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المؤلفون: Tiepolo, T, Angelin, A, Palma, E., Sabatelli, P, Merlini, L, Nicolosi, L, Finetti, Francesca, Braghetta, P, Vuagniaux, G, Dumont, Jm, Baldari, Cosima, Bonaldo, P, Bernardi, P.
مصطلحات موضوعية: Ullrich congenital muscular dystrophy, Apoptosis, Collagen Type VI, Biology, Cyclophilins, Jurkat Cells, Mice, Muscular Diseases, Collagen VI, medicine, Animals, Humans, Mitochondria, Muscular dystrophy, Knockout mice, Muscle, Skeletal, Cyclophilin, Pharmacology, Mice, Knockout, cyclophilin, mitochondria, immunosuppression, Dose-Response Relationship, Drug, Bethlem myopathy, Skeletal muscle, medicine.disease, Molecular biology, Research Papers, Calcineurin, medicine.anatomical_structure, Biochemistry, Mitochondrial permeability transition pore, Cyclosporine
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::6a48991584c2e290ab4ff9dc50b46ab1Test
http://hdl.handle.net/11577/2441067Test -
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المؤلفون: Daniele Capitanio, Manuela Moriggi, Sara De Palma, Dario Bizzotto, Sibilla Molon, Enrica Torretta, Chiara Fania, Paolo Bonaldo, Cecilia Gelfi, Paola Braghetta
المساهمون: Capitanio, D, Moriggi, M, De Palma, S, Bizzotto, D, Molon, S, Torretta, E, Fania, C, Bonaldo, P, Gelfi, C, Braghetta, P
المصدر: Frontiers in Molecular Neuroscience, Vol 10 (2017)
Frontiers in Molecular Neuroscienceمصطلحات موضوعية: 0301 basic medicine, medicine.medical_specialty, Connective tissue, Aging muscle proteome, Autophagy, Collagen VI, Lipotoxicity, Skeletal muscle, Molecular Biology, Cellular and Molecular Neuroscience, Biology, lcsh:RC321-571, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, medicine, Glycolysis, lcsh:Neurosciences. Biological psychiatry. Neuropsychiatry, Original Research, Diaphragm (structural system), Fatty acid synthase, 030104 developmental biology, medicine.anatomical_structure, Endocrinology, biology.protein, 030217 neurology & neurosurgery, Neuroscience
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::09167f3588639099f864753ff596f882Test
http://hdl.handle.net/11577/3252786Test -
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المؤلفون: Tania Tiepolo, Nadir M. Maraldi, Patrizia Sabatelli, Paolo Bernardi, Luciano Merlini, Paolo Bonaldo, Paola Braghetta, Alessandra Ferlini, Alessandra Zamparelli, Alessia Angelin
المساهمون: Merlini L, Angelin A, Tiepolo T, Braghetta P, Sabatelli P, Zamparelli A, Ferlini A, Maraldi NM, Bonaldo P, Bernardi P.
المصدر: Proceedings of the National Academy of Sciences. 105:5225-5229
مصطلحات موضوعية: Mitochondria, Muscular dystrophy, Apoptosis, Adult, Pathology, medicine.medical_specialty, mitochondria, muscular dystrophy, Ullrich congenital muscular dystrophy, Biopsy, Collagen Type VI, Biology, Mice, Muscular Diseases, Collagen VI, Cyclosporin a, medicine, Animals, Humans, Myocyte, Child, Mice, Knockout, Multidisciplinary, Bethlem myopathy, Skeletal muscle, Anatomy, Biological Sciences, Middle Aged, medicine.disease, medicine.anatomical_structure, Cyclosporine, ITGA7
وصف الملف: STAMPA
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d64e8f124f25dcaadbba87435a3ed800Test
https://doi.org/10.1073/pnas.0800962105Test