المؤلفون: Arora, A, Raffaele, A, Agarwala, S, Parigi, G B, Manzoni, F, Klersy, C, Bhatnagar, V

المساهمون: Arora, A, Raffaele, A, Agarwala, S, Parigi, G B, Manzoni, F, Klersy, C, Bhatnagar, V

مصطلحات موضوعية: esophageal atresia, congenital malformations

الوصف: Background The aim is to evaluate if different social reality could represent a prognostic factor as associated anomalies affecting survival of neonates with esophageal atresia (EA). Method Retrospective analysis of records of neonates with EA with or without Tracheoesophageal Fistula (TEF) from January 2011 to September 2018 at Policlinico San Matteo Pavia, Italy(SMAT) and the All India Institute of Medical Sciences New Delhi, India (AIIMS).Survival was correlated with the presence of anomalies, different types and the number of organ systems involved.Age at presentation and birth weight were considered to find an association with mortality. Results Out of 180 patients,162 were from AIIMS and 18 from SMAT.The overall mortality was 28.85%, which occurred at AIIMS, being 0% at SMAT.83.33% at SMAT and 72.84% at AIIMS had associated anomalies.The mortality was 25% for neonates without an anomaly, being 26.15% for those with one (p > 0.05).No statistically significant correlation between outcome and associated anomalies was found.Instead, survival declines gradually as the age at presentation increases. Conclusions The presence of associated anomalies paradoxically does not affect the outcome because incidence of delayed presentation has a stronger effect than the presence of associated anomalies. Sensibilization is necessary to improve survival in EA neonates in developing countries, such as India.

وصف الملف: STAMPA

العلاقة: volume:108; issue:Supplement_6; journal:BRITISH JOURNAL OF SURGERY; https://hdl.handle.net/11571/1495057Test

الإتاحة: https://doi.org/10.1093/bjs/znab259.684Test
https://hdl.handle.net/11571/1495057Test

المؤلفون: BIANCHI, PAOLO EMILIO, C. Barone, A. M. Bezzina, M. Schmid, R. Salati

المساهمون: Bianchi, PAOLO EMILIO, C., Barone, A. M., Bezzina, M., Schmid, R., Salati

مصطلحات موضوعية: Duane's Syndrome, Malformative syndrome, Congenital malformations

الوصف: Duane's retraction syndrome is sometimes associated with developmental ocular and extraocular abnormalities. This disorder may also be present in association with specific malformative syndromes. The authors report the clinical features of a seven-year-old female affected by Duane's retraction syndrome (D.R.S.), rectoperineal fistula, imperforate anus and other congenital malformations. From two extensive reviews of 106 reports published before 1982 and from a search (using Medline 1981-1994) for reports of congenital malformations associated with this syndrome, no cases of sporadic D.R.S. associated with the perineal malformations mentioned were found, even though imperforate anus is considered the commoner of hindgut malformation.

وصف الملف: STAMPA

العلاقة: info:eu-repo/semantics/altIdentifier/pmid/21314383; volume:3; firstpage:123; lastpage:126; numberofpages:3; journal:STRABISMUS; http://hdl.handle.net/11571/241503Test; http://dx.doi.org/10.3109/09273979509087726Test

الإتاحة: https://doi.org/10.3109/09273979509087726Test
http://hdl.handle.net/11571/241503Test