INTERMITTENT POSITIVE AIRWAY PRESSURE BY NASAL MASK AS A TREATMENT FOR RESPIRATORY INSUFFICIENCY IN A PATIENT WITH CHARCOT-MARIE-TOOTH DISEASE
العنوان: | INTERMITTENT POSITIVE AIRWAY PRESSURE BY NASAL MASK AS A TREATMENT FOR RESPIRATORY INSUFFICIENCY IN A PATIENT WITH CHARCOT-MARIE-TOOTH DISEASE |
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المؤلفون: | W. De Backer, P. De Jonghe, Denise Daems, Johan Verbraecken, K. Darquennes |
المصدر: | Acta clinica Belgica |
بيانات النشر: | Informa UK Limited, 2006. |
سنة النشر: | 2006 |
مصطلحات موضوعية: | Adult, medicine.medical_specialty, Cough reflex, Positive pressure, Intermittent Positive-Pressure Ventilation, Sleep Apnea Syndromes, Charcot-Marie-Tooth Disease, Positive airway pressure, medicine, Humans, Respiratory system, business.industry, Muscle weakness, General Medicine, medicine.disease, nervous system diseases, respiratory tract diseases, Surgery, Pneumonia, Respiratory failure, Anesthesia, Female, medicine.symptom, Respiratory Insufficiency, business, Hypopnea |
الوصف: | Charcot-Marie-Tooth disease (CMT) is a slowly progressive hereditary neuropathy characterised by degeneration of motor and sensory peripheral nerves resulting in distal muscle weakness with atrophy and sensory impairment. We report a 35-year-old woman with CMT presenting with respiratory failure due to a pneumonia, sputum impaction and insufficient cough reflex. After recovery, we diagnosed a very severe restrictive lung function disturbance caused by muscle weakness and a possible coexistent unilateral diaphragm paralysis. A very severe REM (Rapid Eye Movement Sleep) related sleep hypopnea syndrome was successfully treated with Nasal Intermittent Positive Pressure Ventilation (NIPPV). |
تدمد: | 2295-3337 1784-3286 0001-5512 |
الوصول الحر: | https://explore.openaire.eu/search/publication?articleId=doi_dedup___::1e00a41d07b0305d7a3a4fce9f94576dTest https://doi.org/10.1179/acb.2006.030Test |
حقوق: | CLOSED |
رقم الانضمام: | edsair.doi.dedup.....1e00a41d07b0305d7a3a4fce9f94576d |
قاعدة البيانات: | OpenAIRE |
تدمد: | 22953337 17843286 00015512 |
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