دورية أكاديمية
Anesthesia for a patient of acromesomelic dysplasia with associated hydrocephalus, Arnold Chiari malformation and syringomyelia
| العنوان: | Anesthesia for a patient of acromesomelic dysplasia with associated hydrocephalus, Arnold Chiari malformation and syringomyelia |
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| المؤلفون: | Rudrashish Haldar, Prakhar Gyanesh, Sukhen Samanta |
| المصدر: | Journal of Anaesthesiology Clinical Pharmacology, Vol 29, Iss 4, Pp 555-557 (2013) |
| بيانات النشر: | Wolters Kluwer Medknow Publications, 2013. |
| سنة النشر: | 2013 |
| المجموعة: | LCC:Anesthesiology LCC:Pharmacy and materia medica |
| مصطلحات موضوعية: | Acromesomelic dysplasia, arnold chiari malformation, osteochondrodysplasia, short stature, syringomyelia, Anesthesiology, RD78.3-87.3, Pharmacy and materia medica, RS1-441 |
| الوصف: | Acromesomelic dysplasias are autosomal recessive osteochondrodysplasias. Acromesomelic dysplasia Maroteaux-type (AMDM), also known as St Helena dysplasia, is of two types: The classical and the mild variety. About 50 cases of AMDM have been reported till date, most of them being the classical variety. There is scarcity of literature on anesthesia for such patients. We are reporting a case of general anesthetic management of AMDM, associated with hydrocephalus, Arnold Chiari malformation type-1 and syringomyelia. The patient was a 10-year-old short-statured boy who presented with symptomatic thoracic kyphoscoliosis, gibbus deformity and back pain. On examination, there was no neurological deficit. Radiology revealed thoracic kyphoscoliosis, mild ventriculomegaly and upper cervical syringomyelia. The patient underwent posterior fossa decompression in the prone position under general anesthesia. We will discuss the anesthetic considerations for such patients and review the pertinent literature. |
| نوع الوثيقة: | article |
| وصف الملف: | electronic resource |
| اللغة: | English |
| تدمد: | 0970-9185 |
| العلاقة: | http://www.joacp.org/article.asp?issn=0970-9185;year=2013;volume=29;issue=4;spage=555;epage=557;aulast=HaldarTest; https://doaj.org/toc/0970-9185Test |
| DOI: | 10.4103/0970-9185.119153 |
| الوصول الحر: | https://doaj.org/article/b2315afb36c0446698d95b610f3ae456Test |
| رقم الانضمام: | edsdoj.b2315afb36c0446698d95b610f3ae456 |
| قاعدة البيانات: | Directory of Open Access Journals |
Full Text Finder | تدمد: | 09709185 |
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| DOI: | 10.4103/0970-9185.119153 |