المؤلفون: Clarisse Billon, Salma Adham, Natalia Hernandez Poblete, Anne Legrand, Michael Frank, Laurent Chiche, Stephane Zuily, Karelle Benistan, Laurent Savale, Khaoula Zaafrane-Khachnaoui, Anne-Claire Brehin, Laurence Bal, Tiffany Busa, Mélanie Fradin, Chloé Quelin, Bertrand Chesneau, Denis Wahl, Patricia Fergelot, Cyril Goizet, Tristan Mirault, Xavier Jeunemaitre, Juliette Albuisson, Bordeaux-cohort collaborators

المساهمون: Hôpital Européen Georges Pompidou [APHP] (HEGP), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpitaux Universitaires Paris Ouest - Hôpitaux Universitaires Île de France Ouest (HUPO), Paris-Centre de Recherche Cardiovasculaire (PARCC (UMR_S 970/ U970)), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpitaux Universitaires Paris Ouest - Hôpitaux Universitaires Île de France Ouest (HUPO)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpitaux Universitaires Paris Ouest - Hôpitaux Universitaires Île de France Ouest (HUPO)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Université Paris Cité (UPCité), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Hôpital Saint-Éloi [Montpellier], Centre Hospitalier Régional Universitaire [Montpellier] (CHRU Montpellier), Hôpital Pellegrin, CHU Bordeaux [Bordeaux]-Groupe hospitalier Pellegrin, CHU Bordeaux [Bordeaux], Laboratoire Maladies Rares: Génétique et Métabolisme (Bordeaux) (U1211 INSERM/MRGM), Université de Bordeaux (UB)-Groupe hospitalier Pellegrin-Institut National de la Santé et de la Recherche Médicale (INSERM), CHU Pitié-Salpêtrière [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), Université Paris-Sorbonne (UP4), Défaillance Cardiovasculaire Aiguë et Chronique (DCAC), Centre Hospitalier Régional Universitaire de Nancy (CHRU Nancy)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Lorraine (UL), Centre Hospitalier Régional Universitaire de Nancy (CHRU Nancy), Hôpital Raymond Poincaré [AP-HP], Handicap neuromusculaire : Physiopathologie, Biothérapie et Pharmacologies appliquées (END-ICAP), Université de Versailles Saint-Quentin-en-Yvelines (UVSQ)-Institut National de la Santé et de la Recherche Médicale (INSERM), Adhésion et Inflammation (LAI), Aix Marseille Université (AMU)-Assistance Publique - Hôpitaux de Marseille (APHM)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Hôpital Marie-Lannelongue, Hôpital Bicêtre, Hôpital l'Archet, Génomique et Médecine Personnalisée du Cancer et des Maladies Neuropsychiatriques (GPMCND), Université de Rouen Normandie (UNIROUEN), Normandie Université (NU)-Normandie Université (NU)-Institut National de la Santé et de la Recherche Médicale (INSERM), CHU Rouen, Normandie Université (NU), Hôpital de la Timone [CHU - APHM] (TIMONE), Hôpital Sud [CHU Rennes], CHU Pontchaillou [Rennes], Centre de référence Maladies Rares CLAD-Ouest [Rennes], Centre Hospitalier Universitaire de Toulouse (CHU Toulouse), Centre Régional de Lutte contre le cancer Georges-François Leclerc [Dijon] (UNICANCER/CRLCC-CGFL), UNICANCER, Bordeaux-cohort collaborators: Anne Dieux, Fabien Labombarda, Sylvain Rheims, Odile Boute, André Vincentelli, Annick Toutain, Sylvie Odent, Gaetan Lesca, Marie Vincent, Juliette Piard, Maud Favier, Philippe Derambure, Patrick Edery, Susanne Thummler, Marion Gérard, Fanny Morice-Picard, Valérie Layet, Cécile Laroche, Laurent Pasquier, Elisabeth Sarrazin, Thierry Billette de Villemeur, Lucie Guyant-Marechal, Adham, Salma

المصدر: Orphanet Journal of Rare Diseases
Orphanet Journal of Rare Diseases, Vol 16, Iss 1, Pp 1-13 (2021)
Orphanet Journal of Rare Diseases, 2021, 16 (1), pp.504. ⟨10.1186/s13023-021-02128-1⟩

مصطلحات موضوعية: Aortic aneurysm and dissection, Research, Filamins, General Medicine, [SDV.GEN.GH] Life Sciences [q-bio]/Genetics/Human genetics, Cardiovascular anomalies, Connective tissue disorder, Ehlers–Danlos, FLNA, [SDV.GEN.GH]Life Sciences [q-bio]/Genetics/Human genetics, Periventricular Nodular Heterotopia, Connective Tissue, Medicine, Humans, Pharmacology (medical), Connective Tissue Diseases, Genetics (clinical), Retrospective Studies

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::47e429d6847fc6d37354b3efc05fdfffTest
https://doi.org/10.1186/s13023-021-02128-1Test

المؤلفون: D. Amar, Xavier Jaïs, Swanny Perrin, Olivier Sitbon, Marc Humbert, Laurent Savale, Caroline O’Connell, Gérald Simonneau, David Montani, Marie-Camille Chaumais

المصدر: Expert Opinion on Pharmacotherapy. 16:2113-2131

مصطلحات موضوعية: Pharmacology, Clinical Trials as Topic, medicine.medical_specialty, Combination therapy, business.industry, Hypertension, Pulmonary, medicine.medical_treatment, MEDLINE, Disease Management, General Medicine, Disease, medicine.disease, Pulmonary hypertension, Targeted therapy, Pharmacotherapy, Quality of Life, medicine, Humans, Pharmacology (medical), Disease management (health), Intensive care medicine, business, Endothelin Pathway, Antihypertensive Agents

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::4eaaa3fa6fdfb7271489e6d45ee95617Test
https://doi.org/10.1517/14656566.2015.1074177Test

المؤلفون: Gérald Simonneau, Laurent Savale, Olivier Sitbon, Delphine Natali, Marc Humbert, Xavier Jaïs, Laura C. Price, Marie-Camille Chaumais, David Montani

المصدر: Advances in Therapy. 26:813-825

مصطلحات موضوعية: Phosphodiesterase Inhibitors, Sildenafil, Hypertension, Pulmonary, Vasodilation, Pharmacology, Piperazines, Sildenafil Citrate, Tadalafil, chemistry.chemical_compound, Vardenafil Dihydrochloride, Humans, Medicine, Pharmacology (medical), Sulfones, Cyclic guanosine monophosphate, Triazines, business.industry, Imidazoles, General Medicine, Phosphodiesterase 5 Inhibitors, medicine.disease, Bosentan, Erectile dysfunction, chemistry, Purines, Vardenafil, cGMP-specific phosphodiesterase type 5, Pulmonary Veno-Occlusive Disease, business, Algorithms, Carbolines, medicine.drug

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8fa2faffb4f51b5796213664f58e555dTest
https://doi.org/10.1007/s12325-009-0064-zTest

المؤلفون: Athénaïs Boucly, Laurent Savale, Olivier Sitbon, Marc Humbert, Marie-Camille Chaumais, Gérald Simonneau, David Montani, Xavier Jaïs, Christophe Guignabert

المساهمون: Hypertension arterielle pulmonaire physiopathologie et innovation thérapeutique, Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre chirurgical Marie Lannelongue, Hôpital Antoine Béclère, Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Université Paris-Sud - Paris 11 (UP11), Université Paris-Sud - Paris 11 (UP11), Centre de Référence de l’Hypertension Pulmonaire Sévère [CHU Le Kremlin Bicêtre], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-AP-HP Hôpital Bicêtre (Le Kremlin-Bicêtre), Service de Pneumologie et Réanimation Respiratoire [AP-HP Hôpital Bicêtre] (DHU TORINO), AP-HP Hôpital Bicêtre (Le Kremlin-Bicêtre)-Centre de Référence de l'Hypertension Pulmonaire Sévère, Centre Chirurgical Marie Lannelongue (CCML)-Institut National de la Santé et de la Recherche Médicale (INSERM), Université Paris-Sud - Paris 11 (UP11)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Guignabert, Christophe, Centre chirurgical Marie Lannelongue-Institut National de la Santé et de la Recherche Médicale (INSERM)

المصدر: American Journal of Cardiovascular Drugs
American Journal of Cardiovascular Drugs, Springer Verlag, 2015, 15 (1), pp.13-26. ⟨10.1007/s40256-014-0095-y⟩

مصطلحات موضوعية: Vasculitis, medicine.medical_specialty, Pulmonary Circulation, Endothelium, medicine.drug_class, Hypertension, Pulmonary, [SDV]Life Sciences [q-bio], [SDV.BC]Life Sciences [q-bio]/Cellular Biology, Pharmacology, Pulmonary arterial hypertension, Models, Biological, [SDV.MHEP.PSR]Life Sciences [q-bio]/Human health and pathology/Pulmonology and respiratory tract, Muscle, Smooth, Vascular, Endothelin, law.invention, Pathogenesis, Pharmacotherapy, [SDV.MHEP.CSC]Life Sciences [q-bio]/Human health and pathology/Cardiology and cardiovascular system, law, Internal medicine, Medicine, Animals, Humans, Pharmacology (medical), Drug Interactions, Endothelial dysfunction, Antihypertensive drug, [SDV.BC] Life Sciences [q-bio]/Cellular Biology, Antihypertensive Agents, Clinical pharmacology, business.industry, Cell growth, Endothelins, General Medicine, [SDV.MHEP.CSC] Life Sciences [q-bio]/Human health and pathology/Cardiology and cardiovascular system, 3. Good health, [SDV] Life Sciences [q-bio], Endothelin receptor antagonists, Endocrinology, medicine.anatomical_structure, Practice Guidelines as Topic, Vascular resistance, [SDV.MHEP.PSR] Life Sciences [q-bio]/Human health and pathology/Pulmonology and respiratory tract, Drug Therapy, Combination, Endothelium, Vascular, Cardiology and Cardiovascular Medicine, business, Endothelin receptor, Signal Transduction

وصف الملف: application/pdf

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::5bea6ebbda559db7cadc3c6a8bf206bcTest
https://www.hal.inserm.fr/inserm-03224640Test

المؤلفون: Sven Günther, Xavier Jaïs, Gérald Simonneau, Laurent Savale, Barbara Girerd, Elise Artaud-Macari, Olivier Sitbon, David Montani, Marc Humbert, Laura C. Price, Peter Dorfmüller, Gilles Garcia, Frédéric Perros

المساهمون: BMC, Ed., Service de Pneumologie et Réanimation Respiratoire (DHU TORINO), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Bicêtre-Centre de Référence de l'Hypertension Pulmonaire Sévère, Université Paris-Sud - Paris 11 (UP11), Hypertension arterielle pulmonaire physiopathologie et innovation thérapeutique, Centre Chirurgical Marie Lannelongue (CCML)-Institut National de la Santé et de la Recherche Médicale (INSERM), Pulmonary Hypertension Service, Royal Brompton Hospital, Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre chirurgical Marie Lannelongue, Centre chirurgical Marie Lannelongue-Institut National de la Santé et de la Recherche Médicale (INSERM)

المصدر: Orphanet Journal of Rare Diseases
Orphanet Journal of Rare Diseases, BioMed Central, 2013, 8 (1), pp.97. ⟨10.1186/1750-1172-8-97⟩

مصطلحات موضوعية: medicine.medical_specialty, Heart Diseases, Ambrisentan, Hypertension, Pulmonary, Review, 030204 cardiovascular system & hematology, 03 medical and health sciences, 0302 clinical medicine, [SDV.MHEP.CSC]Life Sciences [q-bio]/Human health and pathology/Cardiology and cardiovascular system, medicine.artery, Internal medicine, Pulmonary fibrosis, medicine, Humans, Genetics(clinical), Pharmacology (medical), Lung emphysema, Genetics (clinical), Medicine(all), COPD, business.industry, Interstitial lung disease, General Medicine, medicine.disease, Pulmonary hypertension, Bosentan, [SDV.MHEP.CSC] Life Sciences [q-bio]/Human health and pathology/Cardiology and cardiovascular system, 3. Good health, 030228 respiratory system, Pulmonary artery, Cardiology, business, medicine.drug

وصف الملف: application/pdf

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::75a28336151969809ae5715216868e87Test
https://doi.org/10.1186/1750-1172-8-97Test

المؤلفون: Gérald Simonneau, Dermot S. O'Callaghan, Xavier Jaïs, Olivier Sitbon, Marc Humbert, Delphine Natali, David Montani, Florence Parent, Azzedine Yaici, Laurent Savale

المصدر: Expert opinion on pharmacotherapy. 12(10)

مصطلحات موضوعية: Ambrisentan, Endothelin A Receptor Antagonists, Hypertension, Pulmonary, Pharmacology, Mediator, Medicine, Animals, Humans, Pharmacology (medical), Receptor, Antihypertensive Agents, Sulfonamides, Phenylpropionates, Endothelin receptor antagonist, business.industry, Bosentan, General Medicine, Pathophysiology, Endothelin B Receptor Antagonists, Pyridazines, Endothelin receptor, business, Antagonism, medicine.drug

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::5a40615e2cdbf54ac00d0c4612211170Test
https://pubmed.ncbi.nlm.nih.gov/21504371Test