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1دورية أكاديمية
المؤلفون: Ng, Leo Ct, Harris, Brandon J, Larmore, Megan, Ta, My C, Vien, Thuy N, Tokars, Valerie L, Yarov-Yarovoy, Vladimir, DeCaen, Paul G
المصدر: EMBO reports. 24(7)
مصطلحات موضوعية: Animals, Humans, Mice, Calcium Channels, Receptors, Cell Surface, Signal Transduction, Ion Transport, Mutation, Transient Receptor Potential Channels, TRPP Cation Channels, TRP channels, calcium, polycystic kidney disease, polycystins, structural biology, Genetics, Kidney Disease, Polycystic Kidney Disease, Underpinning research, Aetiology, 1.1 Normal biological development and functioning, 2.1 Biological and endogenous factors, Biochemistry and Cell Biology, Developmental Biology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/5c83c26rTest
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2دورية أكاديمية
المؤلفون: Akbari, Masaw, West, Jonathan D, Doerr, Nicholas, Kipp, Kevin R, Marhamati, Neda, Vuong, Sabrina, Wang, Yidi, Rinschen, Markus M, Talbot, Jeffrey J, Wessely, Oliver, Weimbs, Thomas
المصدر: Proceedings of the National Academy of Sciences of the United States of America. 119(30)
مصطلحات موضوعية: Biochemistry and Cell Biology, Biomedical and Clinical Sciences, Biological Sciences, Congenital Structural Anomalies, Kidney Disease, Polycystic Kidney Disease, Pediatric, 5.1 Pharmaceuticals, Development of treatments and therapeutic interventions, Renal and urogenital, Animals, Disease Models, Animal, Disease Progression, Enzyme Activation, Fingolimod Hydrochloride, Humans, Mice, Polycystic Kidney, Autosomal Dominant, Protein Kinase C, TRPP Cation Channels, polycystic kidney disease, polycystin-1, protein kinase C ζ
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/0rw4q0ckTest
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3دورية أكاديمية
المؤلفون: Friend, Brian D, Schneider, Kami Wolfe, Garrington, Timothy, Truscott, Laurel, Martinez‐Agosto, Julian A, Venick, Robert S, Chambers, Eileen Tsai, Weng, Patricia, Farmer, Douglas G, Chang, Vivian Y, Federman, Noah
المصدر: Molecular Genetics & Genomic Medicine. 7(7)
مصطلحات موضوعية: Biological Sciences, Medicinal and Biomolecular Chemistry, Chemical Sciences, Genetics, Kidney Disease, Rare Diseases, Clinical Research, Pediatric, Cancer, Polycystic Kidney Disease, Digestive Diseases, Liver Disease, Aetiology, 2.1 Biological and endogenous factors, Renal and urogenital, Adolescent, Child, Female, Genetic Predisposition to Disease, Humans, Infant, Male, Neoplasms, Polycystic Kidney Diseases, Receptors, Cell Surface, TRPP Cation Channels, genetic predisposition, genetic sequencing, malignancy, polycystic kidney disease, Clinical Sciences, Medicinal and biomolecular chemistry
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/36x4x5tvTest
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4دورية أكاديمية
المؤلفون: Trott, Josephine F, Hwang, Vicki J, Ishimaru, Tatsuto, Chmiel, Kenneth J, Zhou, Julie X, Shim, Kyuhwan, Stewart, Benjamin J, Mahjoub, Moe R, Jen, Kuang-Yu, Barupal, Dinesh K, Li, Xiaogang, Weiss, Robert H
المصدر: American Journal of Physiology. Renal physiology. 315(6)
مصطلحات موضوعية: Pediatric, Congenital Structural Anomalies, Kidney Disease, Polycystic Kidney Disease, 2.1 Biological and endogenous factors, Aetiology, Cancer, Animals, Arginine, Argininosuccinate Synthase, Cell Proliferation, Cells, Cultured, Disease Models, Animal, Energy Metabolism, Female, Genetic Predisposition to Disease, Humans, Kidney, Male, Metabolomics, Mice, Knockout, Phenotype, Polycystic Kidney, Autosomal Dominant, Receptors, Cell Surface, Signal Transduction, TRPP Cation Channels, arginine, cystogenesis, metabolic reprogramming, Physiology, Clinical Sciences, Medical Physiology, Urology & Nephrology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/2th4z137Test
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5دورية أكاديمية
المؤلفون: Ma, Shenghong, Guan, Kun-Liang
المصدر: Genes & Development. 32(11-12)
مصطلحات موضوعية: Biological Sciences, Biomedical and Clinical Sciences, Genetics, Pediatric, Congenital Structural Anomalies, Polycystic Kidney Disease, Kidney Disease, Aetiology, 2.1 Biological and endogenous factors, Renal and urogenital, Adaptor Proteins, Signal Transducing, Animals, Cell Cycle Proteins, Mice, Mutation, Phosphoproteins, Polycystic Kidney Diseases, Polycystic Kidney, Autosomal Dominant, Signal Transduction, TRPP Cation Channels, YAP-Signaling Proteins, rhoA GTP-Binding Protein, 3D culture, ADPKD, Hippo signaling, RhoA signaling, YAP/TAZ, c-Myc, Medical and Health Sciences, Psychology and Cognitive Sciences, Developmental Biology, Biological sciences, Biomedical and clinical sciences, Psychology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/8805c3h4Test
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6دورية أكاديمية
المؤلفون: Hwang, Vicki J, Zhou, Xia, Chen, Xiaonan, Trott, Josephine, Abu Aboud, Omran, Shim, Kyuhwan, Dionne, Lai Kuan, Chmiel, Kenneth J, Senapedis, William, Baloglu, Erkan, Mahjoub, Moe R, Li, Xiaogang, Weiss, Robert H
المصدر: Kidney International. 92(4)
مصطلحات موضوعية: Biomedical and Clinical Sciences, Clinical Sciences, Congenital Structural Anomalies, Pediatric, Kidney Disease, Polycystic Kidney Disease, 5.1 Pharmaceuticals, Development of treatments and therapeutic interventions, Renal and urogenital, Cancer, Acrylamides, Aminopyridines, Animals, Apoptosis, Cell Proliferation, Cytokines, Disease Models, Animal, Drug Evaluation, Preclinical, Epithelial Cells, Female, Humans, Kidney, Male, Mice, Mice, Transgenic, NAD, Nicotinamide Phosphoribosyltransferase, Organ Culture Techniques, Phosphorylation, Polycystic Kidney, Autosomal Dominant, Receptors, Cell Surface, Signal Transduction, TRPP Cation Channels, beta Catenin, p21-Activated Kinases, ADPKD, apoptosis, signaling, Urology & Nephrology, Clinical sciences
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/61q1n6m1Test
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7دورية أكاديمية
المؤلفون: Truscott, Laurel, Gell, Joanna, Chang, Vivian Y, Lee, Hane, Strom, Samuel P, Pillai, Rex, Sisk, Anthony, Martinez‐Agosto, Julian A, Anderson, Martin, Federman, Noah
المصدر: Pediatric Blood & Cancer. 64(1)
مصطلحات موضوعية: Reproductive Medicine, Biomedical and Clinical Sciences, Urologic Diseases, Cancer, Polycystic Kidney Disease, Genetics, Kidney Disease, Pediatric, Aetiology, 2.1 Biological and endogenous factors, Renal and urogenital, Adolescent, Antineoplastic Combined Chemotherapy Protocols, Female, Humans, Male, Mutation, Neoplasms, Germ Cell and Embryonal, Pedigree, Phenotype, Polycystic Kidney, Autosomal Dominant, Prognosis, TRPP Cation Channels, Testicular Neoplasms, PKD1, exome sequencing, familial testicular germ cell tumor, Clinical Sciences, Oncology and Carcinogenesis, Paediatrics and Reproductive Medicine, Oncology & Carcinogenesis, Oncology and carcinogenesis, Paediatrics
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/2nj7m074Test
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8دورية أكاديمية
المؤلفون: Doerr, Nicholas, Wang, Yidi, Kipp, Kevin R, Liu, Guangyi, Benza, Jesse J, Pletnev, Vladimir, Pavlov, Tengis S, Staruschenko, Alexander, Mohieldin, Ashraf M, Takahashi, Maki, Nauli, Surya M, Weimbs, Thomas
المصدر: PLOS ONE. 11(8)
مصطلحات موضوعية: Biochemistry and Cell Biology, Medical Physiology, Biomedical and Clinical Sciences, Biological Sciences, Kidney Disease, Pediatric, Congenital Structural Anomalies, Polycystic Kidney Disease, Aetiology, 2.1 Biological and endogenous factors, Underpinning research, 1.1 Normal biological development and functioning, Renal and urogenital, Generic health relevance, Amino Acid Motifs, Animals, Binding Sites, CHO Cells, Calcium, Calmodulin, Cilia, Cricetulus, Cytoplasm, Cytosol, Dogs, HEK293 Cells, Humans, Kidney, Madin Darby Canine Kidney Cells, Mice, Mutation, Myosin Heavy Chains, Pectinidae, Polycystic Kidney, Autosomal Dominant, Protein Domains, STAT3 Transcription Factor, Signal Transduction, TRPP Cation Channels, Transcription Factor AP-1, General Science & Technology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/7pn0w1cgTest
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9
المصدر: Clinical Science (London, England : 1979)
مصطلحات موضوعية: Epithelial sodium channel, TRPV4, TRPP Cation Channels, Fibrocystin, Electrolyte transport, Receptors, Cell Surface, Kidney, Molecular Bases of Health & Disease, Transient receptor potential channel, Polycystic Kidney Disease, Polycystic kidney disease, Medicine, Animals, Humans, Review Articles, Polycystic Kidney, Autosomal Recessive, Renal Physiology, Ion Transport, biology, business.industry, Purinergic receptor, Membrane Transport Proteins, General Medicine, Purinergic signalling, Water-Electrolyte Balance, medicine.disease, Polycystic Kidney, Autosomal Dominant, Cell biology, medicine.anatomical_structure, Ion channels, Mutation, biology.protein, Cell Membranes, Excitation & Transport, business, purinergic signaling
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::5a7b96f4ab345e1f5ec1120fa70518cfTest
http://europepmc.org/articles/PMC8589009Test -
10
المؤلفون: Peter C. Harris, Hao Ding, Linda Xiaoyan Li, Xiaogang Li, Junwei Yang
المصدر: Nature Communications, Vol 12, Iss 1, Pp 1-18 (2021)
Nature Communicationsمصطلحات موضوعية: 0301 basic medicine, Nephrology, General Physics and Astronomy, urologic and male genital diseases, Exosomes, Kidney, Mice, 0302 clinical medicine, Polycystic kidney disease, Cyst, Cystic kidney, Multidisciplinary, Aniline Compounds, Cysts, Polycystic Kidney, Autosomal Dominant, female genital diseases and pregnancy complications, medicine.anatomical_structure, 030220 oncology & carcinogenesis, Collagen, Signal Transduction, medicine.medical_specialty, Cell biology, TRPP Cation Channels, Science, Autosomal dominant polycystic kidney disease, Biology, Exosome, Benzylidene Compounds, Models, Biological, General Biochemistry, Genetics and Molecular Biology, Article, Exocytosis, Cell Line, 03 medical and health sciences, Internal medicine, medicine, Animals, Cell Proliferation, PKD1, urogenital system, Tetraspanin 30, Epithelial Cells, General Chemistry, medicine.disease, Fibrosis, Rats, MicroRNAs, 030104 developmental biology, Gene Expression Regulation, Mutation, Cancer research
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::a4ce43e767b9d1785b400e6dc81e620aTest
https://doaj.org/article/978a2efe63ee4aecbb0e7b5a78ffde38Test