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1
المؤلفون: Bruno Louis, Karl Leroux, Ghilas Boussaïd, Hélène Prigent, Frédéric Lofaso
المساهمون: Equipe de Recherche Paramédicale sur le Handicap NeuroMoteur (ERPHAN), Université de Versailles Saint-Quentin-en-Yvelines (UVSQ)-Université Paris-Saclay, Handicap neuromusculaire : Physiopathologie, Biothérapie et Pharmacologies appliquées (END-ICAP), Université de Versailles Saint-Quentin-en-Yvelines (UVSQ)-Institut National de la Santé et de la Recherche Médicale (INSERM), Molecular virology and immunology – Physiopathology and therapeutic of chronic viral hepatitis (Team 18) (Inserm U955), Institut Mondor de Recherche Biomédicale (IMRB), Institut National de la Santé et de la Recherche Médicale (INSERM)-IFR10-Université Paris-Est Créteil Val-de-Marne - Paris 12 (UPEC UP12)-Institut National de la Santé et de la Recherche Médicale (INSERM)-IFR10-Université Paris-Est Créteil Val-de-Marne - Paris 12 (UPEC UP12), Biomécanique & Appareil Respiratoire (BAR), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université Paris-Est Créteil Val-de-Marne - Paris 12 (UPEC UP12)-Centre National de la Recherche Scientifique (CNRS)
المصدر: Respiratory Care
Respiratory Care, Daedalus Enterprises Inc, 2020, 65 (9), pp.1258-1267. ⟨10.4187/respcare.07213⟩مصطلحات موضوعية: Pulmonary and Respiratory Medicine, medicine.medical_specialty, Central sleep apnea, Respiratory rate, [SDV]Life Sciences [q-bio], Hyperpnea, Critical Care and Intensive Care Medicine, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, bench study, Tidal Volume, medicine, Humans, Cheyne-Stokes Respiration, Tidal volume, servomechanism, Continuous Positive Airway Pressure, lung model, adaptive servo ventilation, business.industry, pressure support, non-invasive ventilation, Hypoventilation, General Medicine, medicine.disease, Sleep Apnea, Central, 030228 respiratory system, Breathing, Cardiology, Transient (oscillation), medicine.symptom, business, Hypopnea
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::1d1259b8e893b7c1304ed65eb49b4220Test
https://doi.org/10.4187/respcare.07213Test -
2Effect and impact of mechanical ventilation in myotonic dystrophy type 1: a prospective cohort study
المؤلفون: Hélène Prigent, Frédéric Lofaso, Pascal Laforêt, Ghilas Boussaïd, Jean-Claude Raphaël, Djillali Annane, David Orlikowski
المصدر: Thorax. 73:1075-1078
مصطلحات موضوعية: Adult, Male, Pulmonary and Respiratory Medicine, medicine.medical_specialty, medicine.medical_treatment, Myotonic dystrophy, Home ventilation, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, Humans, Myotonic Dystrophy, Medicine, Non-invasive ventilation, In patient, Prospective Studies, Prospective cohort study, Mechanical ventilation, Proportional hazards model, business.industry, Prognosis, medicine.disease, Respiration, Artificial, Respiratory Function Tests, Survival Rate, 030228 respiratory system, Breathing, Patient Compliance, Female, France, Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::db3dda253991ba12111bff08ddec0e8fTest
https://doi.org/10.1136/thoraxjnl-2017-210610Test -
3
المؤلفون: Ghilas Boussaïd, Dante Brasil Santos, Stéphane Bahrami, David Orlikowski, Sandra Pottier, Frédéric Lofaso, Isabelle Vaugier, Hélène Prigent
المصدر: Neuromuscular Disorders. 26:666-674
مصطلحات موضوعية: Adult, Male, Risk, medicine.medical_specialty, medicine.medical_treatment, Vital Capacity, Kaplan-Meier Estimate, Myotonic dystrophy, Body Mass Index, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Millimeter of mercury, Internal medicine, medicine, Humans, Myotonic Dystrophy, Prospective Studies, Occupations, Intensive care medicine, Prospective cohort study, Genetics (clinical), Proportional Hazards Models, Mechanical ventilation, Noninvasive Ventilation, business.industry, Hazard ratio, Middle Aged, medicine.disease, 030228 respiratory system, Neurology, Respiratory failure, Multivariate Analysis, Pediatrics, Perinatology and Child Health, Cohort, Linear Models, Breathing, Patient Compliance, Equipment Failure, Female, Neurology (clinical), Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::fe26af913db365a660caf01faf68af83Test
https://doi.org/10.1016/j.nmd.2016.07.014Test -
4
المؤلفون: Louis Mayaud, Frédéric Lofaso, Hélène Prigent, Guillaume Bao, Sylvain Chevallier, Bernard Bussel, Fabienne Marlats, E. Azabou, Michel Petitjean
المساهمون: Hôpital Raymond Poincaré [AP-HP], Laboratoire d'Ingénierie des Systèmes de Versailles (LISV), Université de Versailles Saint-Quentin-en-Yvelines (UVSQ), Physiologie et physiopathologie de la motricité chez l'homme, Université Pierre et Marie Curie - Paris 6 (UPMC)-IFR70-Institut National de la Santé et de la Recherche Médicale (INSERM), Mensia Technologies [Paris], Groupe de Recherche Clinique et Technologique sur le Handicap (GRCTH)
المصدر: Neurophysiologie Clinique/Clinical Neurophysiology
Neurophysiologie Clinique/Clinical Neurophysiology, Elsevier Masson, 2018, 48 (4), pp.221. ⟨10.1016/j.neucli.2018.06.006⟩مصطلحات موضوعية: medicine.medical_specialty, Sensory processing, medicine.diagnostic_test, business.industry, medicine.medical_treatment, Healthy subjects, 030229 sport sciences, General Medicine, 030204 cardiovascular system & hematology, Audiology, Electroencephalography, [SDV.MHEP.PSR]Life Sciences [q-bio]/Human health and pathology/Pulmonology and respiratory tract, 03 medical and health sciences, 0302 clinical medicine, Neurology, Physiology (medical), Occlusion, Breathing, Medicine, [SDV.NEU]Life Sciences [q-bio]/Neurons and Cognition [q-bio.NC], Neurology (clinical), Evoked potential, Respiratory system, business, Mouthpiece
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8f2c299a316a5d1d58e6dd99511ecf9dTest
https://hal.uvsq.fr/hal-02153493Test -
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المؤلفون: Sandra Pottier, David Orlikowski, Dante Brasil Santos, Ghilas Boussaïd, Stéphane Bahrami, Isabelle Vaugier, Frédéric Lofaso, Hélène Prigent
المصدر: Respiratory Medicine. 115:26-32
مصطلحات موضوعية: Adult, Male, Pulmonary and Respiratory Medicine, medicine.medical_specialty, Adolescent, medicine.medical_treatment, Duchenne muscular dystrophy, Young Adult, 03 medical and health sciences, Tracheostomy, 0302 clinical medicine, Internal medicine, medicine, Humans, Non-invasive ventilation, In patient, Prospective Studies, Child, Prospective cohort study, Heart Failure, Mechanical ventilation, Noninvasive Ventilation, business.industry, Hazard ratio, medicine.disease, Respiration, Artificial, Survival Analysis, Surgery, Muscular Dystrophy, Duchenne, 030228 respiratory system, Child, Preschool, Breathing, France, Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Respiratory care
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::36040a89e19e8fe1b90d18ca594586d1Test
https://doi.org/10.1016/j.rmed.2016.04.009Test -
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المؤلفون: Constantinos Papadopoulos, David Orlikowski, Hélène Prigent, Arnaud Lacour, Céline Tard, Alain Furby, Julien Praline, Guilhem Solé, Jean-Yves Hogrel, Marie De Antonio, Claudio Semplicini, Joelle Deibener-Kaminsky, Pierre Kaminsky, Bruno Eymard, Nadjib Taouagh, Barbara Perniconi, Dalil Hamroun, Pascal Laforêt, G. Bassez, A.-L. Bedat-Millet, A. Behin, B. Eymard, S. Leonard-Louis, T. Stojkovic, A. Canal, V. Decostre, F. Bouhour, F. Boyer, C. Caillaud, Y. Castaing, F. Chapon, P. Cintas, I. Durieu, A. Echaniz-Laguna, L. Feasson, X. Ferrer, R. Froissart, M. Piraud, D. Germain, K. Benistan, N. Guffon-Fouilhoux, H. Journel, P. Labauge, A. Levy, A. Magot, Y. Péréon, M.-C. Minot-Myhié, A. Nadaj-Pakleza, C. Nathier, N. Pellegrini, P. Petiot, F. Lofaso, A. Dutry, D. Renard, S. Sacconi, C. Desnuelle, E. Salort-Campana, J. Pouget, V. Tiffreau, D. Vincent, F. Zagnoli
المساهمون: Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Troubles cognitifs dégénératifs et vasculaires - U 1171 - EA 1046 (TCDV), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Lille, Droit et Santé-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Unité de Recherche Pluridisciplinaire Sport, Santé, Société (URePSSS) - ULR 7369 - ULR 4488 (URePSSS), Université d'Artois (UA)-Université du Littoral Côte d'Opale (ULCO)-Université de Lille, Troubles cognitifs dégénératifs et vasculaires - U 1171 (TCDV), Université de Lille-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille)-Institut National de la Santé et de la Recherche Médicale (INSERM), Université d'Artois (UA)-Université de Lille-Université du Littoral Côte d'Opale (ULCO)
المصدر: Molecular Genetics and Metabolism
Molecular Genetics and Metabolism, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩
Molecular Genetics and Metabolism, Elsevier, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩مصطلحات موضوعية: 0301 basic medicine, Male, Pediatrics, Endocrinology, Diabetes and Metabolism, [SDV]Life Sciences [q-bio], Mesh:Walking, Walking, Mesh:Adult, Respiratory failure, Biochemistry, Late Onset Disorders, Cohort Studies, 0302 clinical medicine, Endocrinology, Mesh:alpha-Glucosidases/therapeutic use, Glycogen Storage Disease Type II, Respiration, Pompe disease, Enzyme replacement therapy, Middle Aged, 3. Good health, Diabetes and Metabolism, Mesh:Late Onset Disorders/drug therapy, Cohort, Breathing, Female, France, Mesh:Respiration, Mesh:alpha-Glucosidases/administration & dosage, Mesh:Enzyme Replacement Therapy*/adverse effects, medicine.drug, Adult, Mesh:Female, medicine.medical_specialty, congenital, hereditary, and neonatal diseases and abnormalities, Mesh:Glycogen Storage Disease Type II/drug therapy, Mesh:Male, Late onset, 03 medical and health sciences, FEV1/FVC ratio, Mesh:alpha-Glucosidases/adverse effects, Mesh:Middle Aged, Mesh:Glycogen Storage Disease Type II/physiopathology, Genetics, medicine, Humans, Mesh:Cohort Studies, Adverse effect, Molecular Biology, Alglucosidase alfa, Mesh:France, Advanced, business.industry, nutritional and metabolic diseases, alpha-Glucosidases, Surgery, Mesh:Humans, 030104 developmental biology, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::2eca040ef3e520953509b66aeb672813Test
https://hal.univ-lille.fr/hal-02369159Test -
7
المؤلفون: Sylvie Chevret, Djillali Annane, Xavier Ambrosi, Abdallah Fayssoil, Frédéric Lofaso, Bernard Clair, Laure Lamothe, Cendrine Chaffaut, David Orlikowski, Adam Ogna, Olivier Nardi, Hélène Prigent
المصدر: Medicine
مصطلحات موضوعية: Duchenne muscular dystrophy, Adult, Cardiac function curve, medicine.medical_specialty, Adolescent, Heart Diseases, pneumothorax, medicine.medical_treatment, Diastole, Observational Study, heart failure, mechanical ventilation, 030204 cardiovascular system & hematology, Doppler echocardiography, Cohort Studies, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, medicine, echocardiography, Humans, Cumulative incidence, Tidal volume, Retrospective Studies, Mechanical ventilation, Ejection fraction, medicine.diagnostic_test, business.industry, respiratory failure, Heart, General Medicine, Respiration, Artificial, Echocardiography, Doppler, 3. Good health, Muscular Dystrophy, Duchenne, 030228 respiratory system, Becker muscular dystrophy, Spirometry, Breathing, Cardiology, Respiratory Insufficiency, business, Research Article
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::68d427f49de85ab74305f67346be1e09Test
https://doi.org/10.1097/md.0000000000011381Test -
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المؤلفون: Bruno Louis, Brigitte Fauroux, Karl Leroux, Frédéric Lofaso, Sonia Khirani, David Orlikowski, Line Falaize, Hélène Prigent
المصدر: Respiratory care. 59(7)
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Adult, medicine.medical_specialty, Time Factors, genetic structures, Respiratory rate, Critical Care and Intensive Care Medicine, Models, Biological, Electric Power Supplies, medicine, Portable ventilators, Ventilator settings, Tidal Volume, Humans, Tidal volume, Ventilators, Mechanical, business.industry, Battery (vacuum tube), General Medicine, Home Care Services, Respiration, Artificial, Surgery, Anesthesia, Breathing, business, circulatory and respiratory physiology
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::dccaadd5a7784a66729aa6234516f16aTest
https://pubmed.ncbi.nlm.nih.gov/24149669Test -
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المؤلفون: J. Boudarham, Hélène Prigent, Didier Pradon, Henri Meric, Marie-Christine Durand, Michel Petitjean, Frédéric Lofaso, Line Falaize
المصدر: Chest. 144(3)
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Thorax, Adult, Male, Weakness, medicine.medical_specialty, Diaphragm, Critical Care and Intensive Care Medicine, Diagnosis, Differential, Medicine, Humans, Diaphragmatic weakness, Phrenic nerve, Aged, Muscle Weakness, medicine.diagnostic_test, business.industry, Respiration, Reproducibility of Results, Middle Aged, Respiratory Paralysis, Electric Stimulation, Diaphragm (structural system), Surgery, Plethysmography, medicine.anatomical_structure, Anesthesia, Breathing, Abdomen, Female, medicine.symptom, Cardiology and Cardiovascular Medicine, business, Chest radiograph, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::94e55724cb5f3df004569c1341a0ff0bTest
https://pubmed.ncbi.nlm.nih.gov/23519378Test -
10
المؤلفون: Pierre G. Carlier, N. Pellegrini, Pascal Laforêt, Djillali Annane, Robert Carlier, Bruno Eymard, Frédéric Lofaso, Hélène Prigent, David Orlikowski
المصدر: Neuromuscular disorders : NMD. 21(7)
مصطلحات موضوعية: Spirometry, Adult, Male, medicine.medical_specialty, Metabolic myopathy, Gastroenterology, Internal medicine, medicine, Humans, Respiratory function, Enzyme Replacement Therapy, Muscle Strength, Prospective Studies, Respiratory system, Alglucosidase alfa, Genetics (clinical), medicine.diagnostic_test, business.industry, Glycogen Storage Disease Type II, alpha-Glucosidases, Enzyme replacement therapy, Middle Aged, medicine.disease, Recombinant Proteins, Surgery, Respiratory Function Tests, Treatment Outcome, Neurology, Respiratory failure, Pediatrics, Perinatology and Child Health, Breathing, Female, Neurology (clinical), business, Respiratory Insufficiency, medicine.drug
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::eca97f5b2cb78a59716a01f1c9512797Test
https://pubmed.ncbi.nlm.nih.gov/21550241Test