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1
المؤلفون: Mariarita Galbiati, A. Boncoraglio, Valeria Crippa, E. Bolzoni, Silvia De Biasi, Daniela Sau, E. Onesto, Angelo Poletti, Elena Fontana, Paola Rusmini, Serena Carra, Marianna Marino, Caterina Bendotti
المصدر: Human Molecular Genetics, 19(17), 3440-3456. Oxford University Press
مصطلحات موضوعية: Male, Protein Folding, animal diseases, Muscle Proteins, Gene mutation, FAMILIAL ALS, Mice, Superoxide Dismutase-1, POLYGLUTAMINE TRACT, Amyotrophic lateral sclerosis, Heat-Shock Proteins, Genetics (clinical), Motor Neurons, CHAPERONE ACTIVITY, ANDROGEN RECEPTOR, SOD1, General Medicine, chaperones, protein degradation, protein mislfolding, Cell biology, DNA-Binding Proteins, Female, SPINAL-CORD, 5-ALPHA-REDUCTASE TYPE-2, Mice, Transgenic, Protein Serine-Threonine Kinases, Protein degradation, Biology, BAG3, Cell Line, Heat shock protein, Autophagy, Genetics, medicine, Animals, Humans, HSP20 Heat-Shock Proteins, MARIE-TOOTH-DISEASE, Molecular Biology, MUTANT MICE, Superoxide Dismutase, MUTATIONS, Amyotrophic Lateral Sclerosis, nutritional and metabolic diseases, medicine.disease, nervous system diseases, Mice, Inbred C57BL, Proteasome, nervous system, Immunology, MOTOR-NEURONS, Molecular Chaperones
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::aecb4e0d64f4f3e2259f5b127752ed80Test
https://hdl.handle.net/11370/3713ab91-fc92-4276-b50f-1ed5004a4870Test -
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المؤلفون: Maria Elena Cicardi, Angelo Poletti, Elisa Giorgetti, Mariarita Galbiati, E. Onesto, Valeria Crippa, Riccardo Cristofani, Elio Messi, Paola Rusmini
المصدر: Neurochemistry international. 79
مصطلحات موضوعية: Denervation, Motor Neurons, Cell type, Muscle Cells, Autophagy, Amyotrophic Lateral Sclerosis, Cell Biology, Protein aggregation, Motor neuron, Biology, medicine.disease, Cellular and Molecular Neuroscience, medicine.anatomical_structure, nervous system, medicine, Myocyte, Animals, Humans, Amyotrophic lateral sclerosis, Proteostasis Deficiencies, Neuroscience, Intracellular
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::a496b0c3d53af823c1030163a8a8913bTest
https://pubmed.ncbi.nlm.nih.gov/25451799Test -
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المؤلفون: Angelo Poletti, Paola Rusmini, A. Zito, Mariarita Galbiati, Valeria Crippa, Nicola Ferri, E. Onesto
المصدر: Journal of Neurochemistry
مصطلحات موضوعية: Cell type, Proteasome Endopeptidase Complex, amyotrophic lateral sclerosis, autophagy, motor neuron diseases, muscle, animal diseases, SOD1, Biology, Biochemistry, Cell Line, motoneuron diseases, Myoblasts, Cellular and Molecular Neuroscience, chemistry.chemical_compound, Superoxide Dismutase-1, Mutant protein, MG132, neurodegeneration, proteasome, aggregation, protein misfolding, medicine, Myocyte, Humans, Cell Line, Transformed, Motor Neurons, Molecular Basis of Disease, Muscle Cells, Superoxide Dismutase, nutritional and metabolic diseases, Original Articles, musculoskeletal system, Muscle atrophy, Cell biology, nervous system diseases, Proteasome, chemistry, nervous system, Cell culture, Immunology, Mutation, medicine.symptom, Proteasome Inhibitors
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::6b09d29e6ac99dfe4242b7bc01f78cbbTest
http://hdl.handle.net/11577/3177789Test