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المؤلفون: Caroline Ovaert, Sylvie Tuffery-Giraud, Sarah Leonard-Louis, Anthony Béhin, Sophie Guillaumont, Maximilien Sochala, Emmanuelle Campana-Salort, Frédérique Audic, Michèle Mayer, Damien Bonnet, Raul Juntas Morales, Mireille Cossée, Isabelle Desguerre, Christophe Meune, Pascal Laforêt, Rabah Ben Yaou, Brigitte Chabrol, Djillali Annane, David Orlikowski, François Godart, Malika Saadi, Helge Amthor, Tanya Stojkovic, Ulrike Walther-Louvier, Frédéric Lofaso, Pascal Amedro, Raphaël Porcher, Céline Tard, Claire Delcourte, Vincent Tiffreau, Karim Wahbi, Christine Barnerias, Guillaume Bassez, Bertrand Fontaine, Arnaud Isapof, Gregoire De La Villeon, Guy Vaksmann, François Rivier, Denis Duboc, Henri Marc Bécane, Philippe Ravaud, Hélène Prigent, Emmanuelle Jaillette, Abdallah Fayssoil, Bruno Eymard
المساهمون: Université de Lille, Univ. Artois, Univ. Littoral Côte d’Opale, Unité de Recherche Pluridisciplinaire Sport, Santé, Société (URePSSS) - ULR 7369 - ULR 4488 [URePSSS], Centre de Recherche Épidémiologie et Statistique Sorbonne Paris Cité (CRESS (U1153 / UMR_A_1125 / UMR_S_1153)), Conservatoire National des Arts et Métiers [CNAM] (CNAM)-Université Sorbonne Paris Cité (USPC)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Paris (UP)-Institut National de Recherche pour l’Agriculture, l’Alimentation et l’Environnement (INRAE), Physiologie & médecine expérimentale du Cœur et des Muscles [U 1046] (PhyMedExp), Université de Montpellier (UM)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Centre Hospitalier Régional Universitaire [Montpellier] (CHRU Montpellier), Conservatoire National des Arts et Métiers [CNAM] (CNAM), HESAM Université - Communauté d'universités et d'établissements Hautes écoles Sorbonne Arts et métiers université (HESAM)-HESAM Université - Communauté d'universités et d'établissements Hautes écoles Sorbonne Arts et métiers université (HESAM)-Université Sorbonne Paris Cité (USPC)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Université Paris Cité (UPCité)-Institut National de Recherche pour l’Agriculture, l’Alimentation et l’Environnement (INRAE), CHU Necker - Enfants Malades [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Handicap neuromusculaire : Physiopathologie, Biothérapie et Pharmacologies appliquées (END-ICAP), Université de Versailles Saint-Quentin-en-Yvelines (UVSQ)-Institut National de la Santé et de la Recherche Médicale (INSERM), Marseille medical genetics - Centre de génétique médicale de Marseille (MMG), Aix Marseille Université (AMU)-Institut National de la Santé et de la Recherche Médicale (INSERM), Département de génétique médicale [Hôpital de la Timone - APHM], Aix Marseille Université (AMU)-Assistance Publique - Hôpitaux de Marseille (APHM)- Hôpital de la Timone [CHU - APHM] (TIMONE)-Institut National de la Santé et de la Recherche Médicale (INSERM), Clinique de pneumologie [CHRU Lille], Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Montpellier (UM)-Centre National de la Recherche Scientifique (CNRS), CHU Trousseau [APHP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), Unité de Recherche Pluridisciplinaire Sport, Santé, Société (URePSSS) - ULR 7369 - ULR 4488 (URePSSS), Université d'Artois (UA)-Université du Littoral Côte d'Opale (ULCO)-Université de Lille, Neurologie, maladies neuro-musculaires [Hôpital de la Timone - APHM], Aix Marseille Université (AMU)-Assistance Publique - Hôpitaux de Marseille (APHM)- Hôpital de la Timone [CHU - APHM] (TIMONE), CHU Pitié-Salpêtrière [AP-HP], Hôpital Cochin [AP-HP], Centre de recherche en Myologie – U974 SU-INSERM, Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU), Filière Neuromusculaire (FILNEMUS), Infection et inflammation (2I), Université de Montpellier (UM), Centre Hospitalier de Versailles André Mignot (CHV), Institut des Neurosciences de Montpellier (INM), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Montpellier (UM), Marqueurs cardiovasculaires en situation de stress (MASCOT (UMR_S_942 / U942)), Institut National de la Santé et de la Recherche Médicale (INSERM)-Groupe Hospitalier Saint Louis - Lariboisière - Fernand Widal [Paris], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Centre National de la Recherche Scientifique (CNRS)-Université Paris Cité (UPCité)-Université Sorbonne Paris Nord, Centre d’Investigation Clinique 1429 [Garches] (CIC 1429), Hôpital Raymond Poincaré [AP-HP]-Institut National de la Santé et de la Recherche Médicale (INSERM), Service de cardiologie Pédiatrique [Marseille], Hôpital de la Timone [CHU - APHM] (TIMONE), Hôpital Raymond Poincaré [AP-HP], Paris-Centre de Recherche Cardiovasculaire (PARCC (UMR_S 970/ U970)), Hôpital Européen Georges Pompidou [APHP] (HEGP), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpitaux Universitaires Paris Ouest - Hôpitaux Universitaires Île de France Ouest (HUPO)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpitaux Universitaires Paris Ouest - Hôpitaux Universitaires Île de France Ouest (HUPO)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Université Paris Cité (UPCité)
المصدر: European Heart Journal
European Heart Journal, Oxford University Press (OUP): Policy B, 2021, ⟨10.1093/eurheartj/ehab054⟩
European Heart Journal, 2021, ⟨10.1093/eurheartj/ehab054⟩مصطلحات موضوعية: Duchenne muscular dystrophy, medicine.medical_specialty, [SDV]Life Sciences [q-bio], Cardiomyopathy, Angiotensin-Converting Enzyme Inhibitors, Heart failure, Angiotensin-converting enzyme inhibitors, 030204 cardiovascular system & hematology, Lower risk, Ventricular Function, Left, Angiotensin Receptor Antagonists, 03 medical and health sciences, 0302 clinical medicine, [SDV.MHEP.CSC]Life Sciences [q-bio]/Human health and pathology/Cardiology and cardiovascular system, Internal medicine, medicine, Humans, Registries, cardiovascular diseases, 030212 general & internal medicine, Medical prescription, Child, ComputingMilieux_MISCELLANEOUS, Heart Failure, biology, business.industry, Proportional hazards model, Hazard ratio, Angiotensin-converting enzyme, medicine.disease, Confidence interval, 3. Good health, Muscular Dystrophy, Duchenne, Treatment Outcome, Child, Preschool, biology.protein, Cardiology and Cardiovascular Medicine, business, cardiomyopathy
وصف الملف: application/octet-stream
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::f84a4eeaae527cf105631ef315b278f7Test
https://doi.org/10.1093/eurheartj/ehab054Test -
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المؤلفون: Sylvie Chevret, Paris Meng, Pascal Crenn, Cendrine Chaffaut, Bernard Clair, Adam Ogna, Djillali Annane, Hélène Prigent, David Orlikowski, Pascal Laforêt, Abdallah Fayssoil, Frédéric Lofaso
المصدر: Pediatric pulmonologyREFERENCES. 56(7)
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Adult, medicine.medical_specialty, Adolescent, medicine.medical_treatment, Duchenne muscular dystrophy, Nutritional Status, Sepsis, 03 medical and health sciences, Young Adult, 0302 clinical medicine, Swallowing, 030225 pediatrics, Internal medicine, medicine, Respiratory muscle, Humans, Respiratory function, Respiratory system, Mechanical ventilation, Univariate analysis, business.industry, Swallowing Disorders, medicine.disease, Prognosis, Respiratory Muscles, Deglutition, Muscular Dystrophy, Duchenne, 030228 respiratory system, Pediatrics, Perinatology and Child Health, Median body, business, Deglutition Disorders
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8475a904e8b59112dc2bbfbc3621000cTest
https://pubmed.ncbi.nlm.nih.gov/33939888Test -
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المؤلفون: Pascal Crenn, Tanya Stojkovic, Dominique Mompoint, Hélène Prigent, David Orlikowski, Helge Amthor, Cendrine Chaffaut, Laure Lamothe, Susana Quijano Roy, Guillaume Bassez, Sylvie Chevret, Djillali Annane, Bernard Clair, Pascal Laforêt, Frédéric Lofaso, Robert Carlier, Paris Meng, Adam Ogna, Anthony Behin, Abdallah Fayssoil, Bruno Eymard
المصدر: Journal of Neuromuscular Diseases. 6:55-64
مصطلحات موضوعية: Adult, Male, 0301 basic medicine, Vital capacity, medicine.medical_specialty, Adolescent, Duchenne muscular dystrophy, Diaphragm, Diaphragmatic breathing, Muscle disorder, Pulmonary function testing, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, Respiratory muscle, Humans, Medicine, Child, Retrospective Studies, Ultrasonography, business.industry, Respiration, Organ Size, Middle Aged, musculoskeletal system, medicine.disease, Respiration, Artificial, Diaphragm (structural system), Muscular Dystrophy, Duchenne, Cross-Sectional Studies, 030104 developmental biology, Neurology, Cardiology, Median body, Neurology (clinical), business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::54576aaa09a075dc125c0779852f4c1bTest
https://doi.org/10.3233/jnd-180326Test -
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المؤلفون: Michel Petitjean, Matthieu Lacombe, David Orlikowski, Line Falaize, Didier Pradon, Frédéric Lofaso, Henri Meric, Hélène Prigent
المصدر: Chronic Respiratory Disease. 14:110-116
مصطلحات موضوعية: Adult, Pulmonary and Respiratory Medicine, Time Factors, Adolescent, Respiratory rate, Duchenne muscular dystrophy, Vital Capacity, Respiratory physiology, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Respiratory Rate, medicine, Respiratory muscle, Humans, Plethysmograph, 030212 general & internal medicine, Thoracic Wall, Tidal volume, Muscle Weakness, business.industry, Muscle weakness, medicine.disease, Respiration, Artificial, Original Papers, Respiratory Muscles, Muscular Dystrophy, Duchenne, Plethysmography, 030228 respiratory system, Anesthesia, Rapid shallow breathing index, Respiratory Mechanics, medicine.symptom, Respiratory Insufficiency, business
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::b13063f65132d1a0c7c920c29b4ff758Test
https://doi.org/10.1177/1479972316674413Test -
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المؤلفون: Hélène Prigent, Frédéric Lofaso, Ghilas Boussaïd, David Orlikowski, Dante Brasil Santos, Isabelle Vaugier
المصدر: Respiratory Care. 61:1530-1535
مصطلحات موضوعية: Male, Pulmonary and Respiratory Medicine, Maximal Respiratory Pressures, Neuromuscular disease, Duchenne muscular dystrophy, Vital Capacity, Critical Care and Intensive Care Medicine, Maximum expiratory pressure, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Forced Expiratory Volume, Tidal Volume, Humans, Medicine, Respiratory function, Lung volumes, Respiratory system, Lung, Retrospective Studies, Noninvasive Ventilation, business.industry, Respiration, Oxygen Inhalation Therapy, General Medicine, medicine.disease, Muscular Dystrophy, Duchenne, Treatment Outcome, 030228 respiratory system, Respiratory failure, Anesthesia, Female, Noninvasive ventilation, Lung Volume Measurements, Respiratory Insufficiency, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::81f86296d9bb3dd4be8ade9aaefa6990Test
https://doi.org/10.4187/respcare.04703Test -
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المؤلفون: Sandra Pottier, David Orlikowski, Dante Brasil Santos, Ghilas Boussaïd, Stéphane Bahrami, Isabelle Vaugier, Frédéric Lofaso, Hélène Prigent
المصدر: Respiratory Medicine. 115:26-32
مصطلحات موضوعية: Adult, Male, Pulmonary and Respiratory Medicine, medicine.medical_specialty, Adolescent, medicine.medical_treatment, Duchenne muscular dystrophy, Young Adult, 03 medical and health sciences, Tracheostomy, 0302 clinical medicine, Internal medicine, medicine, Humans, Non-invasive ventilation, In patient, Prospective Studies, Child, Prospective cohort study, Heart Failure, Mechanical ventilation, Noninvasive Ventilation, business.industry, Hazard ratio, medicine.disease, Respiration, Artificial, Survival Analysis, Surgery, Muscular Dystrophy, Duchenne, 030228 respiratory system, Child, Preschool, Breathing, France, Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Respiratory care
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::36040a89e19e8fe1b90d18ca594586d1Test
https://doi.org/10.1016/j.rmed.2016.04.009Test -
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المؤلفون: Bernard Clair, Sylvie Chevret, Djillali Annane, Raquel Guimarães-Costa, Abdallah Fayssoil, Tanya Stojkovic, Cendrine Chaffaut, Olivier Nardi, David Orlikowski, Adam Ogna, Pascal Laforêt, Karim Wahbi, Anthony Behin, Hélène Prigent, Frédéric Lofaso
المساهمون: HAL UPMC, Gestionnaire, Institut de Myologie, Université Pierre et Marie Curie - Paris 6 (UPMC)-Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Association française contre les myopathies (AFM-Téléthon)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Service de réanimation médicale[Poincaré], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Raymond Poincaré [AP-HP], Centre d’Investigation Clinique 1429 [Garches] (CIC 1429), Hôpital Raymond Poincaré [AP-HP]-Institut National de la Santé et de la Recherche Médicale (INSERM), Service de biostatistique et information médicale de l’hôpital Saint Louis (Equipe ECSTRA) (SBIM), Université Paris Diderot - Paris 7 (UPD7)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Institut national du cancer [Boulogne] (INCA)-Hopital Saint-Louis [AP-HP] (AP-HP), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Service de biochimie et de génétique moléculaire [CHU Cochin], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Cochin [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Service de Cardiologie [CHU Cochin], Service de physiologie et d'explorations fonctionnelles [CHU Raymond-Poincaré], Centre National de la Recherche Scientifique (CNRS)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Association française contre les myopathies (AFM-Téléthon)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Université Pierre et Marie Curie - Paris 6 (UPMC), Hopital Saint-Louis [AP-HP] (AP-HP), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Institut national du cancer [Boulogne] (INCA)-Université Paris Diderot - Paris 7 (UPD7)-Institut National de la Santé et de la Recherche Médicale (INSERM), Hôpital Cochin [AP-HP]
المصدر: PLoS ONE
PLoS ONE, 2016, 11 (4), pp.e0153095. ⟨10.1371/journal.pone.0153095⟩
PLoS ONE, Vol 11, Iss 4, p e0153095 (2016)
PLoS ONE, Public Library of Science, 2016, 11 (4), pp.e0153095. ⟨10.1371/journal.pone.0153095⟩مصطلحات موضوعية: Male, Heredity, Pulmonology, Genetic Linkage, Physiology, Vital Capacity, Cardiomyopathy, lcsh:Medicine, Duchenne Muscular Dystrophy, Cardiovascular Physiology, Muscular Dystrophies, 0302 clinical medicine, Medicine and Health Sciences, Medicine, Respiratory function, Respiratory system, lcsh:Science, Multidisciplinary, Ejection fraction, [SDV.MHEP] Life Sciences [q-bio]/Human health and pathology, Heart, Prognosis, Respiratory Muscles, 3. Good health, Neurology, X-Linked Traits, Sex Linkage, Cardiology, Female, Cardiomyopathies, Respiratory Insufficiency, Research Article, Adult, medicine.medical_specialty, Death Rates, Diastole, 03 medical and health sciences, Population Metrics, Respiratory Failure, Diagnostic Medicine, Internal medicine, Respiratory muscle, Sarcoglycanopathies, Genetics, Humans, Demography, Clinical Genetics, Population Biology, business.industry, lcsh:R, Biology and Life Sciences, Arrhythmias, Cardiac, medicine.disease, Surgery, 030228 respiratory system, Respiratory failure, Muscular Dystrophies, Limb-Girdle, Heart failure, People and Places, lcsh:Q, business, Physiological Processes, Sleep, 030217 neurology & neurosurgery, [SDV.MHEP]Life Sciences [q-bio]/Human health and pathology, Ejection Fraction
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::be31212f679c614f55c1df3526b92aebTest
https://hal.sorbonne-universite.fr/hal-01323875Test -
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المؤلفون: David Orlikowski, Hélène Prigent, J. Nardi, Sylvie Chevret, Djillali Annane, Adam Ogna, Maria-Antonia Quera Salva, Frédéric Lofaso
المصدر: 2.2 Noninvasive Ventilatory Support.
مصطلحات موضوعية: Mechanical ventilation, business.industry, medicine.medical_treatment, Duchenne muscular dystrophy, Hazard ratio, Follow up studies, medicine.disease, Hypoxemia, Hypoventilation, Anesthesia, Oxygen therapy, Medicine, medicine.symptom, business, Hypercapnia
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_________::b90fd9b3e8012e8ff716210deebb5dd7Test
https://doi.org/10.1183/13993003.congress-2015.oa4781Test -
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المؤلفون: Hélène Prigent, David Orlikowski, Djillali Annane, Frédéric Lofaso, Line Falaize, Nicolas Terzi, Michèle Lejaille
المصدر: Neuromuscular Disorders. 20:493-498
مصطلحات موضوعية: Adult, Male, medicine.medical_specialty, medicine.medical_treatment, Duchenne muscular dystrophy, Electromyography, Intermittent Positive-Pressure Ventilation, Young Adult, 03 medical and health sciences, Tracheostomy, 0302 clinical medicine, Bolus (medicine), stomatognathic system, Swallowing, otorhinolaryngologic diseases, medicine, Humans, Plethysmograph, Prospective Studies, Muscular dystrophy, Genetics (clinical), Mechanical ventilation, medicine.diagnostic_test, business.industry, digestive, oral, and skin physiology, medicine.disease, Deglutition, Surgery, Muscular Dystrophy, Duchenne, Plethysmography, 030228 respiratory system, Neurology, Anesthesia, Pediatrics, Perinatology and Child Health, Respiratory Mechanics, Female, Neurology (clinical), Deglutition Disorders, business, Airway, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::c4c71f7d2c17e0deeae10380e891acccTest
https://doi.org/10.1016/j.nmd.2010.05.009Test -
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المؤلفون: David Orlikowski, Hélène Prigent, Betty Garnier, Julie Nardi, François Lebargy, Maria-Antonia Quera-Salva, Frédéric Lofaso
المصدر: Sleep medicine. 13(8)
مصطلحات موضوعية: Adult, Male, Sleep Wake Disorders, Duchenne muscular dystrophy, medicine.medical_treatment, Polysomnography, Carbamide Peroxide, Tracheostomy, Respiration, Medicine, Humans, Urea, Prospective Studies, Muscular dystrophy, Prospective cohort study, Mechanical ventilation, Noninvasive Ventilation, Inhalation, medicine.diagnostic_test, business.industry, General Medicine, Carbon Dioxide, medicine.disease, Respiration, Artificial, Peroxides, Muscular Dystrophy, Duchenne, Anesthesia, Base excess, Female, business, Respiratory Insufficiency
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::c2db0bc89de8fb0da172f5e009bbeaf9Test
https://pubmed.ncbi.nlm.nih.gov/22841025Test