المؤلفون: Valeria Crippa, Riccardo Cristofani, Paola Rusmini, E. Onesto, Elisa Giorgetti, A. Boncoraglio, Mariarita Galbiati, Angela Poletti, A. Zito

المصدر: Biochemical Society Transactions. 41:1598-1604

مصطلحات موضوعية: Motor Neurons, Protein Folding, Cell type, Superoxide Dismutase, Muscles, Amyotrophic Lateral Sclerosis, Skeletal muscle, Biology, musculoskeletal system, MyoD, Biochemistry, Muscle atrophy, Cell biology, Superoxide Dismutase-1, medicine.anatomical_structure, nervous system, Proteotoxicity, Proteasome, medicine, Animals, Humans, Myocyte, medicine.symptom, Myogenin

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::62d4bdd681b2ca488bd73279b4e92240Test
https://doi.org/10.1042/bst20130118Test

المؤلفون: Mariarita Galbiati, A. Boncoraglio, Valeria Crippa, E. Bolzoni, Silvia De Biasi, Daniela Sau, E. Onesto, Angelo Poletti, Elena Fontana, Paola Rusmini, Serena Carra, Marianna Marino, Caterina Bendotti

المصدر: Human Molecular Genetics, 19(17), 3440-3456. Oxford University Press

مصطلحات موضوعية: Male, Protein Folding, animal diseases, Muscle Proteins, Gene mutation, FAMILIAL ALS, Mice, Superoxide Dismutase-1, POLYGLUTAMINE TRACT, Amyotrophic lateral sclerosis, Heat-Shock Proteins, Genetics (clinical), Motor Neurons, CHAPERONE ACTIVITY, ANDROGEN RECEPTOR, SOD1, General Medicine, chaperones, protein degradation, protein mislfolding, Cell biology, DNA-Binding Proteins, Female, SPINAL-CORD, 5-ALPHA-REDUCTASE TYPE-2, Mice, Transgenic, Protein Serine-Threonine Kinases, Protein degradation, Biology, BAG3, Cell Line, Heat shock protein, Autophagy, Genetics, medicine, Animals, Humans, HSP20 Heat-Shock Proteins, MARIE-TOOTH-DISEASE, Molecular Biology, MUTANT MICE, Superoxide Dismutase, MUTATIONS, Amyotrophic Lateral Sclerosis, nutritional and metabolic diseases, medicine.disease, nervous system diseases, Mice, Inbred C57BL, Proteasome, nervous system, Immunology, MOTOR-NEURONS, Molecular Chaperones

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::aecb4e0d64f4f3e2259f5b127752ed80Test
https://hdl.handle.net/11370/3713ab91-fc92-4276-b50f-1ed5004a4870Test

المؤلفون: Maria Elena Cicardi, Angelo Poletti, Elisa Giorgetti, Mariarita Galbiati, E. Onesto, Valeria Crippa, Riccardo Cristofani, Elio Messi, Paola Rusmini

المصدر: Neurochemistry international. 79

مصطلحات موضوعية: Denervation, Motor Neurons, Cell type, Muscle Cells, Autophagy, Amyotrophic Lateral Sclerosis, Cell Biology, Protein aggregation, Motor neuron, Biology, medicine.disease, Cellular and Molecular Neuroscience, medicine.anatomical_structure, nervous system, medicine, Myocyte, Animals, Humans, Amyotrophic lateral sclerosis, Proteostasis Deficiencies, Neuroscience, Intracellular

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::a496b0c3d53af823c1030163a8a8913bTest
https://pubmed.ncbi.nlm.nih.gov/25451799Test

المؤلفون: Angelo Poletti, M. Rizzardini, Paola Rusmini, Laura Conforti, Lavinia Cantoni, Elisabetta Babetto, Alessandra Mangolini, Monica Lupi

المصدر: Molecular Brain Research. 140:63-72

مصطلحات موضوعية: Green Fluorescent Proteins, Mice, Transgenic, Biology, Transfection, Cell Line, Green fluorescent protein, Mice, Cellular and Molecular Neuroscience, Transactivation, Superoxide Dismutase-1, Genes, Reporter, Gene expression, Animals, Humans, Motor Neuron Disease, Molecular Biology, Gene, DNA Primers, Motor Neurons, Regulation of gene expression, Reporter gene, Base Sequence, Reverse Transcriptase Polymerase Chain Reaction, Superoxide Dismutase, Tetracycline, Cell biology, Gene Expression Regulation, nervous system, Cell culture, Immunology

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::81ef9528616bc506cb81746152137385Test
https://doi.org/10.1016/j.molbrainres.2005.07.010Test

المؤلفون: Angelo Poletti, Paola Rusmini, A. Zito, Mariarita Galbiati, Valeria Crippa, Nicola Ferri, E. Onesto

المصدر: Journal of Neurochemistry

مصطلحات موضوعية: Cell type, Proteasome Endopeptidase Complex, amyotrophic lateral sclerosis, autophagy, motor neuron diseases, muscle, animal diseases, SOD1, Biology, Biochemistry, Cell Line, motoneuron diseases, Myoblasts, Cellular and Molecular Neuroscience, chemistry.chemical_compound, Superoxide Dismutase-1, Mutant protein, MG132, neurodegeneration, proteasome, aggregation, protein misfolding, medicine, Myocyte, Humans, Cell Line, Transformed, Motor Neurons, Molecular Basis of Disease, Muscle Cells, Superoxide Dismutase, nutritional and metabolic diseases, Original Articles, musculoskeletal system, Muscle atrophy, Cell biology, nervous system diseases, Proteasome, chemistry, nervous system, Cell culture, Immunology, Mutation, medicine.symptom, Proteasome Inhibitors

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::6b09d29e6ac99dfe4242b7bc01f78cbbTest
http://hdl.handle.net/11577/3177789Test

المؤلفون: Daniela Sau, Paola Rusmini, Valeria Crippa, Patrizia Riso, Caterina Bendotti, E. Onesto, Marisa Porrini, Angelo Poletti, Silvia De Biasi, Silvia Simeoni, Isabella Palazzolo, E. Bolzoni, Serena Guarnieri, L. Vitellaro-Zuccarello

المصدر: Human molecular genetics. 16(13)

مصطلحات موضوعية: Cytoplasm, Proteasome Endopeptidase Complex, DNA damage, animal diseases, SOD1, Mutant, Mice, Transgenic, Biology, medicine.disease_cause, Gene Expression Regulation, Enzymologic, Superoxide dismutase, Mice, Genetics, medicine, Animals, Molecular Biology, Genetics (clinical), Loss function, Cell Nucleus, Mutation, Superoxide Dismutase, Amyotrophic Lateral Sclerosis, nutritional and metabolic diseases, General Medicine, Molecular biology, nervous system diseases, Oxygen, Cell nucleus, Oxidative Stress, medicine.anatomical_structure, nervous system, Proteasome, Microscopy, Fluorescence, Spinal Cord, biology.protein, DNA Damage

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8270f59c73893228fc8fedd9b7364e05Test
https://pubmed.ncbi.nlm.nih.gov/17504823Test