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1
المؤلفون: Valeria Crippa, Riccardo Cristofani, Paola Rusmini, E. Onesto, Elisa Giorgetti, A. Boncoraglio, Mariarita Galbiati, Angela Poletti, A. Zito
المصدر: Biochemical Society Transactions. 41:1598-1604
مصطلحات موضوعية: Motor Neurons, Protein Folding, Cell type, Superoxide Dismutase, Muscles, Amyotrophic Lateral Sclerosis, Skeletal muscle, Biology, musculoskeletal system, MyoD, Biochemistry, Muscle atrophy, Cell biology, Superoxide Dismutase-1, medicine.anatomical_structure, nervous system, Proteotoxicity, Proteasome, medicine, Animals, Humans, Myocyte, medicine.symptom, Myogenin
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::62d4bdd681b2ca488bd73279b4e92240Test
https://doi.org/10.1042/bst20130118Test -
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المؤلفون: Mariarita Galbiati, A. Boncoraglio, Valeria Crippa, E. Bolzoni, Silvia De Biasi, Daniela Sau, E. Onesto, Angelo Poletti, Elena Fontana, Paola Rusmini, Serena Carra, Marianna Marino, Caterina Bendotti
المصدر: Human Molecular Genetics, 19(17), 3440-3456. Oxford University Press
مصطلحات موضوعية: Male, Protein Folding, animal diseases, Muscle Proteins, Gene mutation, FAMILIAL ALS, Mice, Superoxide Dismutase-1, POLYGLUTAMINE TRACT, Amyotrophic lateral sclerosis, Heat-Shock Proteins, Genetics (clinical), Motor Neurons, CHAPERONE ACTIVITY, ANDROGEN RECEPTOR, SOD1, General Medicine, chaperones, protein degradation, protein mislfolding, Cell biology, DNA-Binding Proteins, Female, SPINAL-CORD, 5-ALPHA-REDUCTASE TYPE-2, Mice, Transgenic, Protein Serine-Threonine Kinases, Protein degradation, Biology, BAG3, Cell Line, Heat shock protein, Autophagy, Genetics, medicine, Animals, Humans, HSP20 Heat-Shock Proteins, MARIE-TOOTH-DISEASE, Molecular Biology, MUTANT MICE, Superoxide Dismutase, MUTATIONS, Amyotrophic Lateral Sclerosis, nutritional and metabolic diseases, medicine.disease, nervous system diseases, Mice, Inbred C57BL, Proteasome, nervous system, Immunology, MOTOR-NEURONS, Molecular Chaperones
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::aecb4e0d64f4f3e2259f5b127752ed80Test
https://hdl.handle.net/11370/3713ab91-fc92-4276-b50f-1ed5004a4870Test