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المؤلفون: Angelo Poletti, Paola Rusmini, A. Zito, Mariarita Galbiati, Valeria Crippa, Nicola Ferri, E. Onesto
المصدر: Journal of Neurochemistry
مصطلحات موضوعية: Cell type, Proteasome Endopeptidase Complex, amyotrophic lateral sclerosis, autophagy, motor neuron diseases, muscle, animal diseases, SOD1, Biology, Biochemistry, Cell Line, motoneuron diseases, Myoblasts, Cellular and Molecular Neuroscience, chemistry.chemical_compound, Superoxide Dismutase-1, Mutant protein, MG132, neurodegeneration, proteasome, aggregation, protein misfolding, medicine, Myocyte, Humans, Cell Line, Transformed, Motor Neurons, Molecular Basis of Disease, Muscle Cells, Superoxide Dismutase, nutritional and metabolic diseases, Original Articles, musculoskeletal system, Muscle atrophy, Cell biology, nervous system diseases, Proteasome, chemistry, nervous system, Cell culture, Immunology, Mutation, medicine.symptom, Proteasome Inhibitors
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::6b09d29e6ac99dfe4242b7bc01f78cbbTest
http://hdl.handle.net/11577/3177789Test -
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المؤلفون: Daniela Sau, Paola Rusmini, Valeria Crippa, Patrizia Riso, Caterina Bendotti, E. Onesto, Marisa Porrini, Angelo Poletti, Silvia De Biasi, Silvia Simeoni, Isabella Palazzolo, E. Bolzoni, Serena Guarnieri, L. Vitellaro-Zuccarello
المصدر: Human molecular genetics. 16(13)
مصطلحات موضوعية: Cytoplasm, Proteasome Endopeptidase Complex, DNA damage, animal diseases, SOD1, Mutant, Mice, Transgenic, Biology, medicine.disease_cause, Gene Expression Regulation, Enzymologic, Superoxide dismutase, Mice, Genetics, medicine, Animals, Molecular Biology, Genetics (clinical), Loss function, Cell Nucleus, Mutation, Superoxide Dismutase, Amyotrophic Lateral Sclerosis, nutritional and metabolic diseases, General Medicine, Molecular biology, nervous system diseases, Oxygen, Cell nucleus, Oxidative Stress, medicine.anatomical_structure, nervous system, Proteasome, Microscopy, Fluorescence, Spinal Cord, biology.protein, DNA Damage
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8270f59c73893228fc8fedd9b7364e05Test
https://pubmed.ncbi.nlm.nih.gov/17504823Test