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1دورية أكاديمية
المؤلفون: Chen, Chi-Fen, Lin, Hugo, Riley, Daniel, Chen, Yumay, Chen, Phang-Lang
المصدر: International Journal of Molecular Sciences. 25(5)
مصطلحات موضوعية: ADPKD, ATM, CHK1, CHK2, DNA damage repair, PKD1, PKD2, checkpoint, Humans, Polycystic Kidney, Autosomal Dominant, TRPP Cation Channels, Mutation, Kidney, Cysts, Chromosomal Instability
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/1n7732v8Test
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2دورية أكاديمية
المؤلفون: Ng, Leo Ct, Harris, Brandon J, Larmore, Megan, Ta, My C, Vien, Thuy N, Tokars, Valerie L, Yarov-Yarovoy, Vladimir, DeCaen, Paul G
المصدر: EMBO reports. 24(7)
مصطلحات موضوعية: Animals, Humans, Mice, Calcium Channels, Receptors, Cell Surface, Signal Transduction, Ion Transport, Mutation, Transient Receptor Potential Channels, TRPP Cation Channels, TRP channels, calcium, polycystic kidney disease, polycystins, structural biology, Genetics, Kidney Disease, Polycystic Kidney Disease, Underpinning research, Aetiology, 1.1 Normal biological development and functioning, 2.1 Biological and endogenous factors, Biochemistry and Cell Biology, Developmental Biology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/5c83c26rTest
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3دورية أكاديمية
المؤلفون: Akbari, Masaw, West, Jonathan D, Doerr, Nicholas, Kipp, Kevin R, Marhamati, Neda, Vuong, Sabrina, Wang, Yidi, Rinschen, Markus M, Talbot, Jeffrey J, Wessely, Oliver, Weimbs, Thomas
المصدر: Proceedings of the National Academy of Sciences of the United States of America. 119(30)
مصطلحات موضوعية: Biochemistry and Cell Biology, Biomedical and Clinical Sciences, Biological Sciences, Congenital Structural Anomalies, Kidney Disease, Polycystic Kidney Disease, Pediatric, 5.1 Pharmaceuticals, Development of treatments and therapeutic interventions, Renal and urogenital, Animals, Disease Models, Animal, Disease Progression, Enzyme Activation, Fingolimod Hydrochloride, Humans, Mice, Polycystic Kidney, Autosomal Dominant, Protein Kinase C, TRPP Cation Channels, polycystic kidney disease, polycystin-1, protein kinase C ζ
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/0rw4q0ckTest
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4دورية أكاديمية
المؤلفون: Friend, Brian D, Schneider, Kami Wolfe, Garrington, Timothy, Truscott, Laurel, Martinez‐Agosto, Julian A, Venick, Robert S, Chambers, Eileen Tsai, Weng, Patricia, Farmer, Douglas G, Chang, Vivian Y, Federman, Noah
المصدر: Molecular Genetics & Genomic Medicine. 7(7)
مصطلحات موضوعية: Biological Sciences, Medicinal and Biomolecular Chemistry, Chemical Sciences, Genetics, Kidney Disease, Rare Diseases, Clinical Research, Pediatric, Cancer, Polycystic Kidney Disease, Digestive Diseases, Liver Disease, Aetiology, 2.1 Biological and endogenous factors, Renal and urogenital, Adolescent, Child, Female, Genetic Predisposition to Disease, Humans, Infant, Male, Neoplasms, Polycystic Kidney Diseases, Receptors, Cell Surface, TRPP Cation Channels, genetic predisposition, genetic sequencing, malignancy, polycystic kidney disease, Clinical Sciences, Medicinal and biomolecular chemistry
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/36x4x5tvTest
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5دورية أكاديمية
المؤلفون: Trott, Josephine F, Hwang, Vicki J, Ishimaru, Tatsuto, Chmiel, Kenneth J, Zhou, Julie X, Shim, Kyuhwan, Stewart, Benjamin J, Mahjoub, Moe R, Jen, Kuang-Yu, Barupal, Dinesh K, Li, Xiaogang, Weiss, Robert H
المصدر: American Journal of Physiology. Renal physiology. 315(6)
مصطلحات موضوعية: Pediatric, Congenital Structural Anomalies, Kidney Disease, Polycystic Kidney Disease, 2.1 Biological and endogenous factors, Aetiology, Cancer, Animals, Arginine, Argininosuccinate Synthase, Cell Proliferation, Cells, Cultured, Disease Models, Animal, Energy Metabolism, Female, Genetic Predisposition to Disease, Humans, Kidney, Male, Metabolomics, Mice, Knockout, Phenotype, Polycystic Kidney, Autosomal Dominant, Receptors, Cell Surface, Signal Transduction, TRPP Cation Channels, arginine, cystogenesis, metabolic reprogramming, Physiology, Clinical Sciences, Medical Physiology, Urology & Nephrology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/2th4z137Test
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6دورية أكاديمية
المؤلفون: Trott, Josephine F, Hwang, Vicki J, Ishimaru, Tatsuto, Chmiel, Kenneth J, Zhou, Julie X, Shim, Kyuhwan, Stewart, Benjamin J, Mahjoub, Moe R, Jen, Kuang-Yu, Barupal, Dinesh K, Li, Xiaogang, Weiss, Robert H
المصدر: American journal of physiology. Renal physiology. 315(6)
مصطلحات موضوعية: Kidney, Cells, Cultured, Animals, Mice, Knockout, Humans, Polycystic Kidney, Autosomal Dominant, Disease Models, Animal, Genetic Predisposition to Disease, Argininosuccinate Synthase, Arginine, Receptors, Cell Surface, Signal Transduction, Cell Proliferation, Energy Metabolism, Phenotype, Female, Male, TRPP Cation Channels, Metabolomics, arginine, cystogenesis, metabolic reprogramming, Cells, Cultured, Mice, Knockout, Polycystic Kidney, Autosomal Dominant, Disease Models, Animal, Receptors, Cell Surface, Congenital Structural Anomalies, Kidney Disease, Polycystic Kidney Disease, Pediatric, 2.1 Biological and endogenous factors, Cancer, Urology & Nephrology, Physiology, Medical Physiology, Clinical Sciences
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/2th4z137Test
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7دورية أكاديمية
المؤلفون: Hofherr, Alexis, Seger, Claudia, Fitzpatrick, Fiona, Busch, Tilman, Michel, Elisabeth, Luan, Jingting, Osterried, Lea, Linden, Frieder, Kramer-Zucker, Albrecht, Wakimoto, Barbara, Schütze, Conny, Wiedemann, Nils, Artati, Anna, Adamski, Jerzy, Walz, Gerd, Kunji, Edmund RS, Montell, Craig, Watnick, Terry, Köttgen, Michael
المصدر: PLoS biology. 16(8)
مصطلحات موضوعية: Cilia, Animals, Zebrafish, Humans, Drosophila melanogaster, Calcium, Calcium-Binding Proteins, Amino Acid Transport Systems, Acidic, Ion Channels, Calcium Channels, Antiporters, Mitochondrial Membrane Transport Proteins, Mitochondrial Proteins, Signal Transduction, Heterozygote, TRPP Cation Channels, Amino Acid Transport Systems, Acidic, Developmental Biology, Biological Sciences, Agricultural and Veterinary Sciences, Medical and Health Sciences
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/6z58g0w7Test
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8دورية أكاديمية
المؤلفون: Hofherr, Alexis, Seger, Claudia, Fitzpatrick, Fiona, Busch, Tilman, Michel, Elisabeth, Luan, Jingting, Osterried, Lea, Linden, Frieder, Kramer-Zucker, Albrecht, Wakimoto, Barbara, Schütze, Conny, Wiedemann, Nils, Artati, Anna, Adamski, Jerzy, Walz, Gerd, Kunji, Edmund RS, Montell, Craig, Watnick, Terry, Köttgen, Michael
المصدر: PLoS biology. 16(8)
مصطلحات موضوعية: Cilia, Animals, Zebrafish, Humans, Drosophila melanogaster, Calcium, Calcium-Binding Proteins, Amino Acid Transport Systems, Acidic, Ion Channels, Calcium Channels, Antiporters, Mitochondrial Membrane Transport Proteins, Mitochondrial Proteins, Signal Transduction, Heterozygote, TRPP Cation Channels, Genetics, 1.1 Normal biological development and functioning, Underpinning research, Generic health relevance, Biological Sciences, Agricultural and Veterinary Sciences, Medical and Health Sciences, Developmental Biology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/6z58g0w7Test
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9دورية أكاديمية
المؤلفون: Ma, Shenghong, Guan, Kun-Liang
المصدر: Genes & Development. 32(11-12)
مصطلحات موضوعية: Biological Sciences, Biomedical and Clinical Sciences, Genetics, Pediatric, Congenital Structural Anomalies, Polycystic Kidney Disease, Kidney Disease, Aetiology, 2.1 Biological and endogenous factors, Renal and urogenital, Adaptor Proteins, Signal Transducing, Animals, Cell Cycle Proteins, Mice, Mutation, Phosphoproteins, Polycystic Kidney Diseases, Polycystic Kidney, Autosomal Dominant, Signal Transduction, TRPP Cation Channels, YAP-Signaling Proteins, rhoA GTP-Binding Protein, 3D culture, ADPKD, Hippo signaling, RhoA signaling, YAP/TAZ, c-Myc, Medical and Health Sciences, Psychology and Cognitive Sciences, Developmental Biology, Biological sciences, Biomedical and clinical sciences, Psychology
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/8805c3h4Test
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10دورية أكاديمية
المؤلفون: Hofherr, Alexis, Seger, Claudia, Fitzpatrick, Fiona, Busch, Tilman, Michel, Elisabeth, Luan, Jingting, Osterried, Lea, Linden, Frieder, Kramer-Zucker, Albrecht, Wakimoto, Barbara, Schütze, Conny, Wiedemann, Nils, Artati, Anna, Adamski, Jerzy, Walz, Gerd, Kunji, Edmund RS, Montell, Craig, Watnick, Terry, Köttgen, Michael
المصدر: PLOS Biology. 16(8)
مصطلحات موضوعية: Biochemistry and Cell Biology, Biomedical and Clinical Sciences, Biological Sciences, Genetics, Medical Physiology, Underpinning research, 1.1 Normal biological development and functioning, Generic health relevance, Amino Acid Transport Systems, Acidic, Animals, Antiporters, Calcium, Calcium Channels, Calcium-Binding Proteins, Cilia, Drosophila melanogaster, Heterozygote, Humans, Ion Channels, Mitochondrial Membrane Transport Proteins, Mitochondrial Proteins, Signal Transduction, TRPP Cation Channels, Zebrafish, Agricultural and Veterinary Sciences, Medical and Health Sciences, Developmental Biology, Agricultural, veterinary and food sciences, Biological sciences, Biomedical and clinical sciences
وصف الملف: application/pdf
الوصول الحر: https://escholarship.org/uc/item/6pz3c95kTest