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المؤلفون: Caroline Ovaert, Sylvie Tuffery-Giraud, Sarah Leonard-Louis, Anthony Béhin, Sophie Guillaumont, Maximilien Sochala, Emmanuelle Campana-Salort, Frédérique Audic, Michèle Mayer, Damien Bonnet, Raul Juntas Morales, Mireille Cossée, Isabelle Desguerre, Christophe Meune, Pascal Laforêt, Rabah Ben Yaou, Brigitte Chabrol, Djillali Annane, David Orlikowski, François Godart, Malika Saadi, Helge Amthor, Tanya Stojkovic, Ulrike Walther-Louvier, Frédéric Lofaso, Pascal Amedro, Raphaël Porcher, Céline Tard, Claire Delcourte, Vincent Tiffreau, Karim Wahbi, Christine Barnerias, Guillaume Bassez, Bertrand Fontaine, Arnaud Isapof, Gregoire De La Villeon, Guy Vaksmann, François Rivier, Denis Duboc, Henri Marc Bécane, Philippe Ravaud, Hélène Prigent, Emmanuelle Jaillette, Abdallah Fayssoil, Bruno Eymard
المساهمون: Université de Lille, Univ. Artois, Univ. Littoral Côte d’Opale, Unité de Recherche Pluridisciplinaire Sport, Santé, Société (URePSSS) - ULR 7369 - ULR 4488 [URePSSS], Centre de Recherche Épidémiologie et Statistique Sorbonne Paris Cité (CRESS (U1153 / UMR_A_1125 / UMR_S_1153)), Conservatoire National des Arts et Métiers [CNAM] (CNAM)-Université Sorbonne Paris Cité (USPC)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Paris (UP)-Institut National de Recherche pour l’Agriculture, l’Alimentation et l’Environnement (INRAE), Physiologie & médecine expérimentale du Cœur et des Muscles [U 1046] (PhyMedExp), Université de Montpellier (UM)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Centre Hospitalier Régional Universitaire [Montpellier] (CHRU Montpellier), Conservatoire National des Arts et Métiers [CNAM] (CNAM), HESAM Université - Communauté d'universités et d'établissements Hautes écoles Sorbonne Arts et métiers université (HESAM)-HESAM Université - Communauté d'universités et d'établissements Hautes écoles Sorbonne Arts et métiers université (HESAM)-Université Sorbonne Paris Cité (USPC)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Université Paris Cité (UPCité)-Institut National de Recherche pour l’Agriculture, l’Alimentation et l’Environnement (INRAE), CHU Necker - Enfants Malades [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Handicap neuromusculaire : Physiopathologie, Biothérapie et Pharmacologies appliquées (END-ICAP), Université de Versailles Saint-Quentin-en-Yvelines (UVSQ)-Institut National de la Santé et de la Recherche Médicale (INSERM), Marseille medical genetics - Centre de génétique médicale de Marseille (MMG), Aix Marseille Université (AMU)-Institut National de la Santé et de la Recherche Médicale (INSERM), Département de génétique médicale [Hôpital de la Timone - APHM], Aix Marseille Université (AMU)-Assistance Publique - Hôpitaux de Marseille (APHM)- Hôpital de la Timone [CHU - APHM] (TIMONE)-Institut National de la Santé et de la Recherche Médicale (INSERM), Clinique de pneumologie [CHRU Lille], Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Montpellier (UM)-Centre National de la Recherche Scientifique (CNRS), CHU Trousseau [APHP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), Unité de Recherche Pluridisciplinaire Sport, Santé, Société (URePSSS) - ULR 7369 - ULR 4488 (URePSSS), Université d'Artois (UA)-Université du Littoral Côte d'Opale (ULCO)-Université de Lille, Neurologie, maladies neuro-musculaires [Hôpital de la Timone - APHM], Aix Marseille Université (AMU)-Assistance Publique - Hôpitaux de Marseille (APHM)- Hôpital de la Timone [CHU - APHM] (TIMONE), CHU Pitié-Salpêtrière [AP-HP], Hôpital Cochin [AP-HP], Centre de recherche en Myologie – U974 SU-INSERM, Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU), Filière Neuromusculaire (FILNEMUS), Infection et inflammation (2I), Université de Montpellier (UM), Centre Hospitalier de Versailles André Mignot (CHV), Institut des Neurosciences de Montpellier (INM), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Montpellier (UM), Marqueurs cardiovasculaires en situation de stress (MASCOT (UMR_S_942 / U942)), Institut National de la Santé et de la Recherche Médicale (INSERM)-Groupe Hospitalier Saint Louis - Lariboisière - Fernand Widal [Paris], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Centre National de la Recherche Scientifique (CNRS)-Université Paris Cité (UPCité)-Université Sorbonne Paris Nord, Centre d’Investigation Clinique 1429 [Garches] (CIC 1429), Hôpital Raymond Poincaré [AP-HP]-Institut National de la Santé et de la Recherche Médicale (INSERM), Service de cardiologie Pédiatrique [Marseille], Hôpital de la Timone [CHU - APHM] (TIMONE), Hôpital Raymond Poincaré [AP-HP], Paris-Centre de Recherche Cardiovasculaire (PARCC (UMR_S 970/ U970)), Hôpital Européen Georges Pompidou [APHP] (HEGP), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpitaux Universitaires Paris Ouest - Hôpitaux Universitaires Île de France Ouest (HUPO)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpitaux Universitaires Paris Ouest - Hôpitaux Universitaires Île de France Ouest (HUPO)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Université Paris Cité (UPCité)
المصدر: European Heart Journal
European Heart Journal, Oxford University Press (OUP): Policy B, 2021, ⟨10.1093/eurheartj/ehab054⟩
European Heart Journal, 2021, ⟨10.1093/eurheartj/ehab054⟩مصطلحات موضوعية: Duchenne muscular dystrophy, medicine.medical_specialty, [SDV]Life Sciences [q-bio], Cardiomyopathy, Angiotensin-Converting Enzyme Inhibitors, Heart failure, Angiotensin-converting enzyme inhibitors, 030204 cardiovascular system & hematology, Lower risk, Ventricular Function, Left, Angiotensin Receptor Antagonists, 03 medical and health sciences, 0302 clinical medicine, [SDV.MHEP.CSC]Life Sciences [q-bio]/Human health and pathology/Cardiology and cardiovascular system, Internal medicine, medicine, Humans, Registries, cardiovascular diseases, 030212 general & internal medicine, Medical prescription, Child, ComputingMilieux_MISCELLANEOUS, Heart Failure, biology, business.industry, Proportional hazards model, Hazard ratio, Angiotensin-converting enzyme, medicine.disease, Confidence interval, 3. Good health, Muscular Dystrophy, Duchenne, Treatment Outcome, Child, Preschool, biology.protein, Cardiology and Cardiovascular Medicine, business, cardiomyopathy
وصف الملف: application/octet-stream
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::f84a4eeaae527cf105631ef315b278f7Test
https://doi.org/10.1093/eurheartj/ehab054Test -
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المصدر: Muscle & Nerve. 63:327-335
مصطلحات موضوعية: Adult, Male, 0301 basic medicine, medicine.medical_specialty, Physiology, Neural Conduction, Phrenic nerve conduction, Diagnostic accuracy, 030105 genetics & heredity, Diaphragmatic paralysis, Sensitivity and Specificity, Pulmonary function testing, 03 medical and health sciences, Cellular and Molecular Neuroscience, Esophagus, 0302 clinical medicine, Predictive Value of Tests, Physiology (medical), Internal medicine, mental disorders, Pressure, Transducers, Pressure, medicine, Respiratory muscle, Humans, Aged, Retrospective Studies, business.industry, Electrodiagnosis, Stomach, Transdiaphragmatic pressure, Middle Aged, Respiratory Paralysis, Predictive value, Respiratory Muscles, Respiratory Function Tests, Highly sensitive, Phrenic Nerve, Cardiology, Female, Neurology (clinical), business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::5e12c907a7cc46300b897a91d49927b4Test
https://doi.org/10.1002/mus.27144Test -
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المؤلفون: Bruno Louis, Karl Leroux, Ghilas Boussaïd, Hélène Prigent, Frédéric Lofaso
المساهمون: Equipe de Recherche Paramédicale sur le Handicap NeuroMoteur (ERPHAN), Université de Versailles Saint-Quentin-en-Yvelines (UVSQ)-Université Paris-Saclay, Handicap neuromusculaire : Physiopathologie, Biothérapie et Pharmacologies appliquées (END-ICAP), Université de Versailles Saint-Quentin-en-Yvelines (UVSQ)-Institut National de la Santé et de la Recherche Médicale (INSERM), Molecular virology and immunology – Physiopathology and therapeutic of chronic viral hepatitis (Team 18) (Inserm U955), Institut Mondor de Recherche Biomédicale (IMRB), Institut National de la Santé et de la Recherche Médicale (INSERM)-IFR10-Université Paris-Est Créteil Val-de-Marne - Paris 12 (UPEC UP12)-Institut National de la Santé et de la Recherche Médicale (INSERM)-IFR10-Université Paris-Est Créteil Val-de-Marne - Paris 12 (UPEC UP12), Biomécanique & Appareil Respiratoire (BAR), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université Paris-Est Créteil Val-de-Marne - Paris 12 (UPEC UP12)-Centre National de la Recherche Scientifique (CNRS)
المصدر: Respiratory Care
Respiratory Care, Daedalus Enterprises Inc, 2020, 65 (9), pp.1258-1267. ⟨10.4187/respcare.07213⟩مصطلحات موضوعية: Pulmonary and Respiratory Medicine, medicine.medical_specialty, Central sleep apnea, Respiratory rate, [SDV]Life Sciences [q-bio], Hyperpnea, Critical Care and Intensive Care Medicine, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, bench study, Tidal Volume, medicine, Humans, Cheyne-Stokes Respiration, Tidal volume, servomechanism, Continuous Positive Airway Pressure, lung model, adaptive servo ventilation, business.industry, pressure support, non-invasive ventilation, Hypoventilation, General Medicine, medicine.disease, Sleep Apnea, Central, 030228 respiratory system, Breathing, Cardiology, Transient (oscillation), medicine.symptom, business, Hypopnea
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::1d1259b8e893b7c1304ed65eb49b4220Test
https://doi.org/10.4187/respcare.07213Test -
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المؤلفون: Hélène Prigent, Frédéric Lofaso, Nicolas Terzi
المصدر: ERJ Open Research
article-version (VoR) Version of Record
ERJ Open Research, Vol 7, Iss 4 (2021)مصطلحات موضوعية: Pulmonary and Respiratory Medicine, COPD, medicine.medical_specialty, Exacerbation, business.industry, Conflict of interest, Aspiration pneumonia, medicine.disease, respiratory tract diseases, Open research, Swallowing, Copd exacerbation, Correspondence, Medicine, In patient, business, Intensive care medicine
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::76857b87af7ff8ebd4ab56cef7833588Test
https://pubmed.ncbi.nlm.nih.gov/34708117Test -
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المؤلفون: Sylvie Chevret, Paris Meng, Pascal Crenn, Cendrine Chaffaut, Bernard Clair, Adam Ogna, Djillali Annane, Hélène Prigent, David Orlikowski, Pascal Laforêt, Abdallah Fayssoil, Frédéric Lofaso
المصدر: Pediatric pulmonologyREFERENCES. 56(7)
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Adult, medicine.medical_specialty, Adolescent, medicine.medical_treatment, Duchenne muscular dystrophy, Nutritional Status, Sepsis, 03 medical and health sciences, Young Adult, 0302 clinical medicine, Swallowing, 030225 pediatrics, Internal medicine, medicine, Respiratory muscle, Humans, Respiratory function, Respiratory system, Mechanical ventilation, Univariate analysis, business.industry, Swallowing Disorders, medicine.disease, Prognosis, Respiratory Muscles, Deglutition, Muscular Dystrophy, Duchenne, 030228 respiratory system, Pediatrics, Perinatology and Child Health, Median body, business, Deglutition Disorders
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8475a904e8b59112dc2bbfbc3621000cTest
https://pubmed.ncbi.nlm.nih.gov/33939888Test -
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المؤلفون: Pascal Crenn, Tanya Stojkovic, Dominique Mompoint, Hélène Prigent, David Orlikowski, Helge Amthor, Cendrine Chaffaut, Laure Lamothe, Susana Quijano Roy, Guillaume Bassez, Sylvie Chevret, Djillali Annane, Bernard Clair, Pascal Laforêt, Frédéric Lofaso, Robert Carlier, Paris Meng, Adam Ogna, Anthony Behin, Abdallah Fayssoil, Bruno Eymard
المصدر: Journal of Neuromuscular Diseases. 6:55-64
مصطلحات موضوعية: Adult, Male, 0301 basic medicine, Vital capacity, medicine.medical_specialty, Adolescent, Duchenne muscular dystrophy, Diaphragm, Diaphragmatic breathing, Muscle disorder, Pulmonary function testing, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, Respiratory muscle, Humans, Medicine, Child, Retrospective Studies, Ultrasonography, business.industry, Respiration, Organ Size, Middle Aged, musculoskeletal system, medicine.disease, Respiration, Artificial, Diaphragm (structural system), Muscular Dystrophy, Duchenne, Cross-Sectional Studies, 030104 developmental biology, Neurology, Cardiology, Median body, Neurology (clinical), business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::54576aaa09a075dc125c0779852f4c1bTest
https://doi.org/10.3233/jnd-180326Test -
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المؤلفون: Lorena Del Amo Castrillo, Aurélien Boré, Isabelle Vaugier, Line Falaize, Hélène Prigent, Frédéric Lofaso, Matthieu Lacombe, David Orlikowski
المصدر: Respiratory Care. 64:255-261
مصطلحات موضوعية: Adult, Male, Pulmonary and Respiratory Medicine, Respiratory Therapy, Neuromuscular disease, medicine.medical_treatment, Home Care Services, Hospital-Based, Peak Expiratory Flow Rate, Critical Care and Intensive Care Medicine, Continuous mandatory ventilation, Cohort Studies, Inspiratory Capacity, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Tidal Volume, Respiratory muscle, Humans, Medicine, Tidal volume, Aged, Retrospective Studies, Mechanical ventilation, Ventilators, Mechanical, business.industry, Neuromuscular Diseases, General Medicine, Middle Aged, Prognosis, medicine.disease, Respiration, Artificial, Treatment Outcome, Cough, 030228 respiratory system, Respiratory failure, Intermittent positive pressure breathing, Anesthesia, Female, France, Respiratory Insufficiency, business
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::2b7cba80dfbe23f245439d7fafc05103Test
https://doi.org/10.4187/respcare.06259Test -
8Effect and impact of mechanical ventilation in myotonic dystrophy type 1: a prospective cohort study
المؤلفون: Hélène Prigent, Frédéric Lofaso, Pascal Laforêt, Ghilas Boussaïd, Jean-Claude Raphaël, Djillali Annane, David Orlikowski
المصدر: Thorax. 73:1075-1078
مصطلحات موضوعية: Adult, Male, Pulmonary and Respiratory Medicine, medicine.medical_specialty, medicine.medical_treatment, Myotonic dystrophy, Home ventilation, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, Humans, Myotonic Dystrophy, Medicine, Non-invasive ventilation, In patient, Prospective Studies, Prospective cohort study, Mechanical ventilation, Proportional hazards model, business.industry, Prognosis, medicine.disease, Respiration, Artificial, Respiratory Function Tests, Survival Rate, 030228 respiratory system, Breathing, Patient Compliance, Female, France, Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Follow-Up Studies
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::db3dda253991ba12111bff08ddec0e8fTest
https://doi.org/10.1136/thoraxjnl-2017-210610Test -
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المؤلفون: Gilbert Desmarais, Frédéric Lofaso, Dante Brasil Santos, Sandrine Cognet, Bruno Louis, L. Falaize, Hélène Prigent, Adam Ogna, David Orlikowski
المصدر: Neuromuscular Disorders. 27:518-525
مصطلحات موضوعية: Adult, Male, medicine.medical_specialty, Weakness, Neuromuscular disease, Diaphragm, Diaphragmatic breathing, Stimulation, Sensitivity and Specificity, 03 medical and health sciences, Esophagus, 0302 clinical medicine, Internal medicine, Pressure, medicine, Humans, Respiratory muscle weakness, Genetics (clinical), Mouth, Muscle Weakness, business.industry, Muscle weakness, Neuromuscular Diseases, Middle Aged, musculoskeletal system, medicine.disease, Nasal pressure, Respiratory Muscles, Respiratory Function Tests, Surgery, Phrenic Nerve, Inhalation, 030228 respiratory system, Neurology, Mouth pressure, Pediatrics, Perinatology and Child Health, Cardiology, Female, Neurology (clinical), medicine.symptom, business, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::e478c38ee86be07bebba5ffba6e3c629Test
https://doi.org/10.1016/j.nmd.2017.01.022Test -
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المؤلفون: Hélène Prigent, Christian Devaux, Frédéric Lofaso, David Orlikowski, Gilbert Caranhac, Ghilas Boussaïd, Djillali Annane
المصدر: Journal of Neuromuscular Diseases. 4:165-168
مصطلحات موضوعية: Adult, Male, Emergency Medical Services, medicine.medical_specialty, Referral, medicine.medical_treatment, Muscular Dystrophies, 03 medical and health sciences, 0302 clinical medicine, Oxygen therapy, Health care, Emergency medical services, Humans, Medicine, Hospital Mortality, Muscular dystrophy, Hospitals, Teaching, Retrospective Studies, Cause of death, business.industry, Retrospective cohort study, medicine.disease, Hospitalization, Treatment Outcome, 030228 respiratory system, Neurology, Respiratory failure, Emergency medicine, Female, France, Neurology (clinical), Respiratory Insufficiency, business, 030217 neurology & neurosurgery, Preliminary Data
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::6c0a880250c23a998397d1df5a693f0bTest
https://doi.org/10.3233/jnd-170212Test