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المؤلفون: Elena Quaglio, Vanessa Capone, Vladimiro Artuso, Fabio Fiordaliso, Ignazio Roiter, Davide Ortolan, Michele Sallese, Alessandro Corbelli, Galina V. Beznoussenko, Elena Restelli, Manuela Pozzoli, Roberto Chiesa
المصدر: The Journal of Biological Chemistry
مصطلحات موضوعية: 0301 basic medicine, Protein Folding, HFs, human fibroblasts, PDI, protein disulfide isomerase, Mutant, Golgi Apparatus, Endoplasmic Reticulum, medicine.disease_cause, VSV-G, vesicular stomatite virus glycoprotein, Biochemistry, Creutzfeldt-Jakob Syndrome, DMEM, Dulbecco’s modified Eagle’s medium, Mice, Gerstmann-Straussler-Scheinker Disease, Src family kinase, protein misfolding, genetic prion disease, Cells, Cultured, Mutation, Secretory Pathway, FFI, fatal familial insomnia, moPrP, mouse PrP, Chemistry, MEFs, mouse embryonic fibroblasts, GPCR, G-protein-coupled receptors, VGCCs, voltage-gated calcium channels, GSS, Gerstmann–Sträussler–Scheinker, Cell biology, src-Family Kinases, CCD, charge-coupled device, PM, plasma membrane, symbols, RT, room temperature, PC-I, procollagen I, protein trafficking, Intracellular, Research Article, GPI, glycosylphosphatidylinositol, GFP-GPI, GPI-anchored green fluorescent protein reporter, Mice, Transgenic, gCJD, genetic Creutzfeldt–Jakob disease, Rab GDP, dissociation inhibitor (GDI), CNS, central nervous system, Insomnia, Fatal Familial, Prion Proteins, AMPARs, α-amino-3-hydroxy-5-methyl-4-isoxazolepropionic acid receptors, KDEL-R, KDEL receptor, MEM, minimum essential medium, ER, endoplasmic reticulum, 03 medical and health sciences, symbols.namesake, YAG, yttrium aluminum garnet, Tg, transgenic, medicine, Animals, Humans, IF, immunofluorescence, Molecular Biology, Secretory pathway, Fatal familial insomnia, EM, electron microscopy, PrP, prion protein, KO, knockout, 030102 biochemistry & molecular biology, Endoplasmic reticulum, Cell Biology, Golgi apparatus, medicine.disease, LD, labeling density, WT, wild-type, PG14, moPrP with a nine-octapeptide repeat insertion, Enzyme Activation, Mice, Inbred C57BL, Disease Models, Animal, PenStrep, penicillin/streptomycin, 030104 developmental biology, prion protein, Mice, Inbred CBA, SFK, Src family kinase, BSA, bovine serum albumin, mo, mouse
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::9d3782460cda7c20d4fd5164939fecf2Test
https://doi.org/10.1016/j.jbc.2021.100490Test -
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المؤلفون: Marten Beeg, Luisa Diomede, Mario Salmona, Fabio Fiordaliso, Laura Colombo, Alessandro Corbelli, Marco Gobbi, Alfredo Cagnotto, Ada De Luigi, Carmina Natale, Elisabetta Battocchio
المصدر: The Journal of Biological Chemistry
مصطلحات موضوعية: 0301 basic medicine, Amyloid, Amyloid beta, Tau protein, PB, phosphate buffer, SPR, surface plasmon resonance, tau Proteins, Peptide, Fibril, Biochemistry, Neuroprotection, 03 medical and health sciences, chemistry.chemical_compound, mental disorders, medicine, kinetics of fibril formation, Animals, Humans, ThT, thioflavine T, tau, Surface plasmon resonance, Caenorhabditis elegans, TEM, transmission electron microscopy, Molecular Biology, chemistry.chemical_classification, Amyloid beta-Peptides, 030102 biochemistry & molecular biology, biology, CB, Coomassie blue, amyloid-beta (Aβ), Cell Biology, Alzheimer's disease, medicine.disease, Peptide Fragments, Aβ, amyloid-beta, Kinetics, Neuroprotective Agents, 030104 developmental biology, Monomer, WB, Western blot, chemistry, Larva, biology.protein, Biophysics, AD, Alzheimer's disease, surface plasmon resonance, Research Article
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::006fa36e039871fc3dcdee61dddcd04fTest
https://doi.org/10.1016/j.jbc.2021.100664Test -
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المؤلفون: Elisa Battaglia, Alessandro Corbelli, Francesco Gensano, Elisa Martini, Stefano Garetto, D. Lidonnici, Fabio Fiordaliso, Laura Pasetto, Antonio Vallarola, Gabriella Spaltro, Valentina Bonetto, Caterina Bendotti, Massimo Tortarolo, Marinos Kallikourdis
مصطلحات موضوعية: amyotrophic lateral sclerosis, Spinal neuron, Cells, tumor necrosis factor α, Biochemistry, Type II, motor neuron, neuromuscular junctions, tumor necrosis factor receptor 2, Amyotrophic Lateral Sclerosis, Animals, Astrocytes, Axons, Cell Death, Cells, Cultured, Coculture Techniques, DNA-Binding Proteins, Disease Models, Animal, Disease Progression, Mice, Motor Neurons, Neuroglia, Receptors, Tumor Necrosis Factor, Type II, Cellular and Molecular Neuroscience, Receptors, medicine, Amyotrophic lateral sclerosis, Receptor, Cultured, business.industry, Animal, Neurodegeneration, Motor neuron, medicine.disease, medicine.anatomical_structure, nervous system, Disease Models, Tumor necrosis factor alpha, business, Tumor Necrosis Factor, Neuroscience, Homeostasis, Astrocyte
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::420d3dd98ea1470c623d5ce82e3bae90Test
https://hdl.handle.net/11380/1202117Test -
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المؤلفون: Marialaura Marchetti, Riccardo Percudani, Cristina Zennaro, Federica Tonon, Alessandro Corbelli, Luca Ronda, Paola Zarattini, Gianluca Paredi, Milan Clai, Maria Pia Rastaldi, Michele Carraro
المساهمون: Zennaro, Cristina, Tonon, Federica, Zarattini, Paola, Clai, Milan, Corbelli, Alessandro, Carraro, Michele, Marchetti, Marialaura, Ronda, Luca, Paredi, Gianluca, Pia Rastaldi, Maria, Percudani, Riccardo
المصدر: PLoS ONE, Vol 12, Iss 3, p e0173512 (2017)
PLoS ONEمصطلحات موضوعية: 0301 basic medicine, Hypoxanthine Phosphoribosyltransferase, Lesch-Nyhan Syndrome, LESCH-NYHAN-SYNDROME, 030232 urology & nephrology, lcsh:Medicine, Biochemistry, DISEASE, Mice, chemistry.chemical_compound, 0302 clinical medicine, Medicine and Health Sciences, XANTHINE OXIDOREDUCTASE, Renal Failure, Polarized Light Microscopy, lcsh:Science, Hypoxanthine, Mice, Knockout, Liquid Chromatography, Microscopy, Nephritis, Multidisciplinary, Organic Compounds, Chromatographic Techniques, Light Microscopy, Lipids, Chemistry, Nephrology, Physical Sciences, CLASSICAL XANTHINURIA, Anatomy, Research Article, medicine.drug, Xanthine Oxidase, Materials by Structure, NEPHROPATHY, Allopurinol, Materials Science, URIC-ACID, Biology, Research and Analysis Methods, PURINE NUCLEOSIDE PHOSPHORYLASE, Xanthine, Crystals, Nephropathy, 03 medical and health sciences, medicine, Animals, Xanthine oxidase, MESENCHYMAL TRANSITION, Organic Chemistry, lcsh:R, Chemical Compounds, Biology and Life Sciences, Kidneys, Renal System, medicine.disease, GENE, Molecular biology, High Performance Liquid Chromatography, Uric Acid, 030104 developmental biology, chemistry, Purines, URATE-OXIDASE, Uric acid, lcsh:Q, Lesch–Nyhan syndrome, Acids
وصف الملف: ELETTRONICO
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::06f70904dd8133e2e8899988454ec61bTest
https://doi.org/10.1371/journal.pone.0173512Test -
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المؤلفون: Fabio Fiordaliso, Veronica Valentini, Mario Salmona, Giampaolo Merlini, Elena Del Favero, Vittorio Perfetti, Luisa Diomede, Paola Rognoni, Andrea di Fonzo, Francesca Lavatelli, Margherita Romeo, Elena Maria Ghibaudi, Laura Cantù, Alessandro Corbelli, Giovanni Palladini
مصطلحات موضوعية: Cardiotoxicity, biology, Amyloid, Pharyngeal pumping, heart amyloidosis, Amyloidosis, Immunology, Cardiomyopathy, redox cycling, diagnostic assay, Cell Biology, Hematology, biology.organism_classification, medicine.disease, Immunoglobulin light chain, Biochemistry, Cancer research, medicine, Caenorhabditis elegans, Tropism
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::fd28d2a7615c4cc562cfed7fda06b0c6Test
http://hdl.handle.net/2318/151896Test