-
1
المؤلفون: Roman Tyshynsky, Shailendra B. Patel, Sithara Raju Ponny, Kirthi Pulakanti, Babu Nageswararao Kanuri, Ranjuna Weerasekera, Kriya S. Patel, Vincent Fong
المصدر: Journal of Lipid Research
Journal of Lipid Research, Vol 62, Iss, Pp 100028-(2021)مصطلحات موضوعية: 0301 basic medicine, DHCR24, 030204 cardiovascular system & hematology, Biochemistry, FDFT1, farnesyl-diphosphate farnesyl transferase 1, chemistry.chemical_compound, LDLR, low density lipoprotein receptor, 0302 clinical medicine, Endocrinology, SREBF1/2, sterol regulatory element binding transcription factor 1/2, Desmosterol, Conditional gene knockout, CYP27A1, CEACAM1, carcinoembryonic antigen-related cell adhesion molecule 1, GEO, Gene Expression Omnibus, MTTP, microsomal triglyceride transfer protein, Sterol homeostasis, dysmorphology, CYP7A1, cytochrome P450 family 7 subfamily A member 1, FAS, fatty acid synthase, animal models, liver-X-receptor, desmosterol, HMGCR, 3-hydroxy-3-methylglutaryl-CoA reductase, NR1H2/3/4, nuclear receptor subfamily 1 group H member 2/3/4, Research Article, medicine.medical_specialty, LIPC, hepatic triacylglycerol lipase, CYP8B1, cytochrome P450 family 8 subfamily B member 1, bile, QD415-436, Biology, Cholesterol 7 alpha-hydroxylase, liver, CD36, cluster of differentiation 36, CYP27A1, cytochrome P450 family 27 subfamily A member 1, Lipid Metabolism, Inborn Errors, DHCR7, 3β-hydroxysterol-Δ7 reductase, 03 medical and health sciences, Internal medicine, DHCR24, 3β-hydroxysterol-Δ24 reductase, medicine, Abnormalities, Multiple, Liver X receptor, 7-DHC, 7-dehydrocholsterol, SCARB1, Scavenger receptor class B member 1, cholesterol, Cell Biology, medicine.disease, SCARB1, Desmosterolosis, lipoproteins, 030104 developmental biology, chemistry, gene expression, LXR, liver X receptor, PCSK9, proprotein convertase subtilisin/kexin type 9
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::07891d6a4a13061ce051312bb0c74109Test
http://europepmc.org/articles/PMC7933790Test -
2
المؤلفون: Steven J. Fliesler, Sriganesh Ramachandra Rao, Sithara Raju Ponny, Ned A. Porter, Shailendra B. Patel, Vincent Fong, Babu Nageswararao Kanuri, Keri A. Tallman
المصدر: Journal of Lipid Research, Vol 62, Iss, Pp 100002-(2021)
Journal of Lipid Researchمصطلحات موضوعية: 0301 basic medicine, LC-MS, liquid chromatography-mass spectrometry, dHLan, 24-dihydrolanosterol, 14d-Zyme, 14-dehydrozymostenol, 7-DHC, 7-dehydrocholesterol, 030204 cardiovascular system & hematology, SREBF1/2, sterol regulatory element binding transcription factor half, PPARA, peroxisome proliferator activated receptor alpha, Biochemistry, LKO, liver-specific knockout, LDLR, low density lipoprotein receptor, 0302 clinical medicine, Endocrinology, CYP27A1, Conditional gene knockout, CEACAM1, carcinoembryonic antigen-related cell adhesion molecule 1, Glucose homeostasis, DMAP, 4-dimethylaminopyridine, FDFT1, Farnesyl-diphosphate farnesyl transferase 1, 7-dehydrocholesterol, GEO, Gene Expression Omnibus, SRM, selected reaction monitoring, PPh3, triphenylphosphine, NR1H2/3/4/5, nuclear receptor subfamily 1 group H member 2/3/4/5, 14d-Zym, 14-dehydrozymosterol, ESI, electrospray ionization, Chol, cholesterol, MTTP, microsomal triglyceride transfer protein, dysmorphology, SCARB1, scavenger receptor class B member 1, CYP7A1, cytochrome P450 family 7 subfamily A member 1, FAS, fatty acid synthase, HMGCR, 3-hydroxy-3-methylglutaryl-CoA reductase, Lan, lanosterol, TPM, transcript per million, 7-DHD, 7-dehydrodesmosterol, Knockout mouse, GTT, glucose tolerance test, IACUC, institutional animal care and use committee, Research Article, medicine.medical_specialty, congenital, hereditary, and neonatal diseases and abnormalities, LIPC, hepatic triacylglycerol lipase, CHCl3, trichloromethane, CYP8B1, cytochrome P450 family 8 subfamily B member 1, Et3N, triethylamine, PPARG, peroxisome proliferator activated receptor gamma, ABCB11, ATP binding cassette subfamily B member 11, QD415-436, Biology, Cholesterol 7 alpha-hydroxylase, CD36, cluster of differentiation 36, CYP27A1, cytochrome P450 family 27 subfamily A member 1, ABCG1/5/8, ATP binding cassette subfamily G member 1/5/8, DHCR7, 3β-hydroxysterol-Δ7 reductase, Des, desmosterol, 03 medical and health sciences, Smith-Lemli-Opitz syndrome, Zyme, zymostenol, Internal medicine, DHCR24, 3β-hydroxysterol-Δ24 reductase, medicine, Lath, lathosterol, Liver X receptor, BHT, 2,6-di-tert-butyl-4-methylphenol, 8-DHC, 8-dehydrocholesterol, ITT, insulin tolerance test, UPLC, ultra performance liquid chromatography, ES, embryonic stem, Zym, zymosterol, Cell Biology, medicine.disease, SCARB1, 030104 developmental biology, Smith–Lemli–Opitz syndrome, ABCA1, ATP binding cassette subfamily A member 1, cholesterol synthesis, DMG, dimethylglycine, DHL, 24-dehydrolathosterol, SLOS, Smith-Lemli-Opitz syndrome, APO, apolipoprotein, LXR, liver X receptor, PCSK9, proprotein convertase subtilisin/kexin type 9
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::628669fe15a4d77e5ef7fd0fbdf15f34Test
http://www.sciencedirect.com/science/article/pii/S0022227520437046Test -
3
المؤلفون: David A. Ford, Chris N. Goulbourne, Thomas Q. de Aguiar Vallim, Ayelet Gonen, Elisa N.D. Palladino, Elizabeth J. Tarling, Angela Cheng, Ryan M. Allen, Tisha Wang, Elinor Lee, David J Merriott, Ángel Baldán, Joan Cheng
المصدر: Journal of Lipid Research, Vol 58, Iss 5, Pp 941-954 (2017)
Journal of lipid research, vol 58, iss 5مصطلحات موضوعية: 0301 basic medicine, Male, Cell, 030204 cardiovascular system & hematology, Medical Biochemistry and Metabolomics, Subfamily G, Biochemistry, Mice, Gene Knockout Techniques, 0302 clinical medicine, Endocrinology, Pulmonary surfactant, Homeostasis, 2.1 Biological and endogenous factors, Aetiology, Research Articles, ATP Binding Cassette Transporter, Subfamily G, Member 1, ATP binding cassette transporter G1, Chemistry, Middle Aged, Cell biology, medicine.anatomical_structure, Respiratory, Female, lipids (amino acids, peptides, and proteins), Pulmonary alveolar proteinosis, Adult, Cell type, Member 1, Biochemistry & Molecular Biology, ATP Binding Cassette Transporter, 1.1 Normal biological development and functioning, pulmonary alveolar proteinosis, Immunoglobulins, QD415-436, lung, 03 medical and health sciences, Rare Diseases, Underpinning research, medicine, Animals, Humans, Secretion, Liver X receptor, phospholipid, Lung, Macrophages, cholesterol, Pulmonary Surfactants, Cell Biology, medicine.disease, 030104 developmental biology, Gene Expression Regulation, A549 Cells, Alveolar Epithelial Cells, Biochemistry and Cell Biology
وصف الملف: application/pdf
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::9dab76f30cba82c5c5d6cc41add4645aTest
http://www.sciencedirect.com/science/article/pii/S002222752033830XTest -
4
المؤلفون: Orla M. Conneely, Rajendra K. Tangirala, Liming Pei, Ajay Chawla, Ayaka Ito, Ronald M. Evans, Lily C. Chao, Peter Tontonoz, Erin Soto, Cynthia Hong
المصدر: Journal of Lipid Research, Vol 54, Iss 3, Pp 806-815 (2013)
Journal of Lipid Researchمصطلحات موضوعية: Male, Nerve growth factor IB, Macrophage polarization, Inflammation, QD415-436, 030204 cardiovascular system & hematology, Biology, Real-Time Polymerase Chain Reaction, Biochemistry, Mice, 03 medical and health sciences, Nur77, 0302 clinical medicine, Endocrinology, Genetic model, Nuclear Receptor Subfamily 4, Group A, Member 1, medicine, Animals, nuclear receptor, Liver X receptor, Research Articles, 030304 developmental biology, Mice, Knockout, 0303 health sciences, Macrophages, Monocyte, Cell Biology, Atherosclerosis, Flow Cytometry, medicine.anatomical_structure, Nuclear receptor, Ly6C, LDL receptor, Immunology, Cancer research, medicine.symptom
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::87271a9b289dfaa742c681262c05764fTest
https://doi.org/10.1194/jlr.m034157Test -
5
المؤلفون: Nancy R. Webb, Maria C. de Beer, Deneys R. van der Westhuyzen, Ailing Ji, Joanne M. Wroblewski, Lei Cai
المصدر: Journal of Lipid Research, Vol 53, Iss 3, Pp 446-455 (2012)
مصطلحات موضوعية: Lipoproteins, Blotting, Western, class B scavenger receptor type 1, QD415-436, Biology, Real-Time Polymerase Chain Reaction, Biochemistry, chemistry.chemical_compound, Basal (phylogenetics), Mice, Endocrinology, Nascent HDL, Cellular cholesterol, polycyclic compounds, hepatocyte, Animals, Humans, Immunoprecipitation, high density lipoprotein formation, Liver X receptor, Research Articles, Cells, Cultured, ATP Binding Cassette Transporter, Subfamily G, Member 1, Mice, Knockout, ATP binding cassette transporter G1, Cholesterol, nutritional and metabolic diseases, Cell Biology, Scavenger Receptors, Class B, Molecular biology, chemistry, ABCG1, ABCA1, biology.protein, Hepatocytes, ATP-Binding Cassette Transporters, lipids (amino acids, peptides, and proteins), Efflux, ATP binding cassette transporter A1, Lipoproteins, HDL, cholesterol efflux, ATP Binding Cassette Transporter 1
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::02f737cd53abd1e4e531bdbcfba5c063Test
http://www.sciencedirect.com/science/article/pii/S0022227520413604Test -
6
المؤلفون: Biao Lu, Peter M. Elias, Debbie Crumrine, Mao-Qiang Man, Elizabeth J. Tarling, Peggy Kim, Peter A. Edwards, Yan J. Jiang, Kenneth R. Feingold
المصدر: Journal of Lipid Research, Vol 51, Iss 11, Pp 3185-3195 (2010)
مصطلحات موضوعية: Keratinocytes, Hydrocarbons, Fluorinated, Peroxisome proliferator-activated receptor, Lamellar granule, Biochemistry, Calcitriol receptor, Gene Knockout Techniques, Mice, Endocrinology, PPAR delta, Research Articles, Barrier function, ATP Binding Cassette Transporter, Subfamily G, Member 1, Liver X Receptors, chemistry.chemical_classification, Sulfonamides, Cell Differentiation, Orphan Nuclear Receptors, Up-Regulation, Cell biology, Sterols, Female, adenosine 5′-triphosphate binding cassette transporter, lipids (amino acids, peptides, and proteins), Peroxisome proliferator-activated receptor delta, liver X receptor, medicine.medical_specialty, Lipoproteins, QD415-436, Biology, Retinoid X receptor, Permeability, Internal medicine, medicine, Animals, Humans, lamellar body, RNA, Messenger, Liver X receptor, Dose-Response Relationship, Drug, peroxisome proliferator-activated receptor, Cell Biology, Retinoic acid receptor, Epidermal Cells, Gene Expression Regulation, chemistry, ATP-Binding Cassette Transporters, Epidermis, barrier function
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::b27161089ff02f006a9412ca6a44c2cdTest
https://doi.org/10.1194/jlr.m006445Test -
7
المؤلفون: Mary Jane Thomassen, Mani S. Kavuru, A Malur, Anna D. Baker, Anagha Malur, Shobha Ghosh, Barbara P. Barna
المصدر: Journal of Lipid Research, Vol 51, Iss 6, Pp 1325-1331 (2010)
مصطلحات موضوعية: medicine.medical_specialty, pulmonary alveolar proteinosis, Lipoproteins, Peroxisome proliferator-activated receptor, QD415-436, Biochemistry, Gene Knockout Techniques, Mice, Surface-Active Agents, Endocrinology, Internal medicine, Macrophages, Alveolar, medicine, Animals, Liver X receptor, Lung, Surfactant homeostasis, ATP Binding Cassette Transporter, Subfamily G, Member 1, Liver X Receptors, chemistry.chemical_classification, biology, Catabolism, Lipid metabolism, Cell Biology, respiratory system, Orphan Nuclear Receptors, medicine.disease, PPAR gamma, peroxisome proliferator-activated receptor-γ, Cholesterol, ABCG1, chemistry, granulocyte-macrophage colony-stimulating factor, Organ Specificity, ABCA1, Immunology, biology.protein, ATP-Binding Cassette Transporters, lipids (amino acids, peptides, and proteins), Lipoproteins, HDL, Pulmonary alveolar proteinosis, Research Article
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::01b73a43bb382467dd5a802ec9c9c463Test
https://doi.org/10.1194/jlr.m001651Test -
8
المؤلفون: Peter A. Edwards, Paul T. Tarr
المصدر: Journal of Lipid Research, Vol 49, Iss 1, Pp 169-182 (2008)
مصطلحات موضوعية: Lipoproteins, Central nervous system, Receptors, Cytoplasmic and Nuclear, ATP Binding Cassette Transporter, Subfamily G, Endosomes, QD415-436, Biology, Biochemistry, Mice, Endocrinology, sterol-regulatory element binding protein 2, medicine, Animals, ATP binding cassette transporters G1 and G4, RNA, Messenger, Liver X receptor, Cellular localization, ATP Binding Cassette Transporter, Subfamily G, Member 1, Liver X Receptors, Neurons, Messenger RNA, Microglia, Brain, Cell Biology, Lipid Metabolism, Orphan Nuclear Receptors, central nervous system, Molecular biology, Sterol regulatory element-binding protein, Cell biology, DNA-Binding Proteins, Mice, Inbred C57BL, Vesicular transport protein, Cholesterol, Endocytic vesicle, medicine.anatomical_structure, Astrocytes, ATP-Binding Cassette Transporters, lipids (amino acids, peptides, and proteins), Sterol Regulatory Element Binding Protein 2, liver X receptor
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::75dd2c0a0359da0a04414e10fc69a728Test
https://doi.org/10.1194/jlr.m700364-jlr200Test -
9
المؤلفون: Alan R. Tall, May Brundert, Nan Wang, Takafumi Senokuchi, Tamara A. Pagler, Laurent Yvan-Charvet, Hongna Li, F. Rinninger
المصدر: Journal of Lipid Research, Vol 49, Iss 1, Pp 107-114 (2008)
مصطلحات موضوعية: medicine.medical_specialty, lecithin:cholesterol acyltransferase, Apolipoprotein B, Lipoproteins, Receptors, Cytoplasmic and Nuclear, macrophage, QD415-436, Transfection, Biochemistry, Cell Line, Phosphatidylcholine-Sterol O-Acyltransferase, Mice, chemistry.chemical_compound, Endocrinology, High-density lipoprotein, scavenger receptor class B type I, Internal medicine, medicine, Animals, Humans, RNA, Small Interfering, Scavenger receptor, Liver X receptor, ATP Binding Cassette Transporter, Subfamily G, Member 1, Liver X Receptors, ATP binding cassette transporter G1, biology, Cholesterol, Cholesterol, HDL, Reverse cholesterol transport, Cell Biology, Scavenger Receptors, Class B, Orphan Nuclear Receptors, Mice, Mutant Strains, DNA-Binding Proteins, Lipoproteins, LDL, chemistry, high density lipoprotein, ABCA1, Macrophages, Peritoneal, biology.protein, ATP-Binding Cassette Transporters, lipids (amino acids, peptides, and proteins), Cholesterol Esters, Efflux, Lipoproteins, HDL, liver X receptor
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::5b465fd308de9a005fb30e115d5eeab6Test
https://doi.org/10.1194/jlr.m700200-jlr200Test -
10
المؤلفون: Heidi Dalrymple, Barbara P. Barna, Mani S. Kavuru, Anagha Malur, A Malur, Tracey L. Bonfield, Mary Jane Thomassen, Maria Febbraio, Carol Farver
المصدر: Journal of Lipid Research, Vol 48, Iss 12, Pp 2762-2768 (2007)
مصطلحات موضوعية: medicine.medical_specialty, Lipoproteins, Receptors, Cytoplasmic and Nuclear, Peroxisome proliferator-activated receptor, QD415-436, Pulmonary Alveolar Proteinosis, Biology, Biochemistry, Mice, Endocrinology, Internal medicine, Macrophages, Alveolar, medicine, Animals, Humans, RNA, Messenger, Liver X receptor, Surfactant homeostasis, ATP Binding Cassette Transporter, Subfamily G, Member 1, Liver X Receptors, Mice, Knockout, ATP binding cassette transporter G1, chemistry.chemical_classification, Mice, Inbred BALB C, peroxisome proliferator-activated receptor γ, Lung, liver X receptor α, Cell Biology, Orphan Nuclear Receptors, medicine.disease, foam cells, DNA-Binding Proteins, PPAR gamma, medicine.anatomical_structure, Granulocyte macrophage colony-stimulating factor, chemistry, granulocyte-macrophage colony-stimulating factor, ABCA1, Knockout mouse, biology.protein, ATP-Binding Cassette Transporters, lipids (amino acids, peptides, and proteins), ATP binding cassette transporter A1, Pulmonary alveolar proteinosis, ATP Binding Cassette Transporter 1, medicine.drug
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::e9a70238dd1789a72f66f67d6d803e95Test
https://doi.org/10.1194/jlr.p700022-jlr200Test