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1
المؤلفون: Sandra Pottier, David Orlikowski, Dante Brasil Santos, Ghilas Boussaïd, Stéphane Bahrami, Isabelle Vaugier, Frédéric Lofaso, Hélène Prigent
المصدر: Respiratory Medicine. 115:26-32
مصطلحات موضوعية: Adult, Male, Pulmonary and Respiratory Medicine, medicine.medical_specialty, Adolescent, medicine.medical_treatment, Duchenne muscular dystrophy, Young Adult, 03 medical and health sciences, Tracheostomy, 0302 clinical medicine, Internal medicine, medicine, Humans, Non-invasive ventilation, In patient, Prospective Studies, Child, Prospective cohort study, Heart Failure, Mechanical ventilation, Noninvasive Ventilation, business.industry, Hazard ratio, medicine.disease, Respiration, Artificial, Survival Analysis, Surgery, Muscular Dystrophy, Duchenne, 030228 respiratory system, Child, Preschool, Breathing, France, Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Respiratory care
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::36040a89e19e8fe1b90d18ca594586d1Test
https://doi.org/10.1016/j.rmed.2016.04.009Test -
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المؤلفون: Constantinos Papadopoulos, David Orlikowski, Hélène Prigent, Arnaud Lacour, Céline Tard, Alain Furby, Julien Praline, Guilhem Solé, Jean-Yves Hogrel, Marie De Antonio, Claudio Semplicini, Joelle Deibener-Kaminsky, Pierre Kaminsky, Bruno Eymard, Nadjib Taouagh, Barbara Perniconi, Dalil Hamroun, Pascal Laforêt, G. Bassez, A.-L. Bedat-Millet, A. Behin, B. Eymard, S. Leonard-Louis, T. Stojkovic, A. Canal, V. Decostre, F. Bouhour, F. Boyer, C. Caillaud, Y. Castaing, F. Chapon, P. Cintas, I. Durieu, A. Echaniz-Laguna, L. Feasson, X. Ferrer, R. Froissart, M. Piraud, D. Germain, K. Benistan, N. Guffon-Fouilhoux, H. Journel, P. Labauge, A. Levy, A. Magot, Y. Péréon, M.-C. Minot-Myhié, A. Nadaj-Pakleza, C. Nathier, N. Pellegrini, P. Petiot, F. Lofaso, A. Dutry, D. Renard, S. Sacconi, C. Desnuelle, E. Salort-Campana, J. Pouget, V. Tiffreau, D. Vincent, F. Zagnoli
المساهمون: Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Troubles cognitifs dégénératifs et vasculaires - U 1171 - EA 1046 (TCDV), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Lille, Droit et Santé-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Unité de Recherche Pluridisciplinaire Sport, Santé, Société (URePSSS) - ULR 7369 - ULR 4488 (URePSSS), Université d'Artois (UA)-Université du Littoral Côte d'Opale (ULCO)-Université de Lille, Troubles cognitifs dégénératifs et vasculaires - U 1171 (TCDV), Université de Lille-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille)-Institut National de la Santé et de la Recherche Médicale (INSERM), Université d'Artois (UA)-Université de Lille-Université du Littoral Côte d'Opale (ULCO)
المصدر: Molecular Genetics and Metabolism
Molecular Genetics and Metabolism, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩
Molecular Genetics and Metabolism, Elsevier, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩مصطلحات موضوعية: 0301 basic medicine, Male, Pediatrics, Endocrinology, Diabetes and Metabolism, [SDV]Life Sciences [q-bio], Mesh:Walking, Walking, Mesh:Adult, Respiratory failure, Biochemistry, Late Onset Disorders, Cohort Studies, 0302 clinical medicine, Endocrinology, Mesh:alpha-Glucosidases/therapeutic use, Glycogen Storage Disease Type II, Respiration, Pompe disease, Enzyme replacement therapy, Middle Aged, 3. Good health, Diabetes and Metabolism, Mesh:Late Onset Disorders/drug therapy, Cohort, Breathing, Female, France, Mesh:Respiration, Mesh:alpha-Glucosidases/administration & dosage, Mesh:Enzyme Replacement Therapy*/adverse effects, medicine.drug, Adult, Mesh:Female, medicine.medical_specialty, congenital, hereditary, and neonatal diseases and abnormalities, Mesh:Glycogen Storage Disease Type II/drug therapy, Mesh:Male, Late onset, 03 medical and health sciences, FEV1/FVC ratio, Mesh:alpha-Glucosidases/adverse effects, Mesh:Middle Aged, Mesh:Glycogen Storage Disease Type II/physiopathology, Genetics, medicine, Humans, Mesh:Cohort Studies, Adverse effect, Molecular Biology, Alglucosidase alfa, Mesh:France, Advanced, business.industry, nutritional and metabolic diseases, alpha-Glucosidases, Surgery, Mesh:Humans, 030104 developmental biology, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::2eca040ef3e520953509b66aeb672813Test
https://hal.univ-lille.fr/hal-02369159Test -
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المؤلفون: Bruno Louis, Brigitte Fauroux, Karl Leroux, Frédéric Lofaso, Sonia Khirani, David Orlikowski, Line Falaize, Hélène Prigent
المصدر: Respiratory care. 59(7)
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Adult, medicine.medical_specialty, Time Factors, genetic structures, Respiratory rate, Critical Care and Intensive Care Medicine, Models, Biological, Electric Power Supplies, medicine, Portable ventilators, Ventilator settings, Tidal Volume, Humans, Tidal volume, Ventilators, Mechanical, business.industry, Battery (vacuum tube), General Medicine, Home Care Services, Respiration, Artificial, Surgery, Anesthesia, Breathing, business, circulatory and respiratory physiology
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::dccaadd5a7784a66729aa6234516f16aTest
https://pubmed.ncbi.nlm.nih.gov/24149669Test -
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المؤلفون: J. Boudarham, Hélène Prigent, Didier Pradon, Henri Meric, Marie-Christine Durand, Michel Petitjean, Frédéric Lofaso, Line Falaize
المصدر: Chest. 144(3)
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Thorax, Adult, Male, Weakness, medicine.medical_specialty, Diaphragm, Critical Care and Intensive Care Medicine, Diagnosis, Differential, Medicine, Humans, Diaphragmatic weakness, Phrenic nerve, Aged, Muscle Weakness, medicine.diagnostic_test, business.industry, Respiration, Reproducibility of Results, Middle Aged, Respiratory Paralysis, Electric Stimulation, Diaphragm (structural system), Surgery, Plethysmography, medicine.anatomical_structure, Anesthesia, Breathing, Abdomen, Female, medicine.symptom, Cardiology and Cardiovascular Medicine, business, Chest radiograph, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::94e55724cb5f3df004569c1341a0ff0bTest
https://pubmed.ncbi.nlm.nih.gov/23519378Test -
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المؤلفون: Pierre G. Carlier, N. Pellegrini, Pascal Laforêt, Djillali Annane, Robert Carlier, Bruno Eymard, Frédéric Lofaso, Hélène Prigent, David Orlikowski
المصدر: Neuromuscular disorders : NMD. 21(7)
مصطلحات موضوعية: Spirometry, Adult, Male, medicine.medical_specialty, Metabolic myopathy, Gastroenterology, Internal medicine, medicine, Humans, Respiratory function, Enzyme Replacement Therapy, Muscle Strength, Prospective Studies, Respiratory system, Alglucosidase alfa, Genetics (clinical), medicine.diagnostic_test, business.industry, Glycogen Storage Disease Type II, alpha-Glucosidases, Enzyme replacement therapy, Middle Aged, medicine.disease, Recombinant Proteins, Surgery, Respiratory Function Tests, Treatment Outcome, Neurology, Respiratory failure, Pediatrics, Perinatology and Child Health, Breathing, Female, Neurology (clinical), business, Respiratory Insufficiency, medicine.drug
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::eca97f5b2cb78a59716a01f1c9512797Test
https://pubmed.ncbi.nlm.nih.gov/21550241Test