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المؤلفون: Jean-Philippe Brandel, Gabor G. Kovacs, Anna Ladogana, Stéphane Haïk, Simon Mead, Gianluigi Zanusso, Inga Zerr, Byron Caughey, Franc Llorens, Katsuya Satoh, Maurizio Pocchiari, Michael D. Geschwind, Steven J. Collins, Peter Hermann, Alison Green, Piero Parchi, Suvankar Pal, Noriyuki Nishida, Brian S. Appleby
المساهمون: Hermann P., Appleby B., Brandel J.-P., Caughey B., Collins S., Geschwind M.D., Green A., Haik S., Kovacs G.G., Ladogana A., Llorens F., Mead S., Nishida N., Pal S., Parchi P., Pocchiari M., Satoh K., Zanusso G., Zerr I.
المصدر: The lancet
/ Neurology 20(3), 235-246 (2021). doi:10.1016/S1474-4422(20)30477-4
Hermann, P, Appleby, B, Brandel, J, Caughey, B, Collins, S, Geschwind, M D, Green, A, Haïk, S, Kovacs, G G, Ladogana, A, Llorens, F, Mead, S, Nishida, N, Pal, S, Parchi, P, Pocchiari, M, Satoh, K, Zanusso, G & Zerr, I 2021, ' Biomarkers and diagnostic guidelines for sporadic Creutzfeldt-Jakob disease ', The Lancet Neurology, vol. 20, no. 3, pp. 235-246 . https://doi.org/10.1016/S1474-4422Test(20)30477-4
Lancet Neurolمصطلحات موضوعية: Genetic Markers, 0301 basic medicine, diagnosis, animal diseases, diagnosis [Creutzfeldt-Jakob Syndrome], Guidelines as Topic, Neuroimaging, Total tau, diagnostic imaging [Creutzfeldt-Jakob Syndrome], Disease, Bioinformatics, Sensitivity and Specificity, Article, Creutzfeldt-Jakob Syndrome, pre-symptomatic biomarkers, 03 medical and health sciences, 0302 clinical medicine, mental disorders, Sporadic Creutzfeldt-Jakob disease, Humans, Medicine, ddc:610, business.industry, biomarkers, CSF, prion disease, Creutzfeldt-Jakob disease, diagnosis, RT-QuIC, PRNP, genetics [Creutzfeldt-Jakob Syndrome], nervous system diseases, 3. Good health, Clinical neurology, 030104 developmental biology, Clinical value, Biomarker (medicine), real-time quaking induced conversion (RT-QuIC), Neurology (clinical), Prion Proteins, analysis [Biomarkers], business, Biomarkers, 030217 neurology & neurosurgery
وصف الملف: STAMPA; application/vnd.openxmlformats-officedocument.wordprocessingml.document
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::a87524bd7f22e1aa784687a22f110d16Test
https://doi.org/10.1016/s1474-4422Test(20)30477-4 -
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المؤلفون: Masumi Ito, Keiko Mori, Tetsuyuki Kitamoto, Akio Akagi, Atsushi Kobayashi, Yasushi Iwasaki, Mari Yoshida, Yuichi Riku, Yoshinari Kawai, Hiroaki Miyahara
المصدر: Prion
article-version (VoR) Version of Recordمصطلحات موضوعية: Male, 0301 basic medicine, Pathology, medicine.medical_specialty, animal diseases, Akinetic mutism, Case Report, Disease, Degeneration (medical), Biochemistry, Creutzfeldt-Jakob Syndrome, Prion Proteins, pyramidal tract degeneration, 03 medical and health sciences, Cellular and Molecular Neuroscience, chemistry.chemical_compound, Methionine, 0302 clinical medicine, mental disorders, medicine, Humans, business.industry, Neurodegenerative Diseases, Cell Biology, Sporadic Creutzfeldt-Jakob disease, Middle Aged, medicine.disease, Creutzfeldt-Jakob disease, akinetic mutism state, panencephalopathic-type, nervous system diseases, Akinetic Mutism, 030104 developmental biology, Infectious Diseases, chemistry, system degeneration, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::92698924170b298cf6b2edc76d520dcfTest
https://doi.org/10.1080/19336896.2020.1868931Test -
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المؤلفون: Ichiro Fujishima, Kenjiro Kunieda, Akio Kimura, Takayoshi Shimohata, Yuichi Hayashi, Takuya Kudo
المصدر: Prion
article-version (VoR) Version of Recordمصطلحات موضوعية: 0301 basic medicine, pseudobulbar palsy, Pediatrics, medicine.medical_specialty, dysphagia, animal diseases, Case Report, Disease, Biochemistry, Creutzfeldt-Jakob Syndrome, 03 medical and health sciences, Cellular and Molecular Neuroscience, 0302 clinical medicine, Swallowing, Report, mental disorders, otorhinolaryngologic diseases, medicine, Humans, MM2-cortical-type, Tomography, Emission-Computed, Single-Photon, brainstem function, Sporadic CJD, business.industry, Pharyngeal swallowing, Cell Biology, Sporadic Creutzfeldt-Jakob disease, Middle Aged, Pseudobulbar palsy, medicine.disease, Dysphagia, Creutzfeldt-Jakob disease, Deglutition, nervous system diseases, Diffusion Magnetic Resonance Imaging, 030104 developmental biology, Infectious Diseases, Pharynx, Female, medicine.symptom, business, human activities, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::2d2ce8e318a10f866ad3f48b638d666aTest
https://doi.org/10.1080/19336896.2021.1930851Test -
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المؤلفون: Ryoji Naganuma, Masaaki Matsushima, Tetsuyuki Kitamoto, Katsuya Satoh, Ichiro Yabe, Taichi Nomura, Ikuko Iwata
المصدر: Prion
article-version (VoR) Version of Recordمصطلحات موضوعية: 0301 basic medicine, animal diseases, Case Report, Disease, Biochemistry, spastic paralysis, Creutzfeldt-Jakob Syndrome, Prion Proteins, 03 medical and health sciences, Cellular and Molecular Neuroscience, 0302 clinical medicine, mental disorders, Medicine, Humans, Paralysis, Prion protein, Gene, Aged, Gerstmann-Straussler-Scheinker Disease, Gerstmann-Straussler-Scheinker disease, business.industry, Cell Biology, V180i genetic Creutzfeldt-Jakob disease, Middle Aged, Virology, Magnetic Resonance Imaging, Creutzfeldt-Jakob disease, nervous system diseases, 030104 developmental biology, Infectious Diseases, Spinal Cord, Gerstmann-Sträussler-Scheinker disease, Muscle Spasticity, Mutation (genetic algorithm), Mutation, Disease Progression, business, cortical dysfunction, 030217 neurology & neurosurgery, Spastic paralysis
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::391adafb6f18405472c9625904049a51Test
http://europepmc.org/articles/PMC7518757Test -
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المؤلفون: A. V. Vakhlyaev, I. V. Okuneva, O. Yu. Bronov, D. S. Kan’shina
المصدر: Эпилепсия и пароксизмальные состояния, Vol 13, Iss 2, Pp 124-131 (2021)
مصطلحات موضوعية: medicine.medical_specialty, electroencephalography in critically ill patients, Disease, Electroencephalography, Clinical neurophysiology, law.invention, 03 medical and health sciences, 0302 clinical medicine, law, medicine, periodic discharges of three-phase morphology, Ictal, antiepileptic drugs, 030212 general & internal medicine, Medical prescription, creutzfeldt–jakob disease, RC346-429, Intensive care medicine, medicine.diagnostic_test, business.industry, Intensive care unit, Neurology, Etiology, Neurology. Diseases of the nervous system, Neurology (clinical), Differential diagnosis, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::b2364d25c60d8d7afbf01367ab9e0fd5Test
https://doi.org/10.17749/2077-8333/epi.par.con.2021.052Test -
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المؤلفون: Yerai Vado, Joaquín Castilla, Guiomar Perez de Nanclares, Izaro Kortazar-Zubizarreta, Rebeca Ruiz-Onandi, Arrate Pereda, Hasier Eraña, Gonzalo González-Chinchon
المصدر: European Journal of Neurology
مصطلحات موضوعية: Survival period, Pathology, medicine.medical_specialty, Prions, Creutzfeldt–Jakob disease, Disease, Neuropathology, Grey matter, Creutzfeldt-Jakob Syndrome, PRNP, 03 medical and health sciences, 0302 clinical medicine, sporadic CJD, mental disorders, medicine, Humans, 030212 general & internal medicine, neuropathology, medicine.diagnostic_test, business.industry, Brain, Magnetic resonance imaging, Neurodegenerative Diseases, Middle Aged, Magnetic Resonance Imaging, nervous system diseases, medicine.anatomical_structure, Neurology, Gliosis, Dementia and Cognitive Disorders, Original Article, Female, Neurology (clinical), medicine.symptom, business, long survival, 030217 neurology & neurosurgery, Immunostaining
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::11745772abc282609c3d1333318f4929Test
http://europepmc.org/articles/PMC8457091Test -
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المؤلفون: Pedro-Cuesta, Jesus de, Almazan-Isla, Javier, Tejedor Romero, Laura, Ruiz-Tovar, Maria, Avellanal, Fuencisla, Rábano, Alberto, Calero, Miguel, Garcia Lopez, Fernando Jose, Spanish CJD Surveillance Group
المساهمون: Ministerio de Sanidad (España), Instituto de Salud Carlos III, Unión Europea. Comisión Europea, Fundación Centro De Investigación De Enfermedades Neurológicas, Centro de Investigación Biomédica en Red - CIBERNED (Enfermedades Neurodegenerativas)
المصدر: Repisalud
Instituto de Salud Carlos III (ISCIII)
Prion
article-version (VoR) Version of Recordمصطلحات موضوعية: 0301 basic medicine, Epidemiology, Biochemistry, Creutzfeldt-Jakob Syndrome, Prion Diseases, creutzfeldt-jakob disease, 03 medical and health sciences, Cellular and Molecular Neuroscience, 0302 clinical medicine, Political science, mental disorders, Animals, Humans, Registries, Disease surveillance, Surveillance, Brain, registries, Creutzfeldt-jakob disease, Cell Biology, Virology, nervous system diseases, prion proteins, Encephalopathy, Bovine Spongiform, Prion proteins, 030104 developmental biology, Infectious Diseases, Spain, surveillance, Transmissible spongiform encephalopathies, Cattle, epidemiology, Prion Proteins, 030217 neurology & neurosurgery, Research Article, Research Paper
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::40677b1d0834b000e0278a59e90dbe37Test
https://hdl.handle.net/20.500.12105/13930Test -
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المؤلفون: Sara Garbarino, Janis Blevins, Alberto Bizzi, Mark L. Cohen, Lawrence B. Schonberger, Riccardo Pascuzzo, Pierluigi Gambetti, Alexandra L. Young, Neil P. Oxtoby, Brian S. Appleby, Gianmarco Castelli, Daniel C. Alexander
المصدر: Acta Neuropathologica
مصطلحات موضوعية: Adult, Male, 0301 basic medicine, Pathology, medicine.medical_specialty, Prion disease, Creutzfeldt–Jakob disease, Precuneus, Prion propagation, Spongiform degeneration, Creutzfeldt-Jakob Syndrome, Prion Proteins, Pathology and Forensic Medicine, Lesion, 03 medical and health sciences, Cellular and Molecular Neuroscience, Magnetic resonance imaging, 0302 clinical medicine, medicine, Humans, Aged, Original Paper, Disease progression, Neocortex, medicine.diagnostic_test, business.industry, Sporadic Creutzfeldt-Jakob disease, Middle Aged, Diffusion Magnetic Resonance Imaging, Early Diagnosis, 030104 developmental biology, medicine.anatomical_structure, Female, Epicentre, Neurology (clinical), Abnormality, medicine.symptom, business, 030217 neurology & neurosurgery, Diffusion MRI
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::7ec395f186735e26aba46bc09a793c82Test
https://doi.org/10.1007/s00401-020-02168-0Test -
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المؤلفون: Sabina Capellari, Dolores Catelan, Elisa Colaizzo, Antonio Sanguedolce, Annibale Biggeri, Piero Parchi, Dorina Tiple, Alberto Fedele, Maria Puopolo, Giuseppa Lucia Turco, Luana Vaianella, Anna Ladogana, Maurizio Pocchiari, Valerio Aprile
المساهمون: Puopolo M., Catelan D., Capellari S., Ladogana A., Sanguedolce A., Fedele A., Aprile V., Turco G.L., Colaizzo E., Tiple D., Vaianella L., Parchi P., Biggeri A., Pocchiari M.
المصدر: Neuroepidemiology. 54:83-90
مصطلحات موضوعية: Male, Prion diseases, Geographical analysis, Epidemiology, Scan statistic, Geographic Mapping, Disease, 030501 epidemiology, Disease cluster, Cluster case, Cluster cases, Creutzfeldt-Jakob Syndrome, 03 medical and health sciences, 0302 clinical medicine, mental disorders, Creutzfeldt-Jakob disease, Humans, Medicine, Aged, Single cluster, business.industry, Mortality rate, Spatial epidemiology, Bayes Theorem, Sporadic Creutzfeldt-Jakob disease, Middle Aged, Geographical analysi, nervous system diseases, Italy, Relative risk, Female, Neurology (clinical), 0305 other medical science, business, Cartography, 030217 neurology & neurosurgery
وصف الملف: STAMPA
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::cee37bb2e83329bb9fba4cad21cf2846Test
https://doi.org/10.1159/000503234Test -
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المؤلفون: Dhamidhu Eratne, Luke J. Ney, Blair Ney, Qiao-Xin Li, Victoria Lewis, Dennis Velakoulis, Steven J. Collins, Christiane Stehmann
المصدر: Molecular Neurobiology. 58:3983-3991
مصطلحات موضوعية: Adult, Male, 0301 basic medicine, medicine.medical_specialty, Neurology, PrPSc Proteins, Disease duration, Neuroscience (miscellaneous), Disease, Biology, Creutzfeldt-Jakob Syndrome, 03 medical and health sciences, Cellular and Molecular Neuroscience, 0302 clinical medicine, Disease registry, Genotype, medicine, Humans, Registries, Aged, Glycoproteins, Aged, 80 and over, Genetics, Western immunoblotting, Sporadic Creutzfeldt-Jakob disease, Middle Aged, nervous system diseases, 030104 developmental biology, Disease Progression, Female, Biomarkers, 030217 neurology & neurosurgery, Rare disease
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d0c3ddac9cd7d59a4a04711bed0150a7Test
https://doi.org/10.1007/s12035-021-02396-9Test