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المؤلفون: Sander M. Houten, Nihad Achetib, Myriam Baes, Tetyana Dodatko, Carmen Argmann, Sara Violante, Chunli Yu, Frédéric M. Vaz, Hongjie Chen, Carlo W.T. van Roermund, Jacob Hagen, Hans R. Waterham
مصطلحات موضوعية: 0301 basic medicine, Life Sciences & Biomedicine - Other Topics, PHYTANIC ACID, CARNITINE PALMITOYLTRANSFERASE, Palmitic Acid, ATP-binding cassette transporter, Mitochondrion, Biochemistry, PALMITOYLTRANSFERASE-II DEFICIENCY, MITOCHONDRIAL, Palmitic acid, Mice, chemistry.chemical_compound, 0302 clinical medicine, Peroxisomal Multifunctional Protein-2, Beta oxidation, fatty acid oxidation, Mice, Knockout, biology, Fatty Acids, Lauric Acids, Peroxisome, Recombinant Proteins, Mitochondria, mitochondria, MALONYL-COA, MOUSE-LIVER, BETA-OXIDATION, Oxidation-Reduction, Life Sciences & Biomedicine, Biotechnology, medicine.drug, organellar crosstalk, Biochemistry & Molecular Biology, Peroxisomal Bifunctional Enzyme, PRISTANIC ACID, acylcarnitine, 03 medical and health sciences, ABCD3, Carnitine, Peroxisomes, Genetics, medicine, Animals, Humans, ACETYL MOIETY, Molecular Biology, Biology, Science & Technology, MOLECULAR-CLONING, Carnitine O-Palmitoyltransferase, Research, Membrane Proteins, Cell Biology, Metabolic pathway, HEK293 Cells, 030104 developmental biology, chemistry, biology.protein, ATP-Binding Cassette Transporters, CPT2 deficiency, CRISPR-Cas Systems, 030217 neurology & neurosurgery
وصف الملف: Print-Electronic
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::9257e5d9c1e5b6cd676d0b77300cc2a8Test
https://lirias.kuleuven.be/handle/123456789/640719Test -
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المؤلفون: Cèlia García-Martínez, Anna M. Gómez-Foix, Fausto G. Hegardt, Maria Guitart, Josep M. Orellana-Gavaldà, Guillermina Asins, Caroline Mauvezin, Dolors Serra, David Sebastián
المصدر: Dipòsit Digital de la UB
Universidad de Barcelona
Journal of Lipid Research, Vol 50, Iss 9, Pp 1789-1799 (2009)
Journal of Lipid Researchمصطلحات موضوعية: CD36 Antigens, Male, Muscle Fibers, Skeletal, Muscle cells, Àcids grassos, Antígens, Biochemistry, Mitocondris, Mice, chemistry.chemical_compound, Endocrinology, malonyl-CoA, Cèl·lules musculars, Beta oxidation, chemistry.chemical_classification, biology, Fatty Acids, FAT/CD36, food and beverages, Fatty Acid Transport Proteins, Metabolisme, Mitochondria, mitochondria, Protein Transport, Fatty acid synthase, Free fatty acid receptor, Oxidation-Reduction, Research Article, Oxidation-reduction reaction, Ratolins (Animals de laboratori), carnitine palmitoyltransferase 1, Citologia, QD415-436, Cell Line, Reacció d'oxidació-reducció, Coenzyme A Ligases, Animals, Humans, Immunoprecipitation, Antigens, Fatty acids, adipocyte protein 2, Muscle, Skeletal, Carnitine O-Palmitoyltransferase, Fatty acid, Cell Biology, Lipid Metabolism, Metabolisme dels lípids, Rats, Metabolism, Lipid metabolism, Mice (Laboratory animals), Malonyl-CoA, Gene Expression Regulation, chemistry, biology.protein, Cytology, Etomoxir
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::a0a30e184dffe0c43959813a1640f75cTest
https://doi.org/10.1194/jlr.m800535-jlr200Test -
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المؤلفون: Carina Prip-Buus, Isabel Tavares de Almeida, Lodewijk IJlst, Margarida F. B. Silva, C. C. P. Aires, Marinus Duran, Femke S. Stet, Ronald J.A. Wanders
المساهمون: Laboratory Genetic Metabolic Disease, University of Amsterdam [Amsterdam] (UvA)-Academic Medical Center - Academisch Medisch Centrum [Amsterdam] (AMC), University of Amsterdam [Amsterdam] (UvA), Institut Cochin (IC UM3 (UMR 8104 / U1016)), Université Paris Descartes - Paris 5 (UPD5)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Academic Medical Center - Academisch Medisch Centrum [Amsterdam] (AMC), Laboratoy Genetic Metabolic Diseases, Department of Clinical Chemistry, Academic Medical Centre, University of Amsterdam, AGEM - Amsterdam Gastroenterology Endocrinology Metabolism, Laboratory Genetic Metabolic Diseases, University of Amsterdam [Amsterdam] (UvA)-University of Amsterdam [Amsterdam] (UvA), Centre National de la Recherche Scientifique (CNRS)-Université Paris Descartes - Paris 5 (UPD5)-Institut National de la Santé et de la Recherche Médicale (INSERM)
المصدر: Biochemical Pharmacology
Biochemical Pharmacology, Elsevier, 2010, 79 (5), pp.792-799. ⟨10.1016/j.bcp.2009.10.011⟩
Biochemical pharmacology, 79(5), 792-799. Elsevier Inc.مصطلحات موضوعية: [SDV]Life Sciences [q-bio], Saccharomyces cerevisiae, Transfection, Biochemistry, 03 medical and health sciences, chemistry.chemical_compound, 0302 clinical medicine, medicine, Animals, Humans, Transferase, Carnitine O-palmitoyltransferase, Carnitine, Enzyme Inhibitors, Beta oxidation, Cells, Cultured, ComputingMilieux_MISCELLANEOUS, 030304 developmental biology, Pharmacology, chemistry.chemical_classification, 0303 health sciences, Carnitine O-Palmitoyltransferase, biology, Valproic Acid, Fatty Acids, Fibroblasts, Rats, Fatty Liver, Enzyme, Malonyl-CoA, Mechanism of action, chemistry, Enzyme inhibitor, biology.protein, Anticonvulsants, lipids (amino acids, peptides, and proteins), Acyl Coenzyme A, medicine.symptom, Oxidation-Reduction, 030217 neurology & neurosurgery, Plasmids, medicine.drug
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::9b11a427753f1ae8127c34e744833f1eTest
https://doi.org/10.1016/j.bcp.2009.10.011Test -
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المؤلفون: E D Saggerson, N Alam
المصدر: Biochemical Journal. 334:233-241
مصطلحات موضوعية: Male, medicine.medical_specialty, Carboxy-Lyases, Palmitic Acid, In Vitro Techniques, Models, Biological, Biochemistry, Rats, Sprague-Dawley, chemistry.chemical_compound, Malate Dehydrogenase, Internal medicine, medicine, Animals, Carnitine, Enzyme Inhibitors, Muscle, Skeletal, Molecular Biology, Beta oxidation, Soleus muscle, Carnitine O-Palmitoyltransferase, biology, Chemistry, Skeletal muscle, Cell Biology, Malonyl-CoA decarboxylase, Rats, Malonyl Coenzyme A, Kinetics, Fatty acid synthase, Glucose, medicine.anatomical_structure, Endocrinology, Malonyl-CoA, ATP Citrate (pro-S)-Lyase, biology.protein, Epoxy Compounds, Regression Analysis, lipids (amino acids, peptides, and proteins), Acyl Coenzyme A, Fatty Acid Synthases, Oxidation-Reduction, Etomoxir, Research Article, medicine.drug
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::f64420a1812a25b6bae86566e4e4a5e4Test
https://doi.org/10.1042/bj3340233Test -
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المؤلفون: Carina Prip-Buus, Jean Girard, Martin Sournac, Catherine Esnous, Isabelle Cohen, Marie Akkaoui, Véronique Lenoir
المساهمون: Peer, Hal, Institut Cochin (UMR_S567 / UMR 8104), Université Paris Descartes - Paris 5 (UPD5)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Université Paris Descartes - Paris 5 (UPD5) - Institut National de la Santé et de la Recherche Médicale (INSERM) - Centre National de la Recherche Scientifique (CNRS)
المصدر: Biochemical Journal
Biochemical Journal, 2009, 420 (3), pp.429-438. ⟨10.1042/BJ20081932⟩
Biochemical Journal, Portland Press, 2009, 420 (3), pp.429-438. 〈10.1042/BJ20081932〉مصطلحات موضوعية: Male, medicine.medical_treatment, Fluorescent Antibody Technique, Biochemistry, chemistry.chemical_compound, 0302 clinical medicine, Insulin, Beta oxidation, fatty acid oxidation, Cells, Cultured, 0303 health sciences, Fatty Acids, Mitochondria, Liver, 030220 oncology & carcinogenesis, Lipogenesis, lipids (amino acids, peptides, and proteins), Oxidation-Reduction, medicine.medical_specialty, Genetic Vectors, Immunoblotting, carnitine palmitoyltransferase 1, Biology, Transfection, Models, Biological, Adenoviridae, 03 medical and health sciences, Carnitine palmitoyltransferase 1, Internal medicine, medicine, Animals, triglyceride, Carnitine O-palmitoyltransferase, Rats, Wistar, Glycogen synthase, Molecular Biology, lipogenesis, Triglycerides, 030304 developmental biology, Carnitine O-Palmitoyltransferase, Triglyceride, Cell Biology, Lipid Metabolism, Rats, Glucose, Endocrinology, Malonyl-CoA, chemistry, Mutation, Hepatocytes, biology.protein
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::b4a879788b9626afd81144d52583a294Test
https://doi.org/10.1042/bj20081932Test -
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المؤلفون: Makiko Kajimura, Grant B. McClelland, Andrea J. Morash
المصدر: Biochimica et Biophysica Acta (BBA) - Biomembranes. 1778:1382-1389
مصطلحات موضوعية: medicine.medical_specialty, Transcription, Genetic, Membrane Fluidity, Biophysics, Biology, Mitochondrion, Biochemistry, Gene Expression Regulation, Enzymologic, Mitochondrial Proteins, chemistry.chemical_compound, Allosteric Regulation, Internal medicine, medicine, Membrane fluidity, Animals, Citrate synthase, PPAR alpha, RNA, Messenger, Carnitine, Inner mitochondrial membrane, PPAR-beta, Beta oxidation, Carnitine O-Palmitoyltransferase, Cell Biology, Malonyl-CoA, Mitochondria, Malonyl Coenzyme A, Enzyme inhibition, Endocrinology, chemistry, Organ Specificity, Oncorhynchus mykiss, Mitochondrial Membranes, Membrane composition, Fatty Acids, Unsaturated, biology.protein, Carnitine palmitoyltransferase I, Oxidation-Reduction, medicine.drug
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::7b950deab8cbc500de4303fa33742648Test
https://doi.org/10.1016/j.bbamem.2008.02.013Test -
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المصدر: Canadian Journal of Physiology and Pharmacology. 84:1215-1222
مصطلحات موضوعية: medicine.medical_specialty, Carboxy-Lyases, Physiology, Citric Acid Cycle, Palmitic Acid, macromolecular substances, AMP-Activated Protein Kinases, In Vitro Techniques, Protein Serine-Threonine Kinases, Carbohydrate metabolism, chemistry.chemical_compound, AMP-activated protein kinase, Acetyl Coenzyme A, Multienzyme Complexes, Physiology (medical), Internal medicine, medicine, Animals, Beta oxidation, Pharmacology, chemistry.chemical_classification, Carnitine O-Palmitoyltransferase, Dose-Response Relationship, Drug, biology, Myocardium, Fatty acid, General Medicine, Malonyl Coenzyme A, Citric acid cycle, Dose–response relationship, Glucose, Malonyl-CoA, Endocrinology, Animals, Newborn, chemistry, Biochemistry, Circulatory system, biology.protein, Rabbits, Oxidation-Reduction, Acetyl-CoA Carboxylase
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::ba408f14486d119e27731a28a7d684e4Test
https://doi.org/10.1139/y06-062Test -
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المؤلفون: Joanne S. Kays, Craig D. Hammond, Thomas W. Seng, Tiffanie R. Skillman, Lorri Burris, Nengyu Yang
المصدر: Journal of Pharmacology and Experimental Therapeutics. 312:127-133
مصطلحات موضوعية: endocrine system, endocrine system diseases, Mitochondria, Heart, Enzyme activator, chemistry.chemical_compound, Carnitine palmitoyltransferase 1, 4-Butyrolactone, Yeasts, Tumor Cells, Cultured, medicine, Animals, Humans, heterocyclic compounds, Carnitine, Carnitine O-palmitoyltransferase, neoplasms, Beta oxidation, Pharmacology, Carnitine O-Palmitoyltransferase, biology, Malonyl Coenzyme A, Recombinant Proteins, digestive system diseases, Rats, Enzyme Activation, Fatty acid synthase, Malonyl-CoA, Biochemistry, chemistry, biology.protein, Molecular Medicine, medicine.drug
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::c686d2d2f28ce33f3054d1239d3de0eaTest
https://doi.org/10.1124/jpet.104.074104Test -
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المؤلفون: Asish K. Saha, Lee A. Witters, Neil B. Ruderman, Demetrios G. Vavvas
المصدر: American Journal of Physiology-Endocrinology and Metabolism. 276:E1-E18
مصطلحات موضوعية: medicine.medical_specialty, Physiology, Endocrinology, Diabetes and Metabolism, medicine.medical_treatment, Allosteric regulation, chemistry.chemical_compound, Insulin resistance, AMP-activated protein kinase, Physiology (medical), Internal medicine, medicine, Animals, Humans, Carnitine O-palmitoyltransferase, Carnitine, Muscle, Skeletal, biology, Insulin, Acetyl-CoA carboxylase, medicine.disease, Malonyl Coenzyme A, Malonyl-CoA, Endocrinology, chemistry, Biochemistry, biology.protein, lipids (amino acids, peptides, and proteins), Insulin Resistance, Energy Metabolism, Signal Transduction, medicine.drug
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::20e3996ffca555e396e99e1a41ba0b19Test
https://doi.org/10.1152/ajpendo.1999.276.1.e1Test -
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المؤلفون: John D. Horowitz, Steven A. Unger, Jennifer A. Kennedy
المصدر: Biochemical Pharmacology. 52:273-280
مصطلحات موضوعية: Male, medicine.medical_specialty, Perhexiline, Amiodarone, Mitochondria, Liver, Biochemistry, Mitochondria, Heart, Rats, Sprague-Dawley, chemistry.chemical_compound, Non-competitive inhibition, Carnitine palmitoyltransferase 1, Internal medicine, medicine, Animals, Subtilisins, Carnitine O-palmitoyltransferase, Carnitine, Pharmacology, Carnitine O-Palmitoyltransferase, biology, Cardiovascular Agents, Rats, Malonyl-CoA, Endocrinology, chemistry, Enzyme inhibitor, Cardiovascular agent, biology.protein, Anti-Arrhythmia Agents, medicine.drug
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::82940cfa822195bfb52ce8eb52c41e0aTest
https://doi.org/10.1016/0006-2952Test(96)00204-3