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31دورية أكاديمية
المؤلفون: Krämer, Johannes1, Lenders, Malte2, Canaan-Kühl, Sima3, Nordbeck, Peter4, Üçeyler, Nurcan5, Blaschke, Daniela6, Duning, Thomas7, Reiermann, Stefanie2, Stypmann, Jörg8, Brand, Stefan-Martin9
المصدر: Nephrology Dialysis Transplantation. Aug2018, Vol. 33 Issue 8, p1362-1372. 11p. 7 Charts, 3 Graphs.
مصطلحات موضوعية: *ANGIOKERATOMA corporis diffusum, *DRUG efficacy, *THERAPEUTIC use of enzymes, *LYSOSOMAL storage diseases, *MOLECULAR chaperones
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32دورية أكاديمية
المؤلفون: Johnen, Andreas1 (AUTHOR), Pawlowski, Matthias1 (AUTHOR), Duning, Thomas1 (AUTHOR)
المصدر: Orphanet Journal of Rare Diseases. 6/5/2018, Vol. 13 Issue 1, p91-91. 1p.
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33دورية أكاديمية
المؤلفون: Krämer, Julia1 julia.kraemer@ukmuenster.de, Lueg, Gero1, Schiffler, Patrick1, Vrachimis, Alexis2,3, Weckesser, Matthias2, Wenning, Christian2, Pawlowski, Matthias1, Johnen, Andreas1, Teuber, Anja4, Wersching, Heike4, Meuth, Sven G.1, Duning, Thomas1
المصدر: Journal of Alzheimer's Disease. 2018, Vol. 63 Issue 1, p239-253. 15p.
مصطلحات موضوعية: *FRONTOTEMPORAL dementia, *FLUORODEOXYGLUCOSE F18, *DIFFUSION tensor imaging, *POSITRON emission tomography, *NEURODEGENERATION, *PROGNOSIS, *DIAGNOSIS
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34دورية أكاديمية
المؤلفون: Pawlowski, Matthias1, Lueg, Gero1, Gross, Catharina C.1, Johnen, Andreas1, Krämer, Julia1, Weckesser, Matthias2, Wiendl, Heinz1, Meuth, Sven G.1, Duning, Thomas1 Thomas.Duning@ukmuenster.de
المصدر: Neurobiology of Aging. Feb2018, Vol. 62, p45-52. 8p.
مصطلحات موضوعية: *FRONTOTEMPORAL dementia, *CEREBROSPINAL fluid, *IMMUNE system, *NEUROPSYCHOLOGY, *FLOW cytometry, *PATIENTS
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35دورية أكاديمية
المؤلفون: Heidbreder, Anna1,2, Spießhöfer, Jens1,2,3 jens.spiesshoefer@gmail.com, Stypmann, Jörg4, Boentert, Matthias1,2, Young, Peter1,2, Duning, Thomas1
المصدر: Respiratory Physiology & Neurobiology. Jan2018, Vol. 247, p181-187. 7p.
مصطلحات موضوعية: *TISSUE wounds, *SLEEP apnea syndromes, *CHEYNE-Stokes respiration, *NEUROPLASTICITY, *HEART failure patients, *CONTINUOUS positive airway pressure, *MAGNETIC resonance imaging, *BRAIN stem
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36دورية أكاديمية
المؤلفون: Lenders, Malte1, Schmitz, Boris2, Stypmann, Jörg3, Duning, Thomas4, Brand, Stefan-Martin2, Kurschat, Christine5, Brand, Eva1
المصدر: Nephrology Dialysis Transplantation. Dec2017, Vol. 32 Issue 12, p2090-2097. 8p. 1 Diagram, 3 Charts, 3 Graphs.
مصطلحات موضوعية: *KIDNEY function tests, *ANGIOKERATOMA corporis diffusum, *THERAPEUTIC use of enzymes, *DISEASE progression, *GLOMERULAR filtration rate, *LEFT ventricular hypertrophy, *PATIENTS
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37دورية أكاديمية
المؤلفون: Reul, Sophia1 sophiareul@uni-muenster.de, Lohmann, Hubertus1, Wiendl, Heinz1, Duning, Thomas1, Johnen, Andreas1
المصدر: Alzheimer's Research & Therapy. 8/9/2017, Vol. 9, p1-12. 12p.
مصطلحات موضوعية: *ALZHEIMER'S disease diagnosis, *FRONTOTEMPORAL dementia, *DAS-Naglieri Cognitive Assessment System, *NEUROPSYCHOLOGICAL tests, *SOCIAL perception, *DIAGNOSIS
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38دورية أكاديمية
المؤلفون: Reul, Sophia1 Sophia.Reul@ukmuenster.de, Johnen, Andreas1, Duning, Thomas2, Lohmann, Hubertus1
المصدر: Zeitschrift für Neuropsychologie. 2015, Vol. 26 Issue 3, p197-198. 2p.
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39دورية أكاديمية
المؤلفون: Hendriksz, Christian J.1,2, Anheim, Mathieu3, Bauer, Peter4,5, Bonnot, Olivier6, Chakrapani, Anupam7, Corvol, Jean-Christophe8, De Koning, Tom J.9, Degtyareva, Anna10, Dionisi-Vici, Carlo11, Doss, Sarah12, Duning, Thomas13, Giunti, Paola14, Iodice, Rosa15, Johnston, Tracy16, Kelly, Dierdre17, Klünemann, Hans-Hermann18, Lorenzl, Stefan19,20, Padovani, Alessandro21, Pocovi, Miguel22, Synofzik, Matthis23,24
المصدر: Current Medical Research & Opinion. May2017, Vol. 33 Issue 5, p877-890. 14p.
مصطلحات موضوعية: *NIEMANN-Pick diseases, *INBORN errors of metabolism, *PATIENTS, *SYMPTOMS, *DISEASE prevalence
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40دورية أكاديمية
المؤلفون: Lenders, Malte1, Stypmann, Jörg1, Duning, Thomas1, Schmitz, Boris1, Brand, Stefan-Martin1, Brand, Eva1
المصدر: Molecular Genetics & Metabolism. Feb2016, Vol. 117 Issue 2, pS73-S73. 1p.
مصطلحات موضوعية: *IMMUNOGLOBULINS, *THERAPEUTIC use of enzymes, *FARBER disease, *KIDNEY diseases, *MEDICAL research