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المؤلفون: Lorena Del Amo Castrillo, Aurélien Boré, Isabelle Vaugier, Line Falaize, Hélène Prigent, Frédéric Lofaso, Matthieu Lacombe, David Orlikowski
المصدر: Respiratory Care. 64:255-261
مصطلحات موضوعية: Adult, Male, Pulmonary and Respiratory Medicine, Respiratory Therapy, Neuromuscular disease, medicine.medical_treatment, Home Care Services, Hospital-Based, Peak Expiratory Flow Rate, Critical Care and Intensive Care Medicine, Continuous mandatory ventilation, Cohort Studies, Inspiratory Capacity, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Tidal Volume, Respiratory muscle, Humans, Medicine, Tidal volume, Aged, Retrospective Studies, Mechanical ventilation, Ventilators, Mechanical, business.industry, Neuromuscular Diseases, General Medicine, Middle Aged, Prognosis, medicine.disease, Respiration, Artificial, Treatment Outcome, Cough, 030228 respiratory system, Respiratory failure, Intermittent positive pressure breathing, Anesthesia, Female, France, Respiratory Insufficiency, business
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::2b7cba80dfbe23f245439d7fafc05103Test
https://doi.org/10.4187/respcare.06259Test -
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المؤلفون: Hélène Prigent, Christian Devaux, Frédéric Lofaso, David Orlikowski, Gilbert Caranhac, Ghilas Boussaïd, Djillali Annane
المصدر: Journal of Neuromuscular Diseases. 4:165-168
مصطلحات موضوعية: Adult, Male, Emergency Medical Services, medicine.medical_specialty, Referral, medicine.medical_treatment, Muscular Dystrophies, 03 medical and health sciences, 0302 clinical medicine, Oxygen therapy, Health care, Emergency medical services, Humans, Medicine, Hospital Mortality, Muscular dystrophy, Hospitals, Teaching, Retrospective Studies, Cause of death, business.industry, Retrospective cohort study, medicine.disease, Hospitalization, Treatment Outcome, 030228 respiratory system, Neurology, Respiratory failure, Emergency medicine, Female, France, Neurology (clinical), Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Preliminary Data
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::6c0a880250c23a998397d1df5a693f0bTest
https://doi.org/10.3233/jnd-170212Test -
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المؤلفون: C Joussain, Hélène Prigent, C Hugeron, S. Butel, Jonathan I. Levy, Djamel Bensmail, A Brotier-Chomienne
المصدر: European Journal of Neurology. 24:497-502
مصطلحات موضوعية: Male, Sleep Wake Disorders, medicine.medical_specialty, Multiple Sclerosis, Polysomnography, Vital Capacity, Pulmonary function testing, Disability Evaluation, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, Respiratory muscle, Humans, Medicine, Respiratory function, Lung volumes, Respiratory system, Aged, Expanded Disability Status Scale, business.industry, Multiple sclerosis, Middle Aged, medicine.disease, Respiratory Muscles, Respiratory Function Tests, Cough, Wheelchairs, 030228 respiratory system, Neurology, Respiratory failure, Cardiology, Female, Neurology (clinical), Lung Volume Measurements, Respiratory Insufficiency, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::17d69e1f2ab90d80b596a6dc16c9dce9Test
https://doi.org/10.1111/ene.13231Test -
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المؤلفون: Hélène Prigent, Frédéric Lofaso, Ghilas Boussaïd, David Orlikowski, Dante Brasil Santos, Isabelle Vaugier
المصدر: Respiratory Care. 61:1530-1535
مصطلحات موضوعية: Male, Pulmonary and Respiratory Medicine, Maximal Respiratory Pressures, Neuromuscular disease, Duchenne muscular dystrophy, Vital Capacity, Critical Care and Intensive Care Medicine, Maximum expiratory pressure, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Forced Expiratory Volume, Tidal Volume, Humans, Medicine, Respiratory function, Lung volumes, Respiratory system, Lung, Retrospective Studies, Noninvasive Ventilation, business.industry, Respiration, Oxygen Inhalation Therapy, General Medicine, medicine.disease, Muscular Dystrophy, Duchenne, Treatment Outcome, 030228 respiratory system, Respiratory failure, Anesthesia, Female, Noninvasive ventilation, Lung Volume Measurements, Respiratory Insufficiency, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::81f86296d9bb3dd4be8ade9aaefa6990Test
https://doi.org/10.4187/respcare.04703Test -
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المؤلفون: Ghilas Boussaïd, Dante Brasil Santos, Stéphane Bahrami, David Orlikowski, Sandra Pottier, Frédéric Lofaso, Isabelle Vaugier, Hélène Prigent
المصدر: Neuromuscular Disorders. 26:666-674
مصطلحات موضوعية: Adult, Male, Risk, medicine.medical_specialty, medicine.medical_treatment, Vital Capacity, Kaplan-Meier Estimate, Myotonic dystrophy, Body Mass Index, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Millimeter of mercury, Internal medicine, medicine, Humans, Myotonic Dystrophy, Prospective Studies, Occupations, Intensive care medicine, Prospective cohort study, Genetics (clinical), Proportional Hazards Models, Mechanical ventilation, Noninvasive Ventilation, business.industry, Hazard ratio, Middle Aged, medicine.disease, 030228 respiratory system, Neurology, Respiratory failure, Multivariate Analysis, Pediatrics, Perinatology and Child Health, Cohort, Linear Models, Breathing, Patient Compliance, Equipment Failure, Female, Neurology (clinical), Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::fe26af913db365a660caf01faf68af83Test
https://doi.org/10.1016/j.nmd.2016.07.014Test -
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المؤلفون: Ghassane Mroue, Isabelle Vaugier, Adam Ogna, David Orlikowski, Djillali Annane, Hélène Prigent, Maria-Antonia Quera Salva, Frédéric Lofaso
المصدر: Sleep and Breathing. 20:575-581
مصطلحات موضوعية: Adult, Male, Pediatrics, medicine.medical_specialty, Neuromuscular disease, medicine.medical_treatment, Concordance, Population, 03 medical and health sciences, 0302 clinical medicine, Oxygen therapy, medicine, Humans, Oximetry, education, Retrospective Studies, Acid-Base Equilibrium, Mechanical ventilation, education.field_of_study, business.industry, Hypoventilation, Neuromuscular Diseases, Middle Aged, medicine.disease, Circadian Rhythm, Cross-Sectional Studies, 030228 respiratory system, Otorhinolaryngology, Respiratory failure, Female, Neurology (clinical), medicine.symptom, Respiratory Insufficiency, business, Blood Gas Monitoring, Transcutaneous, Hypercapnia, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8809fe080f2fde651150efe5e587acdbTest
https://doi.org/10.1007/s11325-015-1247-2Test -
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المؤلفون: Frédéric Lofaso, Ghilas Boussaïd, Dante Brasil Santos, David Orlikowski, Hélène Prigent, Sandrine Butel, Anthony Behin, Nadège Letilly, Tanya Stojkovic
المصدر: Neuromuscular Disorders. 25:632-639
مصطلحات موضوعية: Adult, Male, Vital Capacity, Pulmonary function testing, Young Adult, Respiratory muscle, Humans, Medicine, Facioscapulohumeral muscular dystrophy, Respiratory function, Lung volumes, Respiratory system, Genetics (clinical), Aged, Aged, 80 and over, Muscle Weakness, business.industry, Sleep apnea, Middle Aged, medicine.disease, Muscular Dystrophy, Facioscapulohumeral, Respiratory Muscles, Neurology, Respiratory failure, Exhalation, Anesthesia, Pediatrics, Perinatology and Child Health, Female, Neurology (clinical), Respiratory Insufficiency, business, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::fb0055b7e65dfb83dab92716d43e7f8aTest
https://doi.org/10.1016/j.nmd.2015.04.011Test -
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المؤلفون: Constantinos Papadopoulos, David Orlikowski, Hélène Prigent, Arnaud Lacour, Céline Tard, Alain Furby, Julien Praline, Guilhem Solé, Jean-Yves Hogrel, Marie De Antonio, Claudio Semplicini, Joelle Deibener-Kaminsky, Pierre Kaminsky, Bruno Eymard, Nadjib Taouagh, Barbara Perniconi, Dalil Hamroun, Pascal Laforêt, G. Bassez, A.-L. Bedat-Millet, A. Behin, B. Eymard, S. Leonard-Louis, T. Stojkovic, A. Canal, V. Decostre, F. Bouhour, F. Boyer, C. Caillaud, Y. Castaing, F. Chapon, P. Cintas, I. Durieu, A. Echaniz-Laguna, L. Feasson, X. Ferrer, R. Froissart, M. Piraud, D. Germain, K. Benistan, N. Guffon-Fouilhoux, H. Journel, P. Labauge, A. Levy, A. Magot, Y. Péréon, M.-C. Minot-Myhié, A. Nadaj-Pakleza, C. Nathier, N. Pellegrini, P. Petiot, F. Lofaso, A. Dutry, D. Renard, S. Sacconi, C. Desnuelle, E. Salort-Campana, J. Pouget, V. Tiffreau, D. Vincent, F. Zagnoli
المساهمون: Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Troubles cognitifs dégénératifs et vasculaires - U 1171 - EA 1046 (TCDV), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Lille, Droit et Santé-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Unité de Recherche Pluridisciplinaire Sport, Santé, Société (URePSSS) - ULR 7369 - ULR 4488 (URePSSS), Université d'Artois (UA)-Université du Littoral Côte d'Opale (ULCO)-Université de Lille, Troubles cognitifs dégénératifs et vasculaires - U 1171 (TCDV), Université de Lille-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille)-Institut National de la Santé et de la Recherche Médicale (INSERM), Université d'Artois (UA)-Université de Lille-Université du Littoral Côte d'Opale (ULCO)
المصدر: Molecular Genetics and Metabolism
Molecular Genetics and Metabolism, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩
Molecular Genetics and Metabolism, Elsevier, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩مصطلحات موضوعية: 0301 basic medicine, Male, Pediatrics, Endocrinology, Diabetes and Metabolism, [SDV]Life Sciences [q-bio], Mesh:Walking, Walking, Mesh:Adult, Respiratory failure, Biochemistry, Late Onset Disorders, Cohort Studies, 0302 clinical medicine, Endocrinology, Mesh:alpha-Glucosidases/therapeutic use, Glycogen Storage Disease Type II, Respiration, Pompe disease, Enzyme replacement therapy, Middle Aged, 3. Good health, Diabetes and Metabolism, Mesh:Late Onset Disorders/drug therapy, Cohort, Breathing, Female, France, Mesh:Respiration, Mesh:alpha-Glucosidases/administration & dosage, Mesh:Enzyme Replacement Therapy*/adverse effects, medicine.drug, Adult, Mesh:Female, medicine.medical_specialty, congenital, hereditary, and neonatal diseases and abnormalities, Mesh:Glycogen Storage Disease Type II/drug therapy, Mesh:Male, Late onset, 03 medical and health sciences, FEV1/FVC ratio, Mesh:alpha-Glucosidases/adverse effects, Mesh:Middle Aged, Mesh:Glycogen Storage Disease Type II/physiopathology, Genetics, medicine, Humans, Mesh:Cohort Studies, Adverse effect, Molecular Biology, Alglucosidase alfa, Mesh:France, Advanced, business.industry, nutritional and metabolic diseases, alpha-Glucosidases, Surgery, Mesh:Humans, 030104 developmental biology, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::2eca040ef3e520953509b66aeb672813Test
https://hal.univ-lille.fr/hal-02369159Test -
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المؤلفون: Michelle Lejaille, Hélène Prigent, Aurélien Boré, Lorena Del Amo Castrillo, David Orlikowski, Matthieu Lacombe, Isabelle Vaugier, Frédéric Lofaso, David Chapeau, Eric Horvat
المصدر: Respiration. 88:215-222
مصطلحات موضوعية: Adult, Male, Pulmonary and Respiratory Medicine, Insufflation, Respiratory Therapy, Muscular Dystrophies, Muscular Atrophy, Spinal, Random order, Young Adult, Respiratory muscle, Humans, Medicine, In patient, Intermittent Positive-Pressure Breathing, Aged, Cross-Over Studies, business.industry, Neuromuscular Diseases, Middle Aged, Respiratory Paralysis, Treatment Outcome, Cough, Respiratory failure, Intermittent positive pressure breathing, Anesthesia, Breathing, Female, Exsufflation, Respiratory Insufficiency, business, Metabolism, Inborn Errors
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::02f29f66c7a6df04fdd9daa4143e4394Test
https://doi.org/10.1159/000364911Test -
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المؤلفون: Thomas Similowski, Valérie Attali, Jesus Gonzalez Bermejo, Vincent Meininger, Capucine Morélot-Panzini, Nathalie Guy, Tanguy Marie Laure, Christophe Perrin, Claude Desnuelle, François Salachas, Hélène Prigent, Nierat Marie-Cecile, Philippe Couratier
المصدر: 1.2 Rehabilitation and Chronic Care.
مصطلحات موضوعية: medicine.medical_specialty, Vital capacity, Randomization, business.industry, medicine.disease, Surgery, law.invention, Diaphragm pacing, Respiratory failure, Randomized controlled trial, law, Medicine, Respiratory system, Amyotrophic lateral sclerosis, business, Phrenic nerve
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_________::5da6c5903439c6d8789bf20eaf1899d2Test
https://doi.org/10.1183/13993003.congress-2016.oa270Test