AT/RT involving the spine and the spinal cord is extremely rare and can occur anywhere along the spinal axis with only few case reports in the literature. As far as spinal AT/RT is concerned these tumors present between 7 months to 17 years of age, with a mean age of 6.5 years with a male preponderance. Usually the location of these tumors is either intramedullary or extramedullary, determining their clinical presentation and course of the disease. Para-spinal AT/RT has many similarities with brain and spinal locations including rapid and fatal clinical course, histopathological features and lack of definitive treatment protocol. Because of the rarity of the para-spinal AT/RT, the present reported literature is not enough to make any concrete conclusions and there is a need for prospective studies to further understand the biology of the disease and also to develop optimal treatment approaches for children with para-spinal AT/RT.
