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1
المؤلفون: Hélène Prigent, Christian Devaux, Frédéric Lofaso, David Orlikowski, Gilbert Caranhac, Ghilas Boussaïd, Djillali Annane
المصدر: Journal of Neuromuscular Diseases. 4:165-168
مصطلحات موضوعية: Adult, Male, Emergency Medical Services, medicine.medical_specialty, Referral, medicine.medical_treatment, Muscular Dystrophies, 03 medical and health sciences, 0302 clinical medicine, Oxygen therapy, Health care, Emergency medical services, Humans, Medicine, Hospital Mortality, Muscular dystrophy, Hospitals, Teaching, Retrospective Studies, Cause of death, business.industry, Retrospective cohort study, medicine.disease, Hospitalization, Treatment Outcome, 030228 respiratory system, Neurology, Respiratory failure, Emergency medicine, Female, France, Neurology (clinical), Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Preliminary Data
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::6c0a880250c23a998397d1df5a693f0bTest
https://doi.org/10.3233/jnd-170212Test -
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المؤلفون: C Joussain, Hélène Prigent, C Hugeron, S. Butel, Jonathan I. Levy, Djamel Bensmail, A Brotier-Chomienne
المصدر: European Journal of Neurology. 24:497-502
مصطلحات موضوعية: Male, Sleep Wake Disorders, medicine.medical_specialty, Multiple Sclerosis, Polysomnography, Vital Capacity, Pulmonary function testing, Disability Evaluation, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, Respiratory muscle, Humans, Medicine, Respiratory function, Lung volumes, Respiratory system, Aged, Expanded Disability Status Scale, business.industry, Multiple sclerosis, Middle Aged, medicine.disease, Respiratory Muscles, Respiratory Function Tests, Cough, Wheelchairs, 030228 respiratory system, Neurology, Respiratory failure, Cardiology, Female, Neurology (clinical), Lung Volume Measurements, Respiratory Insufficiency, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::17d69e1f2ab90d80b596a6dc16c9dce9Test
https://doi.org/10.1111/ene.13231Test -
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المؤلفون: Ghilas Boussaïd, Dante Brasil Santos, Stéphane Bahrami, David Orlikowski, Sandra Pottier, Frédéric Lofaso, Isabelle Vaugier, Hélène Prigent
المصدر: Neuromuscular Disorders. 26:666-674
مصطلحات موضوعية: Adult, Male, Risk, medicine.medical_specialty, medicine.medical_treatment, Vital Capacity, Kaplan-Meier Estimate, Myotonic dystrophy, Body Mass Index, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Millimeter of mercury, Internal medicine, medicine, Humans, Myotonic Dystrophy, Prospective Studies, Occupations, Intensive care medicine, Prospective cohort study, Genetics (clinical), Proportional Hazards Models, Mechanical ventilation, Noninvasive Ventilation, business.industry, Hazard ratio, Middle Aged, medicine.disease, 030228 respiratory system, Neurology, Respiratory failure, Multivariate Analysis, Pediatrics, Perinatology and Child Health, Cohort, Linear Models, Breathing, Patient Compliance, Equipment Failure, Female, Neurology (clinical), Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::fe26af913db365a660caf01faf68af83Test
https://doi.org/10.1016/j.nmd.2016.07.014Test -
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المؤلفون: Ghassane Mroue, Isabelle Vaugier, Adam Ogna, David Orlikowski, Djillali Annane, Hélène Prigent, Maria-Antonia Quera Salva, Frédéric Lofaso
المصدر: Sleep and Breathing. 20:575-581
مصطلحات موضوعية: Adult, Male, Pediatrics, medicine.medical_specialty, Neuromuscular disease, medicine.medical_treatment, Concordance, Population, 03 medical and health sciences, 0302 clinical medicine, Oxygen therapy, medicine, Humans, Oximetry, education, Retrospective Studies, Acid-Base Equilibrium, Mechanical ventilation, education.field_of_study, business.industry, Hypoventilation, Neuromuscular Diseases, Middle Aged, medicine.disease, Circadian Rhythm, Cross-Sectional Studies, 030228 respiratory system, Otorhinolaryngology, Respiratory failure, Female, Neurology (clinical), medicine.symptom, Respiratory Insufficiency, business, Blood Gas Monitoring, Transcutaneous, Hypercapnia, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8809fe080f2fde651150efe5e587acdbTest
https://doi.org/10.1007/s11325-015-1247-2Test -
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المؤلفون: Constantinos Papadopoulos, David Orlikowski, Hélène Prigent, Arnaud Lacour, Céline Tard, Alain Furby, Julien Praline, Guilhem Solé, Jean-Yves Hogrel, Marie De Antonio, Claudio Semplicini, Joelle Deibener-Kaminsky, Pierre Kaminsky, Bruno Eymard, Nadjib Taouagh, Barbara Perniconi, Dalil Hamroun, Pascal Laforêt, G. Bassez, A.-L. Bedat-Millet, A. Behin, B. Eymard, S. Leonard-Louis, T. Stojkovic, A. Canal, V. Decostre, F. Bouhour, F. Boyer, C. Caillaud, Y. Castaing, F. Chapon, P. Cintas, I. Durieu, A. Echaniz-Laguna, L. Feasson, X. Ferrer, R. Froissart, M. Piraud, D. Germain, K. Benistan, N. Guffon-Fouilhoux, H. Journel, P. Labauge, A. Levy, A. Magot, Y. Péréon, M.-C. Minot-Myhié, A. Nadaj-Pakleza, C. Nathier, N. Pellegrini, P. Petiot, F. Lofaso, A. Dutry, D. Renard, S. Sacconi, C. Desnuelle, E. Salort-Campana, J. Pouget, V. Tiffreau, D. Vincent, F. Zagnoli
المساهمون: Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Troubles cognitifs dégénératifs et vasculaires - U 1171 - EA 1046 (TCDV), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Lille, Droit et Santé-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Unité de Recherche Pluridisciplinaire Sport, Santé, Société (URePSSS) - ULR 7369 - ULR 4488 (URePSSS), Université d'Artois (UA)-Université du Littoral Côte d'Opale (ULCO)-Université de Lille, Troubles cognitifs dégénératifs et vasculaires - U 1171 (TCDV), Université de Lille-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille)-Institut National de la Santé et de la Recherche Médicale (INSERM), Université d'Artois (UA)-Université de Lille-Université du Littoral Côte d'Opale (ULCO)
المصدر: Molecular Genetics and Metabolism
Molecular Genetics and Metabolism, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩
Molecular Genetics and Metabolism, Elsevier, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩مصطلحات موضوعية: 0301 basic medicine, Male, Pediatrics, Endocrinology, Diabetes and Metabolism, [SDV]Life Sciences [q-bio], Mesh:Walking, Walking, Mesh:Adult, Respiratory failure, Biochemistry, Late Onset Disorders, Cohort Studies, 0302 clinical medicine, Endocrinology, Mesh:alpha-Glucosidases/therapeutic use, Glycogen Storage Disease Type II, Respiration, Pompe disease, Enzyme replacement therapy, Middle Aged, 3. Good health, Diabetes and Metabolism, Mesh:Late Onset Disorders/drug therapy, Cohort, Breathing, Female, France, Mesh:Respiration, Mesh:alpha-Glucosidases/administration & dosage, Mesh:Enzyme Replacement Therapy*/adverse effects, medicine.drug, Adult, Mesh:Female, medicine.medical_specialty, congenital, hereditary, and neonatal diseases and abnormalities, Mesh:Glycogen Storage Disease Type II/drug therapy, Mesh:Male, Late onset, 03 medical and health sciences, FEV1/FVC ratio, Mesh:alpha-Glucosidases/adverse effects, Mesh:Middle Aged, Mesh:Glycogen Storage Disease Type II/physiopathology, Genetics, medicine, Humans, Mesh:Cohort Studies, Adverse effect, Molecular Biology, Alglucosidase alfa, Mesh:France, Advanced, business.industry, nutritional and metabolic diseases, alpha-Glucosidases, Surgery, Mesh:Humans, 030104 developmental biology, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::2eca040ef3e520953509b66aeb672813Test
https://hal.univ-lille.fr/hal-02369159Test -
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المؤلفون: Thomas Similowski, Valérie Attali, Jesus Gonzalez Bermejo, Vincent Meininger, Capucine Morélot-Panzini, Nathalie Guy, Tanguy Marie Laure, Christophe Perrin, Claude Desnuelle, François Salachas, Hélène Prigent, Nierat Marie-Cecile, Philippe Couratier
المصدر: 1.2 Rehabilitation and Chronic Care.
مصطلحات موضوعية: medicine.medical_specialty, Vital capacity, Randomization, business.industry, medicine.disease, Surgery, law.invention, Diaphragm pacing, Respiratory failure, Randomized controlled trial, law, Medicine, Respiratory system, Amyotrophic lateral sclerosis, business, Phrenic nerve
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_________::5da6c5903439c6d8789bf20eaf1899d2Test
https://doi.org/10.1183/13993003.congress-2016.oa270Test -
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المؤلفون: Christophe Perrin, Marie-Cécile Niérat, Thomas Similowski, Jésus Gonzalez-Bermejo, Philippe Couratier, Catherine Fargeot, Claude Desnuelle, Capucine Morélot-Panzini, Marie-Laure Tanguy, Timothée Lenglet, Gaëlle Bruneteau, Catherine Royer, Valérie Attali, Vincent Meininger, François Salachas, Nathalie Guy, Nadine Le Forestier, Pierre-François Pradat, Hélène Prigent, Fabrice Menegaux
المصدر: The Lancet. Neurology. 15(12)
مصطلحات موضوعية: Male, medicine.medical_specialty, Population, Diaphragm, Electric Stimulation Therapy, law.invention, 03 medical and health sciences, 0302 clinical medicine, Randomized controlled trial, Double-Blind Method, law, medicine, Humans, Respiratory system, education, Phrenic nerve, Aged, education.field_of_study, business.industry, Amyotrophic Lateral Sclerosis, Middle Aged, Respiration Disorders, Respiration, Artificial, Hypoventilation, Diaphragm (structural system), Surgery, Phrenic Nerve, Diaphragm pacing, 030228 respiratory system, Respiratory failure, Anesthesia, Early Termination of Clinical Trials, Female, Laparoscopy, Neurology (clinical), medicine.symptom, business, Respiratory Insufficiency, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::19a260bb434838c0442a1dfe0bf80b1bTest
https://pubmed.ncbi.nlm.nih.gov/27751535Test -
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المؤلفون: Bernard Clair, Sylvie Chevret, Djillali Annane, Raquel Guimarães-Costa, Abdallah Fayssoil, Tanya Stojkovic, Cendrine Chaffaut, Olivier Nardi, David Orlikowski, Adam Ogna, Pascal Laforêt, Karim Wahbi, Anthony Behin, Hélène Prigent, Frédéric Lofaso
المساهمون: HAL UPMC, Gestionnaire, Institut de Myologie, Université Pierre et Marie Curie - Paris 6 (UPMC)-Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Association française contre les myopathies (AFM-Téléthon)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Service de réanimation médicale[Poincaré], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Raymond Poincaré [AP-HP], Centre d’Investigation Clinique 1429 [Garches] (CIC 1429), Hôpital Raymond Poincaré [AP-HP]-Institut National de la Santé et de la Recherche Médicale (INSERM), Service de biostatistique et information médicale de l’hôpital Saint Louis (Equipe ECSTRA) (SBIM), Université Paris Diderot - Paris 7 (UPD7)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Institut national du cancer [Boulogne] (INCA)-Hopital Saint-Louis [AP-HP] (AP-HP), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Service de biochimie et de génétique moléculaire [CHU Cochin], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Cochin [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Service de Cardiologie [CHU Cochin], Service de physiologie et d'explorations fonctionnelles [CHU Raymond-Poincaré], Centre National de la Recherche Scientifique (CNRS)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Association française contre les myopathies (AFM-Téléthon)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Université Pierre et Marie Curie - Paris 6 (UPMC), Hopital Saint-Louis [AP-HP] (AP-HP), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Institut national du cancer [Boulogne] (INCA)-Université Paris Diderot - Paris 7 (UPD7)-Institut National de la Santé et de la Recherche Médicale (INSERM), Hôpital Cochin [AP-HP]
المصدر: PLoS ONE
PLoS ONE, 2016, 11 (4), pp.e0153095. ⟨10.1371/journal.pone.0153095⟩
PLoS ONE, Vol 11, Iss 4, p e0153095 (2016)
PLoS ONE, Public Library of Science, 2016, 11 (4), pp.e0153095. ⟨10.1371/journal.pone.0153095⟩مصطلحات موضوعية: Male, Heredity, Pulmonology, Genetic Linkage, Physiology, Vital Capacity, Cardiomyopathy, lcsh:Medicine, Duchenne Muscular Dystrophy, Cardiovascular Physiology, Muscular Dystrophies, 0302 clinical medicine, Medicine and Health Sciences, Medicine, Respiratory function, Respiratory system, lcsh:Science, Multidisciplinary, Ejection fraction, [SDV.MHEP] Life Sciences [q-bio]/Human health and pathology, Heart, Prognosis, Respiratory Muscles, 3. Good health, Neurology, X-Linked Traits, Sex Linkage, Cardiology, Female, Cardiomyopathies, Respiratory Insufficiency, Research Article, Adult, medicine.medical_specialty, Death Rates, Diastole, 03 medical and health sciences, Population Metrics, Respiratory Failure, Diagnostic Medicine, Internal medicine, Respiratory muscle, Sarcoglycanopathies, Genetics, Humans, Demography, Clinical Genetics, Population Biology, business.industry, lcsh:R, Biology and Life Sciences, Arrhythmias, Cardiac, medicine.disease, Surgery, 030228 respiratory system, Respiratory failure, Muscular Dystrophies, Limb-Girdle, Heart failure, People and Places, lcsh:Q, business, Physiological Processes, Sleep, 030217 neurology & neurosurgery, [SDV.MHEP]Life Sciences [q-bio]/Human health and pathology, Ejection Fraction
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::be31212f679c614f55c1df3526b92aebTest
https://hal.sorbonne-universite.fr/hal-01323875Test -
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المؤلفون: Leire Santisteban, Florian Kunst, L. Falaize, M. Lejaille, Hélène Prigent, Frédéric Lofaso, Isabelle Vaugier, Caroline Hugeron
المصدر: 1.2 Rehabilitation and Chronic Care.
مصطلحات موضوعية: education.field_of_study, medicine.medical_specialty, business.industry, Maximal Respiratory Pressures, Population, medicine.disease, Pulmonary function testing, Functional residual capacity, Respiratory failure, medicine, Physical therapy, Respiratory function, Lung volumes, business, education, Spinal cord injury
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_________::1d1293978124ad0b38dc55856b0f5209Test
https://doi.org/10.1183/13993003.congress-2015.pa3704Test -
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المؤلفون: Sylvie Chevret, Djillali Annane, Xavier Ambrosi, Abdallah Fayssoil, Frédéric Lofaso, Bernard Clair, Laure Lamothe, Cendrine Chaffaut, David Orlikowski, Adam Ogna, Olivier Nardi, Hélène Prigent
المصدر: Medicine
مصطلحات موضوعية: Duchenne muscular dystrophy, Adult, Cardiac function curve, medicine.medical_specialty, Adolescent, Heart Diseases, pneumothorax, medicine.medical_treatment, Diastole, Observational Study, heart failure, mechanical ventilation, 030204 cardiovascular system & hematology, Doppler echocardiography, Cohort Studies, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, medicine, echocardiography, Humans, Cumulative incidence, Tidal volume, Retrospective Studies, Mechanical ventilation, Ejection fraction, medicine.diagnostic_test, business.industry, respiratory failure, Heart, General Medicine, Respiration, Artificial, Echocardiography, Doppler, 3. Good health, Muscular Dystrophy, Duchenne, 030228 respiratory system, Becker muscular dystrophy, Spirometry, Breathing, Cardiology, Respiratory Insufficiency, business, Research Article
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::68d427f49de85ab74305f67346be1e09Test
https://doi.org/10.1097/md.0000000000011381Test