المؤلفون: Ruiz Mar, Gabriela¹ (AUTHOR) rvgaby@hotmail.com, Cárdenas Serrano, Óscar E.² (AUTHOR), Roldan García, Jorge³ (AUTHOR), Cañavera-Constantino, Abraham⁴ (AUTHOR), Menéndez Trejo, Víctor M.⁵ (AUTHOR), Chapa Azuela, Óscar⁶ (AUTHOR)

المصدر: Reumatología Clínica. Sep2019, Vol. 15 Issue 5, pe27-e29. 3p.

مصطلحات موضوعية: *RETROPERITONEAL fibrosis, *KIDNEY pelvis, *LUMBOSACRAL region, *GERMINAL centers, *PLASMA cells, *COMPUTED tomography, *PANCREATECTOMY

مستخلص: Paciente de 55 años de edad con cuadro de dolor en flanco izquierdo irradiado a región lumbar de 4 meses de evolución, con tomografía axial computarizada que reporta tumoración quística en región retroperitoneal que comprime uréter y sistema pielocaliceal izquierdo en contacto con cuerpo y cola de páncreas. Es intervenida quirúrgicamente y se encuentra en reporte patológico definitivo fibrosis retroperitoneal nodular asociada a IgG4; con Ki67 positivo en centros germinales (5%) e IgG4 positivo (40 células plasmáticas en 3 campos de 40x) por inmunohistoquímica. La fibrosis retroperitoneal nodular es una enfermedad poco frecuente, de evolución paulatina con excelente respuesta al manejo con esteroides. El tratamiento quirúrgico se reserva para casos que comprometen estructuras adyacentes, por lo que el identificarlo al estudiar una tumoración retroperitoneal conlleva un mejor pronóstico y sobrevida. The patient was a 55-year-old woman with a 4-month history of pain in left flank that irradiated to the lumbar region. Computed tomography revealed a cystic tumor in the retroperitoneal region that compresses the ureter and left renal pelvis in contact with pancreatic body and tail. Surgery was performed and the definitive pathological report diagnosed nodular retroperitoneal fibrosis associated with IgG4; Ki67-positive in germinal centers (5%) and IgG4-positive (40 plasma cells in 3 fields of 40x) by immunohistochemistry. Retroperitoneal fibrosis is a rare disease, that develops gradually and has an excellent response to steroid management. Surgical treatment is reserved for cases that compromise adjacent structures. Thus, identifying it when studying a retroperitoneal tumor leads to better prognosis and survival. [ABSTRACT FROM AUTHOR]

العنوان البديل: Ormond's disease: Experience with five cases.

المصدر: Reumatología Clínica. jul/ago2010, Vol. 6 Issue 4, p199-202. 4p.

مصطلحات موضوعية: *RETROPERITONEAL fibrosis, *ETIOLOGY of diseases, *IMMUNOSUPPRESSIVE agents, *RETROSPECTIVE studies, *TOMOGRAPHY, *MAGNETIC resonance imaging, *ABDOMINAL aortic aneurysms

المؤلفون: Suárez-Díaz, Silvia, Núñez-Batalla, Faustino, Fernández-García, María Soledad, Fernández-Llana, María Belén, Yllera-Gutiérrez, Carmen, Caminal-Montero, Luis

المصدر: Reumatología Clínica; Sep2020:Part 2, Vol. 16 Issue 5, p416-418, 3p

مصطلحات موضوعية: CANKER sores, BEHCET'S disease, RETROPERITONEAL fibrosis, PAROTID glands, PLASMA cells, NECROTIZING pancreatitis, PHLEBITIS

مستخلص: La enfermedad relacionada con IgG4 (ER-IgG4) se caracteriza por un infiltrado linfoplasmocítico rico en células plasmáticas IgG4 positivas, fibrosis estoriforme y flebitis obliterativa. Se puede presentar como seudotumor orbitario, parotidomegalia, nefritis túbulo intersticial, fibrosis retroperitoneal o pancreatitis, aunque prácticamente cualquier órgano puede verse afectado. Presentamos el caso de una mujer de 37 años, que presenta un cuadro de disfonía severa y aftosis oral dolorosa recurrente, con unos hallazgos histopatológicos a nivel laríngeo que muestran infiltrado linfoplasmocítico y positividad para IgG4, así como amplios estudios descartando otras etiologías, por lo que se confirma una laringitis por ER-IgG4, cuya descripción en la literatura es excepcional. IgG4-related disease is characterized by a lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells, storiform fibrosis and obliterative phlebitis. It can present as parotid gland enlargement, tubulointerstitial nephritis, retroperitoneal fibrosis or pancreatitis, although nearly any organ can be affected. We report the case of a 37-year-old woman who presented with severe dysphonia and recurrent painful aphthous ulcers, with histopathological findings at the level of the larynx that revealed a lymphoplasmacytic infiltrate and IgG4 positivity. In addition, extensive studies were performed to rule out other diseases. Thus the diagnosis was IgG4-related laryngitis, an exceptional finding in the literature. [ABSTRACT FROM AUTHOR]

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المؤلفون: Luis Caminal-Montero, Silvia Suárez-Díaz, Carmen Yllera-Gutiérrez, Faustino Núñez-Batalla, María Belén Fernández-Llana, María Soledad Fernández-García

المصدر: Reumatología Clínica. 16:416-418

مصطلحات موضوعية: Pathology, medicine.medical_specialty, Parotid gland enlargement, business.industry, Laryngitis, medicine.disease, Retroperitoneal fibrosis, Tubulointerstitial Nephritis, Rheumatology, Lymphoplasmacytic Infiltrate, Fibrosis, Medicine, Pancreatitis, medicine.symptom, business

الوصف: espanolLa enfermedad relacionada con IgG4 (ER-IgG4) se caracteriza por un infiltrado linfoplasmocitico rico en celulas plasmaticas IgG4 positivas, fibrosis estoriforme y flebitis obliterativa. Se puede presentar como seudotumor orbitario, parotidomegalia, nefritis tubulo intersticial, fibrosis retroperitoneal o pancreatitis, aunque practicamente cualquier organo puede verse afectado. Presentamos el caso de una mujer de 37 anos, que presenta un cuadro de disfonia severa y aftosis oral dolorosa recurrente, con unos hallazgos histopatologicos a nivel laringeo que muestran infiltrado linfoplasmocitico y positividad para IgG4, asi como amplios estudios descartando otras etiologias, por lo que se confirma una laringitis por ER-IgG4, cuya descripcion en la literatura es excepcional. EnglishIgG4-related disease is characterized by a lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells, storiform fibrosis and obliterative phlebitis. It can present as parotid gland enlargement, tubulointerstitial nephritis, retroperitoneal fibrosis or pancreatitis, although nearly any organ can be affected. We report the case of a 37-year-old woman who presented with severe dysphonia and recurrent painful aphthous ulcers, with histopathological findings at the level of the larynx that revealed a lymphoplasmacytic infiltrate and IgG4 positivity. In addition, extensive studies were performed to rule out other diseases. Thus the diagnosis was IgG4-related laryngitis, an exceptional finding in the literature.

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_________::9b5c31f4b12c1214c28eb05dee5bf835Test
https://doi.org/10.1016/j.reuma.2018.08.011Test

المؤلفون: Óscar E. Cárdenas Serrano, Óscar Chapa Azuela, Gabriela Ruiz Mar, Víctor M. Menéndez Trejo, Jorge Roldan García, Abraham Cañavera-Constantino

المصدر: Reumatologia clinica. 15(5)

مصطلحات موضوعية: medicine.medical_specialty, Retroperitoneal fibrosis, Diagnosis, Differential, 03 medical and health sciences, 0302 clinical medicine, Ureter, Lumbar, Medicine, Humans, Retroperitoneal Neoplasms, Pathological, business.industry, Retroperitoneal Fibrosis, General Medicine, Middle Aged, medicine.disease, medicine.anatomical_structure, Ki-67 Antigen, 030220 oncology & carcinogenesis, Immunoglobulin G, Immunohistochemistry, 030211 gastroenterology & hepatology, IgG4-related disease, Female, Radiology, Immunoglobulin G4-Related Disease, Differential diagnosis, medicine.symptom, business, Rare disease

الوصف: The patient was a 55-year-old woman with a 4-month history of pain in left flank that irradiated to the lumbar region. Computed tomography revealed a cystic tumor in the retroperitoneal region that compresses the ureter and left renal pelvis in contact with pancreatic body and tail. Surgery was performed and the definitive pathological report diagnosed nodular retroperitoneal fibrosis associated with IgG4; Ki67-positive in germinal centers (5%) and IgG4-positive (40 plasma cells in 3 fields of 40x) by immunohistochemistry. Retroperitoneal fibrosis is a rare disease, that develops gradually and has an excellent response to steroid management. Surgical treatment is reserved for cases that compromise adjacent structures. Thus, identifying it when studying a retroperitoneal tumor leads to better prognosis and survival.

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::fb5deca696f897da515849baaa4484c4Test
https://pubmed.ncbi.nlm.nih.gov/28734747Test

المؤلفون: Luis Caminal-Montero, Carmen Yllera-Gutiérrez, María Belén Fernández-Llana, Faustino Núñez-Batalla, Silvia Suárez-Díaz, María Soledad Fernández-García

المصدر: Reumatologia clinica. 16(5 Pt 2)

مصطلحات موضوعية: Adult, medicine.medical_specialty, business.industry, fungi, General Medicine, Behcet's disease, Laryngitis, medicine.disease, Retroperitoneal fibrosis, Dermatology, Lymphoplasmacytic Infiltrate, Fibrosis, parasitic diseases, medicine, Pancreatitis, Humans, IgG4-related disease, Female, Stomatitis, Aphthous, Immunoglobulin G4-Related Disease, medicine.symptom, business, Stomatitis

الوصف: IgG4-related disease is characterized by a lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells, storiform fibrosis and obliterative phlebitis. It can present as parotid gland enlargement, tubulointerstitial nephritis, retroperitoneal fibrosis or pancreatitis, although nearly any organ can be affected. We report the case of a 37-year-old woman who presented with severe dysphonia and recurrent painful aphthous ulcers, with histopathological findings at the level of the larynx that revealed a lymphoplasmacytic infiltrate and IgG4 positivity. In addition, extensive studies were performed to rule out other diseases. Thus the diagnosis was IgG4-related laryngitis, an exceptional finding in the literature.

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::aca0c325997a4c13044b64e3ec2f7bfeTest
https://pubmed.ncbi.nlm.nih.gov/30297197Test

المؤلفون: Virginia Velasco-Tirado, Sheila Martín-Barba, Moncef Belhassen-García, Adela Carpio-Pérez, Sandra Inés-Revuelta, Natalia Castro-Iglesias, Javier Pardo-Lledias

المصدر: Reumatologia clinica. 6(4)

مصطلحات موضوعية: medicine.medical_specialty, Pediatrics, Ormond's Disease, business.industry, General Medicine, Disease, University hospital, Retroperitoneal fibrosis, Annual incidence, ORMOND DISEASE, Surgery, medicine, Etiology, medicine.symptom, Surgical treatment, business

الوصف: a b s t r a c t Ormond's disease (OD) is an uncommon process with an annual incidence nearing 1 per million inhabitants. The etiology in most of the cases is unknown and several pathogenic mechanisms are implicated in secondary OD. Ormond disease is characterized by a fibrotic and inflammatory mass with three different clinical features: 1) retroperitoneal fibrosis, 2) perianeurysmatic retroperitoneal fibrosis and 3) inflammatory abdominal aortic aneurysms. Classic management is based on surgical treatment associated or not with steroids. Immunosuppressive agents have been used in the last years with unclear results. We report five cases from the University Hospital of Salamanca occurring during 2000-2008. We highlight the lack of trials designed to establish clinical guidelines for the treatment of the disease and improvement of outcome.

الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::5cbceb675ad5c25c71042053b4aeead8Test
https://pubmed.ncbi.nlm.nih.gov/21794713Test

العنوان البديل: Paniculitis mesentérica en un paciente con espondilitis anquilosante. (Spanish)

المؤلفون: Tejón Menéndez, Patricia, Alonso, Sara, Alperi, Mercedes, Ballina, Javier

المصدر: Reumatología Clínica; may/jun2013, Vol. 9 Issue 3, p197-197, 1p

مصطلحات موضوعية: MESENTERIC artery diseases, ANKYLOSING spondylitis, ADIPOSE tissues, INFLAMMATION, RETROPERITONEAL fibrosis, AUTOIMMUNE diseases, UVEITIS, PATIENTS