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1دورية أكاديمية
المؤلفون: Bidault, Guillaume, Garcia, Marie, Capeau, Jacqueline, Morichon, Romain, Vigouroux, Corinne, Béreziat, Véronique
المساهمون: Unité de Recherche sur les Maladies Cardiovasculaires, du Métabolisme et de la Nutrition = Research Unit on Cardiovascular and Metabolic Diseases (ICAN), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU)-Institut de Cardiométabolisme et Nutrition = Institute of Cardiometabolism and Nutrition CHU Pitié Salpêtrière (IHU ICAN), CHU Pitié-Salpêtrière AP-HP, Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU)-CHU Pitié-Salpêtrière AP-HP, Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), Centre de Recherche Saint-Antoine (CRSA), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU), Cytométrie et Imagerie Saint-Antoine (CISA), Unité Mixte de Service d'Imagerie et de Cytométrie CHU Saint-Antoine (UMS LUMIC), Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU), Sorbonne Université (SU), CHU Saint-Antoine AP-HP, ANR-15-RHUS-0003,CARMMA,Role de la sénescence du tissu adipeux dans les co-morbidités des pathologies métaboliques(2015)
المصدر: ISSN: 2073-4409 ; Cells ; https://hal.sorbonne-universite.fr/hal-02879665Test ; Cells, 2020, 9 (5), pp.1201. ⟨10.3390/cells9051201⟩.
مصطلحات موضوعية: Hutchinson–Gilford progeria syndrome, LMNA, aging, atherosclerosis, endothelial dysfunction, inflammation, lamin A, prenylation, progerin, Hutchinson-Gilford progeria syndrome, [SDV.BBM.GTP]Life Sciences [q-bio]/Biochemistry, Molecular Biology/Genomics [q-bio.GN], [SDV.BC.BC]Life Sciences [q-bio]/Cellular Biology/Subcellular Processes [q-bio.SC], [SDV.MHEP.EM]Life Sciences [q-bio]/Human health and pathology/Endocrinology and metabolism
العلاقة: info:eu-repo/semantics/altIdentifier/pmid/32408587; hal-02879665; https://hal.sorbonne-universite.fr/hal-02879665Test; https://hal.sorbonne-universite.fr/hal-02879665/documentTest; https://hal.sorbonne-universite.fr/hal-02879665/file/cells-09-01201.pdfTest; PUBMED: 32408587; PUBMEDCENTRAL: PMC7290406
الإتاحة: https://doi.org/10.3390/cells9051201Test
https://hal.sorbonne-universite.fr/hal-02879665Test
https://hal.sorbonne-universite.fr/hal-02879665/documentTest
https://hal.sorbonne-universite.fr/hal-02879665/file/cells-09-01201.pdfTest -
2دورية أكاديمية
المؤلفون: Magda R. Hamczyk, Vicente Andrés
المصدر: Nucleus, Vol 10, Iss 1, Pp 48-54 (2019)
مصطلحات موضوعية: atherosclerosis, hutchinson-gilford progeria syndrome, lamin a, progerin, vascular smooth muscle cells, Genetics, QH426-470, Cytology, QH573-671
وصف الملف: electronic resource
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3دورية أكاديمية
مصطلحات موضوعية: rare diseases, Hutchinson–Gilford progeria syndrome (HGPS), progeria, progerin, lamin A, Química orgánica (Química), 2306 Química Orgánica
الوقت: 547
وصف الملف: application/pdf
العلاقة: (PRF 2016-65); (PID2019-106279RBI00); https://doi.org/10.3390Test/ ijms22137190; https://hdl.handle.net/20.500.14352/7471Test
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4دورية أكاديمية
المؤلفون: Jon Macicior, Beatriz Marcos-Ramiro, Silvia Ortega-Gutiérrez
المصدر: International Journal of Molecular Sciences; Volume 22; Issue 13; Pages: 7190
مصطلحات موضوعية: rare diseases, Hutchinson–Gilford progeria syndrome (HGPS), progeria, progerin, lamin A
جغرافية الموضوع: agris
وصف الملف: application/pdf
العلاقة: Molecular Pathology, Diagnostics, and Therapeutics; https://dx.doi.org/10.3390/ijms22137190Test
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5دورية أكاديمية
المؤلفون: Guillaume Bidault, Marie Garcia, Jacqueline Capeau, Romain Morichon, Corinne Vigouroux, Véronique Béréziat
المصدر: Cells; Volume 9; Issue 5; Pages: 1201
مصطلحات موضوعية: Hutchinson–Gilford progeria syndrome, LMNA, progerin, lamin A, atherosclerosis, endothelial dysfunction, inflammation, prenylation, aging
وصف الملف: application/pdf
العلاقة: Cell Nuclei: Function, Transport and Receptors; https://dx.doi.org/10.3390/cells9051201Test
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6دورية أكاديمية
المؤلفون: Hamczyk, Magda R., Andres, Vicente
المساهمون: Ministerio de Ciencia, Innovación y Universidades (España), Unión Europea. Fondo Europeo de Desarrollo Regional (FEDER/ERDF), Progeria Research Foundation, Fundación La Marató TV3, Fundación ProCNIC, Instituto de Salud Carlos III
مصطلحات موضوعية: Atherosclerosis, Hutchinson-Gilford progeria syndrome, lamin A, progerin, vascular smooth muscle cells
العلاقة: https://doi.org/10.1080/19491034.2019.1589359Test; info:eu-repo/grantAgreement/ES/FJCI-2017-33299; info:eu-repo/grantAgreement/ES/AC16/00091; info:eu-repo/grantAgreement/ES/AC17/00067; info:eu-repo/grantAgreement/ES/SAF2016-79490-R; info:eu-repo/grantAgreement/ES/SEV-2015-0505; Nucleus. 2019; 10(1):28-34; http://hdl.handle.net/20.500.12105/7404Test; Nucleus (Austin, Tex.)
الإتاحة: https://doi.org/20.500.12105/7404Test
https://doi.org/10.1080/19491034.2019.1589359Test
https://hdl.handle.net/20.500.12105/7404Test -
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المؤلفون: Vicente Andrés, Magda R. Hamczyk
المساهمون: Ministerio de Ciencia, Innovación y Universidades (España), European Regional Development Fund (ERDF/FEDER), Progeria Research Foundation, Fundacio La Marato, Fundación ProCNIC, Instituto de Salud Carlos III
المصدر: Nucleus, Vol 10, Iss 1, Pp 48-54 (2019)
Nucleus
Repisalud
Instituto de Salud Carlos III (ISCIII)
Scopus
RUO. Repositorio Institucional de la Universidad de Oviedo
instnameمصطلحات موضوعية: Premature aging, congenital, hereditary, and neonatal diseases and abnormalities, Vascular smooth muscle, lcsh:QH426-470, Cellular differentiation, Disease, Muscle, Smooth, Vascular, LMNA, 03 medical and health sciences, Progeria, medicine, Animals, Humans, vascular smooth muscle cells, lcsh:QH573-671, 030304 developmental biology, lamin A, 0303 health sciences, integumentary system, business.industry, lcsh:Cytology, Extra View, 030302 biochemistry & molecular biology, nutritional and metabolic diseases, Cell Biology, medicine.disease, Progerin, Lamin Type A, Atherosclerosis, Hutchinson-Gilford progeria syndrome, lcsh:Genetics, progerin, Cancer research, atherosclerosis, business, Lamin, hutchinson-gilford progeria syndrome, lamin a
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d2f615358e3f276e90d7de7571bb59ceTest
https://doaj.org/article/f44fdf8a65c245f1b6a1e4410d172064Test -
8
المؤلفون: Silvia Ortega-Gutiérrez, Beatriz Marcos-Ramiro, Jon Macicior
المصدر: International Journal of Molecular Sciences
International Journal of Molecular Sciences, Vol 22, Iss 7190, p 7190 (2021)مصطلحات موضوعية: 0301 basic medicine, Aging, Pyridines, Review, medicine.disease_cause, chemistry.chemical_compound, 0302 clinical medicine, Piperidines, Lonafarnib, Biology (General), Hutchinson–Gilford progeria syndrome (HGPS), Spectroscopy, Cellular Senescence, Skin, Progeria, Mutation, integumentary system, rare diseases, Aging, Premature, General Medicine, Progerin, Lamin Type A, Computer Science Applications, Chemistry, Phenotype, 030220 oncology & carcinogenesis, Nuclear lamina, congenital, hereditary, and neonatal diseases and abnormalities, QH301-705.5, Context (language use), Biology, Catalysis, Inorganic Chemistry, Small Molecule Libraries, 03 medical and health sciences, medicine, Humans, Physical and Theoretical Chemistry, Molecular Biology, QD1-999, lamin A, Cell Nucleus, Nuclear Lamina, Point mutation, Organic Chemistry, Laminopathies, Química orgánica, nutritional and metabolic diseases, progeria, Fibroblasts, medicine.disease, 030104 developmental biology, chemistry, progerin, Cancer research, Lamin
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::3fb1b7093f85929d11daee5c183d56dcTest
http://europepmc.org/articles/PMC8267806Test -
9
المؤلفون: Corinne Vigouroux, Guillaume Bidault, Marie Garcia, Jacqueline Capeau, Romain Morichon, Véronique Béréziat
المساهمون: Unité de Recherche sur les Maladies Cardiovasculaires, du Métabolisme et de la Nutrition = Institute of cardiometabolism and nutrition (ICAN), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Institut National de la Santé et de la Recherche Médicale (INSERM)-CHU Pitié-Salpêtrière [AP-HP], Sorbonne Université (SU)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), Centre de Recherche Saint-Antoine (CR Saint-Antoine), Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU)-CHU Saint-Antoine [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), Cytométrie et Imagerie Saint-Antoine (CISA), Unité Mixte de Service d'Imagerie et de Cytométrie [CHU Saint-Antoine] (UMS LUMIC), Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU), Laboratoire commun de biologie et génétique moléculaires [CHU Saint-Antoine], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-CHU Saint-Antoine [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU)-Sorbonne Université (SU), Service d'Endocrinologie, diabétologie et endocrinologie de la reproduction [CHU Saint-Antoine], CHU Saint-Antoine [AP-HP], Sorbonne Université-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université-Sorbonne Université (SU), Sorbonne Université (SU), Unité de Recherche sur les Maladies Cardiovasculaires, du Métabolisme et de la Nutrition = Research Unit on Cardiovascular and Metabolic Diseases (ICAN), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU)-Institut de Cardiométabolisme et Nutrition = Institute of Cardiometabolism and Nutrition [CHU Pitié Salpêtrière] (IHU ICAN), CHU Pitié-Salpêtrière [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU)-CHU Pitié-Salpêtrière [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), Centre de Recherche Saint-Antoine (CRSA), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU), Gestionnaire, Hal Sorbonne Université
المصدر: Cells
Cells, MDPI, 2020, 9 (5), pp.1201. ⟨10.3390/cells9051201⟩
Cells, Vol 9, Iss 1201, p 1201 (2020)
Volume 9
Issue 5
Cells, 2020, 9 (5), pp.1201. ⟨10.3390/cells9051201⟩مصطلحات موضوعية: 0301 basic medicine, [SDV.BC.BC]Life Sciences [q-bio]/Cellular Biology/Subcellular Processes [q-bio.SC], 030204 cardiovascular system & hematology, endothelial dysfunction, LMNA, 0302 clinical medicine, Endothelial dysfunction, lcsh:QH301-705.5, ComputingMilieux_MISCELLANEOUS, Cells, Cultured, Cellular Senescence, [SDV.MHEP.EM] Life Sciences [q-bio]/Human health and pathology/Endocrinology and metabolism, Progeria, integumentary system, General Medicine, prenylation, [SDV.MHEP.EM]Life Sciences [q-bio]/Human health and pathology/Endocrinology and metabolism, Progerin, Lamin Type A, Coronary Vessels, Cell biology, Hutchinson-Gilford progeria syndrome, Endothelial stem cell, [SDV.BBM.GTP] Life Sciences [q-bio]/Biochemistry, Molecular Biology/Genomics [q-bio.GN], medicine.symptom, Senescence, Premature aging, congenital, hereditary, and neonatal diseases and abnormalities, Cell Nucleus Shape, Protein Prenylation, Inflammation, [SDV.BC]Life Sciences [q-bio]/Cellular Biology, Article, 03 medical and health sciences, [SDV.BBM.GTP]Life Sciences [q-bio]/Biochemistry, Molecular Biology/Genomics [q-bio.GN], [SDV.BC.BC] Life Sciences [q-bio]/Cellular Biology/Subcellular Processes [q-bio.SC], medicine, Humans, lamin A, Cell Nucleus, Hutchinson–Gilford progeria syndrome, business.industry, aging, nutritional and metabolic diseases, Endothelial Cells, medicine.disease, Oxidative Stress, 030104 developmental biology, lcsh:Biology (General), progerin, Nitric Oxide Synthase, atherosclerosis, business, DNA Damage
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d151f4a20a1b7a37fd7b9ed758bd9626Test
https://pubmed.ncbi.nlm.nih.gov/32408587Test -
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المؤلفون: Elisabeth P. Carpenter, Timothy D. Babatz, Olivia L. Sun, Wenxin Xu, Susan Michaelis, Laiyin Nie, Eric D. Spear
المصدر: The Journal of Biological Chemistry
مصطلحات موضوعية: 0301 basic medicine, Premature aging, congenital, hereditary, and neonatal diseases and abnormalities, substrate specificity, LMNA, HGPS, Hutchinson–Gilford progeria syndrome, Cleavage (embryo), Biochemistry, intramembrane proteolysis, 03 medical and health sciences, Scissile bond, MAD-B, mandibuloacral dysplasia type-B, Catalytic Domain, Consensus sequence, Humans, CAAX motif, Amino Acid Sequence, Molecular Biology, lamin A, Metalloproteinase, 030102 biochemistry & molecular biology, integumentary system, Chemistry, nutritional and metabolic diseases, Membrane Proteins, Metalloendopeptidases, progeria, protease, Cell Biology, Lamin Type A, RD, restrictive dermopathy, WT, wild-type, Transmembrane protein, Recombinant Proteins, farnesylation, Cell biology, Zinc, 030104 developmental biology, Mutation, Proteolysis, Protein farnesylation, Lamin, Research Article
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::7bea20a97fc97ca35dd6bb9fdba9238bTest
https://pubmed.ncbi.nlm.nih.gov/33293369Test