Primary Sjogren syndrome with diffuse alveolar hemorrhage, cryoglobulinaemia and thrombotic microangiopathy
| العنوان: | Primary Sjogren syndrome with diffuse alveolar hemorrhage, cryoglobulinaemia and thrombotic microangiopathy |
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| المؤلفون: | Parimi Vp, Rajasekhar L |
| المصدر: | Journal of Medical and Scientific Research, Vol 4, Iss 1, Pp 26-27 (2016) |
| بيانات النشر: | KIMS Foundation and Research Center, 2016. |
| سنة النشر: | 2016 |
| مصطلحات موضوعية: | musculoskeletal diseases, Pathology, medicine.medical_specialty, Thrombotic microangiopathy, Sjögren syndrome, cryoglobulinemia, Fibrin, stomatognathic system, hemic and lymphatic diseases, medicine, Sjogren syndrome, Primary Sjögren Syndrome, lcsh:R5-920, alveolar hemorrhage, biology, pulmonary-renal syndrome, Microvascular thrombosis, business.industry, Diffuse alveolar hemorrhage, medicine.disease, Cryoglobulinemia, eye diseases, thrombotic microangiopathy, Small vessel vasculitis, stomatognathic diseases, biology.protein, lcsh:Medicine (General), business |
| الوصف: | Sjogren syndrome is an autoimmune exocrinopathy with various extra glandular manifestations. Cryoglobulinemia, small vessel vasculitis has been reported in 5-10% of patients with primary Sjogren syndrome. It may be associated with a higher prevalence of extra glandular disease in Sjogren patients. Thrombotic microangiopathy (TMA), a potentially lethal condition characterized by microvascular thrombosis due to endothelial injury, is rare in SS. Its most characteristic histological finding is intravascular and intraglomerular fibrin thrombi. The association of Sjogren syndrome, cryoglobulinemia and thrombotic microangiopathy has not been previously reported. We report the first case of Sjogren syndrome with these three manifestations, occurring in combination. |
| تدمد: | 2394-112X 2321-1326 |
| الوصول الحر: | https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d8182aaf8398bc2db3fa1577a5aabd17Test https://doi.org/10.17727/jmsr.2016/4-008Test |
| حقوق: | OPEN |
| رقم الانضمام: | edsair.doi.dedup.....d8182aaf8398bc2db3fa1577a5aabd17 |
| قاعدة البيانات: | OpenAIRE |
| تدمد: | 2394112X 23211326 |
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