualités. 4:118-122
مصطلحات موضوعية: Pulmonary and Respiratory Medicine
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_________::287007252b139f06d4f988313bf451a8Test
https://doi.org/10.1016/s1877-1203Test(12)70205-7 -
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المؤلفون: G Serratrice, C Desnuelle, S Sacconi
المصدر: EMC - Neurologie. 8:1-11
مصطلحات موضوعية: business.industry, Medicine, Anatomy, business
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_________::d9512285d9bb38117f04d22733990ad8Test
https://doi.org/10.1016/s0246-0378Test(11)53739-x -
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المؤلفون: C. Desnuelle, M.-H. Soriani
المصدر: Revue Neurologique. 165:627-640
مصطلحات موضوعية: medicine.medical_specialty, Pediatrics, Disease, Environmental exposure, medicine.disease, Dysphagia, Neurology, Epidemiology, medicine, Etiology, Neurology (clinical), medicine.symptom, Risk factor, Amyotrophic lateral sclerosis, Survival analysis
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_________::3526ed5d998dae503085927156f86552Test
https://doi.org/10.1016/j.neurol.2009.04.004Test -
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المؤلفون: J. Serratrice, C. Desnuelle
المصدر: EMC - Traité de médecine AKOS. 1:1-9
مصطلحات موضوعية: General Medicine
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::cdb6116b2ca359d92da687010adc67e8Test
https://doi.org/10.1016/s1634-6939Test(06)75428-x