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المؤلفون: Gilbert Desmarais, Frédéric Lofaso, Dante Brasil Santos, Sandrine Cognet, Bruno Louis, L. Falaize, Hélène Prigent, Adam Ogna, David Orlikowski
المصدر: Neuromuscular Disorders. 27:518-525
مصطلحات موضوعية: Adult, Male, medicine.medical_specialty, Weakness, Neuromuscular disease, Diaphragm, Diaphragmatic breathing, Stimulation, Sensitivity and Specificity, 03 medical and health sciences, Esophagus, 0302 clinical medicine, Internal medicine, Pressure, medicine, Humans, Respiratory muscle weakness, Genetics (clinical), Mouth, Muscle Weakness, business.industry, Muscle weakness, Neuromuscular Diseases, Middle Aged, musculoskeletal system, medicine.disease, Nasal pressure, Respiratory Muscles, Respiratory Function Tests, Surgery, Phrenic Nerve, Inhalation, 030228 respiratory system, Neurology, Mouth pressure, Pediatrics, Perinatology and Child Health, Cardiology, Female, Neurology (clinical), medicine.symptom, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::e478c38ee86be07bebba5ffba6e3c629Test
https://doi.org/10.1016/j.nmd.2017.01.022Test -
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المؤلفون: Sandra Pottier, David Orlikowski, Dante Brasil Santos, Ghilas Boussaïd, Stéphane Bahrami, Isabelle Vaugier, Frédéric Lofaso, Hélène Prigent
المصدر: Respiratory Medicine. 115:26-32
مصطلحات موضوعية: Adult, Male, Pulmonary and Respiratory Medicine, medicine.medical_specialty, Adolescent, medicine.medical_treatment, Duchenne muscular dystrophy, Young Adult, 03 medical and health sciences, Tracheostomy, 0302 clinical medicine, Internal medicine, medicine, Humans, Non-invasive ventilation, In patient, Prospective Studies, Child, Prospective cohort study, Heart Failure, Mechanical ventilation, Noninvasive Ventilation, business.industry, Hazard ratio, medicine.disease, Respiration, Artificial, Survival Analysis, Surgery, Muscular Dystrophy, Duchenne, 030228 respiratory system, Child, Preschool, Breathing, France, Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Respiratory care
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::36040a89e19e8fe1b90d18ca594586d1Test
https://doi.org/10.1016/j.rmed.2016.04.009Test -
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المؤلفون: Constantinos Papadopoulos, David Orlikowski, Hélène Prigent, Arnaud Lacour, Céline Tard, Alain Furby, Julien Praline, Guilhem Solé, Jean-Yves Hogrel, Marie De Antonio, Claudio Semplicini, Joelle Deibener-Kaminsky, Pierre Kaminsky, Bruno Eymard, Nadjib Taouagh, Barbara Perniconi, Dalil Hamroun, Pascal Laforêt, G. Bassez, A.-L. Bedat-Millet, A. Behin, B. Eymard, S. Leonard-Louis, T. Stojkovic, A. Canal, V. Decostre, F. Bouhour, F. Boyer, C. Caillaud, Y. Castaing, F. Chapon, P. Cintas, I. Durieu, A. Echaniz-Laguna, L. Feasson, X. Ferrer, R. Froissart, M. Piraud, D. Germain, K. Benistan, N. Guffon-Fouilhoux, H. Journel, P. Labauge, A. Levy, A. Magot, Y. Péréon, M.-C. Minot-Myhié, A. Nadaj-Pakleza, C. Nathier, N. Pellegrini, P. Petiot, F. Lofaso, A. Dutry, D. Renard, S. Sacconi, C. Desnuelle, E. Salort-Campana, J. Pouget, V. Tiffreau, D. Vincent, F. Zagnoli
المساهمون: Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Troubles cognitifs dégénératifs et vasculaires - U 1171 - EA 1046 (TCDV), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Lille, Droit et Santé-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Unité de Recherche Pluridisciplinaire Sport, Santé, Société (URePSSS) - ULR 7369 - ULR 4488 (URePSSS), Université d'Artois (UA)-Université du Littoral Côte d'Opale (ULCO)-Université de Lille, Troubles cognitifs dégénératifs et vasculaires - U 1171 (TCDV), Université de Lille-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille)-Institut National de la Santé et de la Recherche Médicale (INSERM), Université d'Artois (UA)-Université de Lille-Université du Littoral Côte d'Opale (ULCO)
المصدر: Molecular Genetics and Metabolism
Molecular Genetics and Metabolism, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩
Molecular Genetics and Metabolism, Elsevier, 2017, Molecular genetics and metabolism, 122 (1-2), pp.80-85. ⟨10.1016/j.ymgme.2017.06.007⟩مصطلحات موضوعية: 0301 basic medicine, Male, Pediatrics, Endocrinology, Diabetes and Metabolism, [SDV]Life Sciences [q-bio], Mesh:Walking, Walking, Mesh:Adult, Respiratory failure, Biochemistry, Late Onset Disorders, Cohort Studies, 0302 clinical medicine, Endocrinology, Mesh:alpha-Glucosidases/therapeutic use, Glycogen Storage Disease Type II, Respiration, Pompe disease, Enzyme replacement therapy, Middle Aged, 3. Good health, Diabetes and Metabolism, Mesh:Late Onset Disorders/drug therapy, Cohort, Breathing, Female, France, Mesh:Respiration, Mesh:alpha-Glucosidases/administration & dosage, Mesh:Enzyme Replacement Therapy*/adverse effects, medicine.drug, Adult, Mesh:Female, medicine.medical_specialty, congenital, hereditary, and neonatal diseases and abnormalities, Mesh:Glycogen Storage Disease Type II/drug therapy, Mesh:Male, Late onset, 03 medical and health sciences, FEV1/FVC ratio, Mesh:alpha-Glucosidases/adverse effects, Mesh:Middle Aged, Mesh:Glycogen Storage Disease Type II/physiopathology, Genetics, medicine, Humans, Mesh:Cohort Studies, Adverse effect, Molecular Biology, Alglucosidase alfa, Mesh:France, Advanced, business.industry, nutritional and metabolic diseases, alpha-Glucosidases, Surgery, Mesh:Humans, 030104 developmental biology, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::2eca040ef3e520953509b66aeb672813Test
https://hal.univ-lille.fr/hal-02369159Test -
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المؤلفون: Djillali Annane, Tarek Sharshar, M. Lejaille, Adam Ogna, David Orlikowski, Frédéric Lofaso, Hélène Prigent, Patricia Samb
المصدر: Brain and Behavior
مصطلحات موضوعية: Adult, Male, medicine.medical_specialty, dysphagia, medicine.medical_treatment, Guillain-Barre Syndrome, intubation, 03 medical and health sciences, Behavioral Neuroscience, 0302 clinical medicine, Swallowing, Tongue, medicine, Respiratory muscle, otorhinolaryngologic diseases, Intubation, Humans, Respiratory function, Original Research, Aged, Guillain-Barre syndrome, business.industry, digestive, oral, and skin physiology, vital capacity, Pneumonia, Ventilator-Associated, tongue strength, Middle Aged, medicine.disease, Prognosis, Dysphagia, Surgery, Pneumonia, Intensive Care Units, medicine.anatomical_structure, 030228 respiratory system, Anesthesia, ICU, Female, Guillain‐Barré syndrome, medicine.symptom, business, Deglutition Disorders, Respiratory Insufficiency, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8b40f683dfd29497914719066641065cTest
http://europepmc.org/articles/PMC5318364Test -
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المؤلفون: Frédéric Lofaso, Nicholas Heming, Cendrine Chaffaut, David Orlikowski, Maria-Antonia Quera Salva, Adam Ogna, Sylvie Chevret, Djillali Annane, Hélène Prigent
المصدر: Neuromuscular disorders : NMD. 27(4)
مصطلحات موضوعية: Adult, Male, medicine.medical_specialty, Vital capacity, Neuromuscular disease, medicine.medical_treatment, Nocturnal, Hypercapnia, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, medicine, Humans, Genetics (clinical), Mechanical ventilation, business.industry, Hazard ratio, Hypoventilation, Neuromuscular Diseases, Middle Aged, medicine.disease, Prognosis, Respiration, Artificial, Surgery, 030228 respiratory system, Neurology, Pediatrics, Perinatology and Child Health, Cohort, Cardiology, Female, Neurology (clinical), medicine.symptom, business, 030217 neurology & neurosurgery, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::c1b7f29db3b91b2e5bcb9b3870b6ca72Test
https://pubmed.ncbi.nlm.nih.gov/28153460Test -
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المؤلفون: Bernard Clair, Sylvie Chevret, Djillali Annane, Raquel Guimarães-Costa, Abdallah Fayssoil, Tanya Stojkovic, Cendrine Chaffaut, Olivier Nardi, David Orlikowski, Adam Ogna, Pascal Laforêt, Karim Wahbi, Anthony Behin, Hélène Prigent, Frédéric Lofaso
المساهمون: HAL UPMC, Gestionnaire, Institut de Myologie, Université Pierre et Marie Curie - Paris 6 (UPMC)-Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Association française contre les myopathies (AFM-Téléthon)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Service de réanimation médicale[Poincaré], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Raymond Poincaré [AP-HP], Centre d’Investigation Clinique 1429 [Garches] (CIC 1429), Hôpital Raymond Poincaré [AP-HP]-Institut National de la Santé et de la Recherche Médicale (INSERM), Service de biostatistique et information médicale de l’hôpital Saint Louis (Equipe ECSTRA) (SBIM), Université Paris Diderot - Paris 7 (UPD7)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Institut national du cancer [Boulogne] (INCA)-Hopital Saint-Louis [AP-HP] (AP-HP), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Service de biochimie et de génétique moléculaire [CHU Cochin], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Cochin [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Service de Cardiologie [CHU Cochin], Service de physiologie et d'explorations fonctionnelles [CHU Raymond-Poincaré], Centre National de la Recherche Scientifique (CNRS)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Association française contre les myopathies (AFM-Téléthon)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Université Pierre et Marie Curie - Paris 6 (UPMC), Hopital Saint-Louis [AP-HP] (AP-HP), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Institut national du cancer [Boulogne] (INCA)-Université Paris Diderot - Paris 7 (UPD7)-Institut National de la Santé et de la Recherche Médicale (INSERM), Hôpital Cochin [AP-HP]
المصدر: PLoS ONE
PLoS ONE, 2016, 11 (4), pp.e0153095. ⟨10.1371/journal.pone.0153095⟩
PLoS ONE, Vol 11, Iss 4, p e0153095 (2016)
PLoS ONE, Public Library of Science, 2016, 11 (4), pp.e0153095. ⟨10.1371/journal.pone.0153095⟩مصطلحات موضوعية: Male, Heredity, Pulmonology, Genetic Linkage, Physiology, Vital Capacity, Cardiomyopathy, lcsh:Medicine, Duchenne Muscular Dystrophy, Cardiovascular Physiology, Muscular Dystrophies, 0302 clinical medicine, Medicine and Health Sciences, Medicine, Respiratory function, Respiratory system, lcsh:Science, Multidisciplinary, Ejection fraction, [SDV.MHEP] Life Sciences [q-bio]/Human health and pathology, Heart, Prognosis, Respiratory Muscles, 3. Good health, Neurology, X-Linked Traits, Sex Linkage, Cardiology, Female, Cardiomyopathies, Respiratory Insufficiency, Research Article, Adult, medicine.medical_specialty, Death Rates, Diastole, 03 medical and health sciences, Population Metrics, Respiratory Failure, Diagnostic Medicine, Internal medicine, Respiratory muscle, Sarcoglycanopathies, Genetics, Humans, Demography, Clinical Genetics, Population Biology, business.industry, lcsh:R, Biology and Life Sciences, Arrhythmias, Cardiac, medicine.disease, Surgery, 030228 respiratory system, Respiratory failure, Muscular Dystrophies, Limb-Girdle, Heart failure, People and Places, lcsh:Q, business, Physiological Processes, Sleep, 030217 neurology & neurosurgery, [SDV.MHEP]Life Sciences [q-bio]/Human health and pathology, Ejection Fraction
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::be31212f679c614f55c1df3526b92aebTest
https://hal.sorbonne-universite.fr/hal-01323875Test -
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المؤلفون: Hélène Prigent, David Orlikowski, Djillali Annane, Frédéric Lofaso, Line Falaize, Nicolas Terzi, Michèle Lejaille
المصدر: Neuromuscular Disorders. 20:493-498
مصطلحات موضوعية: Adult, Male, medicine.medical_specialty, medicine.medical_treatment, Duchenne muscular dystrophy, Electromyography, Intermittent Positive-Pressure Ventilation, Young Adult, 03 medical and health sciences, Tracheostomy, 0302 clinical medicine, Bolus (medicine), stomatognathic system, Swallowing, otorhinolaryngologic diseases, medicine, Humans, Plethysmograph, Prospective Studies, Muscular dystrophy, Genetics (clinical), Mechanical ventilation, medicine.diagnostic_test, business.industry, digestive, oral, and skin physiology, medicine.disease, Deglutition, Surgery, Muscular Dystrophy, Duchenne, Plethysmography, 030228 respiratory system, Neurology, Anesthesia, Pediatrics, Perinatology and Child Health, Respiratory Mechanics, Female, Neurology (clinical), Deglutition Disorders, business, Airway, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::c4c71f7d2c17e0deeae10380e891acccTest
https://doi.org/10.1016/j.nmd.2010.05.009Test -
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المؤلفون: Bruno Louis, Brigitte Fauroux, Karl Leroux, Frédéric Lofaso, Sonia Khirani, David Orlikowski, Line Falaize, Hélène Prigent
المصدر: Respiratory care. 59(7)
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Adult, medicine.medical_specialty, Time Factors, genetic structures, Respiratory rate, Critical Care and Intensive Care Medicine, Models, Biological, Electric Power Supplies, medicine, Portable ventilators, Ventilator settings, Tidal Volume, Humans, Tidal volume, Ventilators, Mechanical, business.industry, Battery (vacuum tube), General Medicine, Home Care Services, Respiration, Artificial, Surgery, Anesthesia, Breathing, business, circulatory and respiratory physiology
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::dccaadd5a7784a66729aa6234516f16aTest
https://pubmed.ncbi.nlm.nih.gov/24149669Test -
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المؤلفون: J. Boudarham, Hélène Prigent, Didier Pradon, Henri Meric, Marie-Christine Durand, Michel Petitjean, Frédéric Lofaso, Line Falaize
المصدر: Chest. 144(3)
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Thorax, Adult, Male, Weakness, medicine.medical_specialty, Diaphragm, Critical Care and Intensive Care Medicine, Diagnosis, Differential, Medicine, Humans, Diaphragmatic weakness, Phrenic nerve, Aged, Muscle Weakness, medicine.diagnostic_test, business.industry, Respiration, Reproducibility of Results, Middle Aged, Respiratory Paralysis, Electric Stimulation, Diaphragm (structural system), Surgery, Plethysmography, medicine.anatomical_structure, Anesthesia, Breathing, Abdomen, Female, medicine.symptom, Cardiology and Cardiovascular Medicine, business, Chest radiograph, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::94e55724cb5f3df004569c1341a0ff0bTest
https://pubmed.ncbi.nlm.nih.gov/23519378Test -
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المؤلفون: Pierre G. Carlier, N. Pellegrini, Pascal Laforêt, Djillali Annane, Robert Carlier, Bruno Eymard, Frédéric Lofaso, Hélène Prigent, David Orlikowski
المصدر: Neuromuscular disorders : NMD. 21(7)
مصطلحات موضوعية: Spirometry, Adult, Male, medicine.medical_specialty, Metabolic myopathy, Gastroenterology, Internal medicine, medicine, Humans, Respiratory function, Enzyme Replacement Therapy, Muscle Strength, Prospective Studies, Respiratory system, Alglucosidase alfa, Genetics (clinical), medicine.diagnostic_test, business.industry, Glycogen Storage Disease Type II, alpha-Glucosidases, Enzyme replacement therapy, Middle Aged, medicine.disease, Recombinant Proteins, Surgery, Respiratory Function Tests, Treatment Outcome, Neurology, Respiratory failure, Pediatrics, Perinatology and Child Health, Breathing, Female, Neurology (clinical), business, Respiratory Insufficiency, medicine.drug
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::eca97f5b2cb78a59716a01f1c9512797Test
https://pubmed.ncbi.nlm.nih.gov/21550241Test