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1
المؤلفون: Jean-François Goossens, Sylviane Marouillat, Amandine Descat, Thomas Baranek, Blandine Madji Hounoum, Clément Bruno, Samuel Leman, Christian R. Andres, Patrick Vourc'h, Franck Patin, Lydie Nadal-Desbarats, Philippe Corcia, Hélène Blasco, Anne-Frédérique Dessein
المصدر: Molecular Neurobiology. 54:5361-5374
مصطلحات موضوعية: Male, 0301 basic medicine, Genetically modified mouse, Proline, Arginine, Neuroscience (miscellaneous), Mice, Transgenic, Pharmacology, Biology, Bioinformatics, 03 medical and health sciences, Cellular and Molecular Neuroscience, 0302 clinical medicine, Metabolomics, medicine, Metabolome, Animals, Humans, Longitudinal Studies, Amyotrophic lateral sclerosis, Motor Neurons, Superoxide Dismutase, Amyotrophic Lateral Sclerosis, Tryptophan, Metabolism, medicine.disease, Omics, Disease Models, Animal, 030104 developmental biology, medicine.anatomical_structure, Neurology, Cerebral cortex, Female, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::1b27f99c7ee00eb989dae4c672a51860Test
https://doi.org/10.1007/s12035-016-0078-xTest -
2
المؤلفون: Sylviane Marouillat, Christian R. Andres, Patrick Vourc'h, Hélène Blasco, Cindy Maurel, Philippe Corcia, Anna A. Chami, Rose Anne Thépault
المصدر: Molecular neurobiology. 57(3)
مصطلحات موضوعية: 0301 basic medicine, Cytoplasm, SOD1, Neuroscience (miscellaneous), SUMO protein, medicine.disease_cause, 03 medical and health sciences, Cellular and Molecular Neuroscience, Mice, 0302 clinical medicine, mental disorders, medicine, Animals, Humans, Viability assay, Cellular localization, Motor Neurons, Mutation, Chemistry, Mutagenesis, Amyotrophic Lateral Sclerosis, nutritional and metabolic diseases, Sumoylation, nervous system diseases, Cell biology, DNA-Binding Proteins, 030104 developmental biology, medicine.anatomical_structure, Neurology, Nucleus, 030217 neurology & neurosurgery
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::42fa3fdb1161e10cfd8339775373f49fTest
https://pubmed.ncbi.nlm.nih.gov/31728929Test -
3
المؤلفون: Patrick Vourc'h, Christian R. Andres, Céline Brulard, Cindy Maurel, P. Corcia, Rudolf Hergesheimer, Hélène Blasco, Audrey Dangoumau, Anna A. Chami, Sylviane Marouillat
المصدر: Molecular neurobiology. 55(8)
مصطلحات موضوعية: 0301 basic medicine, Neuroscience (miscellaneous), Excitotoxicity, Protein degradation, medicine.disease_cause, 03 medical and health sciences, Cellular and Molecular Neuroscience, Ubiquitin, medicine, Autophagy, Animals, Humans, Genetic Predisposition to Disease, Amyotrophic lateral sclerosis, biology, Neurodegeneration, Amyotrophic Lateral Sclerosis, medicine.disease, 030104 developmental biology, Proteostasis, Neurology, Proteasome, Nerve Degeneration, Proteolysis, biology.protein, Neuroscience
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::58464605cfd61248ddb327fdab83c2f6Test
https://pubmed.ncbi.nlm.nih.gov/29322304Test -
4
المؤلفون: Lydie Nadal-Desbarats, Hélène Blasco, Patrick Vourc'h, Patrick Emond, Flore Gouel, Audrey Dangoumau, Frédéric Laumonnier, Charlotte Veyrat-Durebex, Christian R. Andres, David Devos, Eric Piver, Philippe Corcia, Paul H. Gordon
المصدر: Molecular neurobiology. 53(10)
مصطلحات موضوعية: 0301 basic medicine, Quality Control, Time Factors, Cell Survival, SOD1, Citric Acid Cycle, Green Fluorescent Proteins, Neuroscience (miscellaneous), Biology, medicine.disease_cause, Models, Biological, Gas Chromatography-Mass Spectrometry, Cell Line, 03 medical and health sciences, Cellular and Molecular Neuroscience, 0302 clinical medicine, Metabolomics, Glutamates, medicine, Humans, Amyotrophic lateral sclerosis, Principal Component Analysis, Superoxide Dismutase, Amyotrophic Lateral Sclerosis, Discriminant Analysis, Reproducibility of Results, Vitamin K 3, medicine.disease, Coculture Techniques, Citric acid cycle, Oxidative Stress, 030104 developmental biology, medicine.anatomical_structure, Neurology, Biochemistry, Cellular model, Reactive Oxygen Species, 030217 neurology & neurosurgery, Intracellular, Oxidative stress, Astrocyte
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::3bc7c394635d1a3098cbd69874a42ebaTest
https://pubmed.ncbi.nlm.nih.gov/26666663Test -
5
المؤلفون: Frédéric Laumonnier, Eric Piver, Patrick Vourc'h, Christian R. Andres, P. H. Gordon, Charlotte Veyrat-Durebex, Hélène Blasco, Audrey Dangoumau, P. Corcia
المصدر: Molecular neurobiology. 49(2)
مصطلحات موضوعية: Cell type, Neuroscience (miscellaneous), Excitotoxicity, Cell Culture Techniques, Disease, Biology, medicine.disease_cause, Cell Line, Cellular and Molecular Neuroscience, medicine, Animals, Humans, Amyotrophic lateral sclerosis, Induced pluripotent stem cell, Neurons, Amyotrophic Lateral Sclerosis, Robustness (evolution), medicine.disease, Pathophysiology, Coculture Techniques, Oxidative Stress, medicine.anatomical_structure, Neurology, Astrocytes, Neuroglia, Neuroscience
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::9a2e1b035f9259b616962cc442ebcbdfTest
https://pubmed.ncbi.nlm.nih.gov/24198229Test