التفاصيل البيبلوغرافية
العنوان: |
Case for diagnosis |
المؤلفون: |
Zanuncio,Virginia Vinha, Carvalho,Luciana Rabelo de, Guedes,Antônio Carlos Martins, Silva,Cláudia Márcia Resende, Gontijo,Bernardo |
المصدر: |
Anais Brasileiros de Dermatologia v.88 n.6 2013 |
بيانات النشر: |
Sociedade Brasileira de Dermatologia |
سنة النشر: |
2013 |
المجموعة: |
SciELO Brazil (Scientific Electronic Library Online) |
مصطلحات موضوعية: |
Histiocytosis, Langerhans-cell, Immunohistochemistry, Prognosis |
الوصف: |
Langerhans cell histiocytosis is a rare, clinically heterogeneous desease. Since there is considerable clinical overlap among the four described variants (Hand-Schüller-Christian, eosinophilic granuloma, Letterer-Siwe and Hashimoto-Pritzker), the concept of spectral disease applies to this entity. The Hashimoto-Pritzker variant was first described in 1973. Characteristically, it is present at birth or during the first days of life, impairment is limited to the skin and prognosis is favorable with spontaneous resolution. We report a newborn male patient with Hashimoto-Pritzker disease presenting as a S100 + and CD1a + single congenital perianal lesion with rapid involution in two months. |
نوع الوثيقة: |
article in journal/newspaper |
وصف الملف: |
text/html |
اللغة: |
English |
الإتاحة: |
http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000601001Test |
رقم الانضمام: |
edsbas.582766CA |
قاعدة البيانات: |
BASE |