دورية أكاديمية

Pulmonary Involvement in Neuromuscular Diseases: A review

التفاصيل البيبلوغرافية
العنوان: Pulmonary Involvement in Neuromuscular Diseases: A review
المؤلفون: Khanbabaee, Ghamartaj, Karim Zadeh, Parvaneh, Nasehi, Mohammad Mahdi, Tabatabaii, Seyed Ahmad, pourghasem, Matin, Alaei, Fariba, Sadr, Saeed, Farahbakhsh, Nazanin, Modarresi, Seyedeh Zalfa, Khazaii, Fatemeh, Soflaee, Maedeh, taghizadeh behbahani, Abdolhamid, Fadavi, Nafiseh, Pourghasem, Mahsa
المصدر: Iranian Journal of Child Neurology; Vol. 17 No. 2 (2023): spring; 9-17 ; 2008-0700 ; 1735-4668
بيانات النشر: Iranian Journal of Child Neurology
سنة النشر: 2023
المجموعة: Portal of Scientific Journals at Shahid Beheshti University of Medical Science
مصطلحات موضوعية: Neuromuscular diseases (NMDs), respiratory muscle weakness(RMW), Respiratory involvement, Pulmonary Involvement in Neuromuscular Diseases: A review
الوصف: Neuromuscular diseases (NMDs) affect muscle function directly or indirectly by affecting nerves or neuromuscular junctions. One of the leading causes of death in patients with NMD is respiratory muscleweakness (RMW). Respiratory involvement in patients with NMD can manifest widely, from mild failure that may initially affect only sleep to severe failure that can be life-threatening. Care approaches include arranged and precise clinical follow-ups of signs of sleep-disordered breathing, daytime hypoventilation, coughing, and swallowing disturbances. This manuscript will review the mechanisms and abnormalities of respiratory function in patients with NMD and help optimize NMD management.
نوع الوثيقة: article in journal/newspaper
وصف الملف: application/pdf
اللغة: English
العلاقة: https://journals.sbmu.ac.ir/ijcn/article/view/40131/31025Test; https://journals.sbmu.ac.ir/ijcn/article/view/40131Test
DOI: 10.22037/ijcn.v17i2.40131
الإتاحة: https://doi.org/10.22037/ijcn.v17i2.40131Test
https://journals.sbmu.ac.ir/ijcn/article/view/40131Test
حقوق: Copyright (c) 2023 Iranian Journal of Child Neurology
رقم الانضمام: edsbas.408EC0CB
قاعدة البيانات: BASE