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المؤلفون: Charlotte Dupé, Claire Lefeuvre, Guilhem Solé, Anthony Behin, Corinne Pottier, Fanny Duval, Robert‐Yves Carlier, Hélène Prigent, Jean Lacau St Guily, Azzeddine Arrassi, Nadjib Taouagh, Dalil Hamroun, Guillaume Nicolas, Pascal Laforêt
المصدر: European journal of neurologyREFERENCES. 29(7)
مصطلحات موضوعية: Aged, 80 and over, Male, Neurology, Glycogen Storage Disease Type II, Macroglossia, Humans, Female, alpha-Glucosidases, Neurology (clinical), Aged, Retrospective Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::a2e3d3e9684a23fd9e23c3f7a7d5491cTest
https://pubmed.ncbi.nlm.nih.gov/35302691Test -
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المصدر: Muscle & Nerve. 63:327-335
مصطلحات موضوعية: Adult, Male, 0301 basic medicine, medicine.medical_specialty, Physiology, Neural Conduction, Phrenic nerve conduction, Diagnostic accuracy, 030105 genetics & heredity, Diaphragmatic paralysis, Sensitivity and Specificity, Pulmonary function testing, 03 medical and health sciences, Cellular and Molecular Neuroscience, Esophagus, 0302 clinical medicine, Predictive Value of Tests, Physiology (medical), Internal medicine, mental disorders, Pressure, Transducers, Pressure, medicine, Respiratory muscle, Humans, Aged, Retrospective Studies, business.industry, Electrodiagnosis, Stomach, Transdiaphragmatic pressure, Middle Aged, Respiratory Paralysis, Predictive value, Respiratory Muscles, Respiratory Function Tests, Highly sensitive, Phrenic Nerve, Cardiology, Female, Neurology (clinical), business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::5e12c907a7cc46300b897a91d49927b4Test
https://doi.org/10.1002/mus.27144Test -
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المؤلفون: Pascal Crenn, Tanya Stojkovic, Dominique Mompoint, Hélène Prigent, David Orlikowski, Helge Amthor, Cendrine Chaffaut, Laure Lamothe, Susana Quijano Roy, Guillaume Bassez, Sylvie Chevret, Djillali Annane, Bernard Clair, Pascal Laforêt, Frédéric Lofaso, Robert Carlier, Paris Meng, Adam Ogna, Anthony Behin, Abdallah Fayssoil, Bruno Eymard
المصدر: Journal of Neuromuscular Diseases. 6:55-64
مصطلحات موضوعية: Adult, Male, 0301 basic medicine, Vital capacity, medicine.medical_specialty, Adolescent, Duchenne muscular dystrophy, Diaphragm, Diaphragmatic breathing, Muscle disorder, Pulmonary function testing, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, Respiratory muscle, Humans, Medicine, Child, Retrospective Studies, Ultrasonography, business.industry, Respiration, Organ Size, Middle Aged, musculoskeletal system, medicine.disease, Respiration, Artificial, Diaphragm (structural system), Muscular Dystrophy, Duchenne, Cross-Sectional Studies, 030104 developmental biology, Neurology, Cardiology, Median body, Neurology (clinical), business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::54576aaa09a075dc125c0779852f4c1bTest
https://doi.org/10.3233/jnd-180326Test -
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المؤلفون: Tanya Stojkovic, Helge Amthor, David Orlikowski, Hélène Prigent, Djillali Annane, Frédéric Lofaso, Stéphane Vinit, Bernard Clair, Anthony Behin, Arnaud Mansart, Dominique Mompoint, Abdallah Fayssoil, Bruno Eymard, Robert Carlier, Pascal Laforêt, Adam Ogna
المصدر: Journal of Neuromuscular Diseases
مصطلحات موضوعية: medicine.medical_specialty, Diaphragm, Respiratory pattern, Review, neuromuscular disorders, 03 medical and health sciences, 0302 clinical medicine, Respiratory muscle, Medicine, Humans, Respiratory system, Ultrasonography, business.industry, ultrasound, Ultrasound, Neuromuscular Diseases, musculoskeletal system, Pathophysiology, Diaphragm (structural system), 030228 respiratory system, Neurology, Ultrasound imaging, Neurology (clinical), Radiology, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::13c8b6d88488a2d0a3d8a4aaf8e04296Test
http://europepmc.org/articles/PMC5836400Test -
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المؤلفون: Gilbert Desmarais, Frédéric Lofaso, Dante Brasil Santos, Sandrine Cognet, Bruno Louis, L. Falaize, Hélène Prigent, Adam Ogna, David Orlikowski
المصدر: Neuromuscular Disorders. 27:518-525
مصطلحات موضوعية: Adult, Male, medicine.medical_specialty, Weakness, Neuromuscular disease, Diaphragm, Diaphragmatic breathing, Stimulation, Sensitivity and Specificity, 03 medical and health sciences, Esophagus, 0302 clinical medicine, Internal medicine, Pressure, medicine, Humans, Respiratory muscle weakness, Genetics (clinical), Mouth, Muscle Weakness, business.industry, Muscle weakness, Neuromuscular Diseases, Middle Aged, musculoskeletal system, medicine.disease, Nasal pressure, Respiratory Muscles, Respiratory Function Tests, Surgery, Phrenic Nerve, Inhalation, 030228 respiratory system, Neurology, Mouth pressure, Pediatrics, Perinatology and Child Health, Cardiology, Female, Neurology (clinical), medicine.symptom, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::e478c38ee86be07bebba5ffba6e3c629Test
https://doi.org/10.1016/j.nmd.2017.01.022Test -
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المؤلفون: Hélène Prigent, Christian Devaux, Frédéric Lofaso, David Orlikowski, Gilbert Caranhac, Ghilas Boussaïd, Djillali Annane
المصدر: Journal of Neuromuscular Diseases. 4:165-168
مصطلحات موضوعية: Adult, Male, Emergency Medical Services, medicine.medical_specialty, Referral, medicine.medical_treatment, Muscular Dystrophies, 03 medical and health sciences, 0302 clinical medicine, Oxygen therapy, Health care, Emergency medical services, Humans, Medicine, Hospital Mortality, Muscular dystrophy, Hospitals, Teaching, Retrospective Studies, Cause of death, business.industry, Retrospective cohort study, medicine.disease, Hospitalization, Treatment Outcome, 030228 respiratory system, Neurology, Respiratory failure, Emergency medicine, Female, France, Neurology (clinical), Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Preliminary Data
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::6c0a880250c23a998397d1df5a693f0bTest
https://doi.org/10.3233/jnd-170212Test -
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المؤلفون: C Joussain, Hélène Prigent, C Hugeron, S. Butel, Jonathan I. Levy, Djamel Bensmail, A Brotier-Chomienne
المصدر: European Journal of Neurology. 24:497-502
مصطلحات موضوعية: Male, Sleep Wake Disorders, medicine.medical_specialty, Multiple Sclerosis, Polysomnography, Vital Capacity, Pulmonary function testing, Disability Evaluation, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, Respiratory muscle, Humans, Medicine, Respiratory function, Lung volumes, Respiratory system, Aged, Expanded Disability Status Scale, business.industry, Multiple sclerosis, Middle Aged, medicine.disease, Respiratory Muscles, Respiratory Function Tests, Cough, Wheelchairs, 030228 respiratory system, Neurology, Respiratory failure, Cardiology, Female, Neurology (clinical), Lung Volume Measurements, Respiratory Insufficiency, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::17d69e1f2ab90d80b596a6dc16c9dce9Test
https://doi.org/10.1111/ene.13231Test -
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المؤلفون: Ghilas Boussaïd, Dante Brasil Santos, Stéphane Bahrami, David Orlikowski, Sandra Pottier, Frédéric Lofaso, Isabelle Vaugier, Hélène Prigent
المصدر: Neuromuscular Disorders. 26:666-674
مصطلحات موضوعية: Adult, Male, Risk, medicine.medical_specialty, medicine.medical_treatment, Vital Capacity, Kaplan-Meier Estimate, Myotonic dystrophy, Body Mass Index, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Millimeter of mercury, Internal medicine, medicine, Humans, Myotonic Dystrophy, Prospective Studies, Occupations, Intensive care medicine, Prospective cohort study, Genetics (clinical), Proportional Hazards Models, Mechanical ventilation, Noninvasive Ventilation, business.industry, Hazard ratio, Middle Aged, medicine.disease, 030228 respiratory system, Neurology, Respiratory failure, Multivariate Analysis, Pediatrics, Perinatology and Child Health, Cohort, Linear Models, Breathing, Patient Compliance, Equipment Failure, Female, Neurology (clinical), Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::fe26af913db365a660caf01faf68af83Test
https://doi.org/10.1016/j.nmd.2016.07.014Test -
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المؤلفون: Ghassane Mroue, Isabelle Vaugier, Adam Ogna, David Orlikowski, Djillali Annane, Hélène Prigent, Maria-Antonia Quera Salva, Frédéric Lofaso
المصدر: Sleep and Breathing. 20:575-581
مصطلحات موضوعية: Adult, Male, Pediatrics, medicine.medical_specialty, Neuromuscular disease, medicine.medical_treatment, Concordance, Population, 03 medical and health sciences, 0302 clinical medicine, Oxygen therapy, medicine, Humans, Oximetry, education, Retrospective Studies, Acid-Base Equilibrium, Mechanical ventilation, education.field_of_study, business.industry, Hypoventilation, Neuromuscular Diseases, Middle Aged, medicine.disease, Circadian Rhythm, Cross-Sectional Studies, 030228 respiratory system, Otorhinolaryngology, Respiratory failure, Female, Neurology (clinical), medicine.symptom, Respiratory Insufficiency, business, Blood Gas Monitoring, Transcutaneous, Hypercapnia, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8809fe080f2fde651150efe5e587acdbTest
https://doi.org/10.1007/s11325-015-1247-2Test -
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المؤلفون: Frédéric Lofaso, Ghilas Boussaïd, Dante Brasil Santos, David Orlikowski, Hélène Prigent, Sandrine Butel, Anthony Behin, Nadège Letilly, Tanya Stojkovic
المصدر: Neuromuscular Disorders. 25:632-639
مصطلحات موضوعية: Adult, Male, Vital Capacity, Pulmonary function testing, Young Adult, Respiratory muscle, Humans, Medicine, Facioscapulohumeral muscular dystrophy, Respiratory function, Lung volumes, Respiratory system, Genetics (clinical), Aged, Aged, 80 and over, Muscle Weakness, business.industry, Sleep apnea, Middle Aged, medicine.disease, Muscular Dystrophy, Facioscapulohumeral, Respiratory Muscles, Neurology, Respiratory failure, Exhalation, Anesthesia, Pediatrics, Perinatology and Child Health, Female, Neurology (clinical), Respiratory Insufficiency, business, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::fb0055b7e65dfb83dab92716d43e7f8aTest
https://doi.org/10.1016/j.nmd.2015.04.011Test