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المؤلفون: Fengyin Liang, Shichang Li, Jean-Marc Burgunder, Guangqing Xu, Qinmei Wang, Yixuan Zeng, Xi-Lin Lu, Wenyuan Guo, Zhong Pei, Jie-Bin Zhou, Ji-Yan Pang, Yi Huang, Simei Long, Luyang Feng
المصدر: Drug Design, Development and Therapy
مصطلحات موضوعية: 0301 basic medicine, congenital, hereditary, and neonatal diseases and abnormalities, Huntingtin, Mutant, Pharmaceutical Science, Protein aggregation, Neuroprotection, molecular target, Small Molecule Libraries, xyloketal derivatives, 03 medical and health sciences, Protein Aggregates, Huntington's disease, mutant Huntingtin, Drug Discovery, mental disorders, medicine, Huntingtin Protein, Animals, protein misfolding, Caenorhabditis elegans, Pyrans, Original Research, Pharmacology, Genetics, Drug Design, Development and Therapy, biology, Chorea, biology.organism_classification, medicine.disease, Cell biology, nervous system diseases, Molecular Docking Simulation, Disease Models, Animal, 030104 developmental biology, Huntington Disease, Neuroprotective Agents, medicine.symptom, Huntington’s disease
وصف الملف: text/html
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::dc8fcea67e2258c9d419944fe7fc01e0Test
https://pubmed.ncbi.nlm.nih.gov/27110099Test -
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المؤلفون: Jean-Marc Burgunder, Walter Hunziker
المصدر: IUBMB Life (International Union of Biochemistry and Molecular Biology: Life). 55:347-352
مصطلحات موضوعية: Atlastin, Spastin, Hereditary spastic paraplegia, Proteolipids, Clinical Biochemistry, Kinesins, Cell Cycle Proteins, Degeneration (medical), Biochemistry, GTP Phosphohydrolases, GTP-Binding Proteins, Genetics, medicine, Humans, Spasticity, Molecular Biology, Adenosine Triphosphatases, Spastic Paraplegia, Hereditary, Gait Disturbance, business.industry, Calcium-Binding Proteins, Membrane Proteins, Proteins, Chaperonin 60, Cell Biology, medicine.disease, nervous system diseases, Membrane protein, Corticospinal tract, medicine.symptom, Hereditary Sensory and Motor Neuropathy, business, Neuroscience
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::561f8e03c7635c57160d33384192a9e4Test
https://doi.org/10.1080/1521654032000114311Test -
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المؤلفون: Jean-Marc Burgunder, How-Lung Eng, Wei Cheng, Jing Tian, Walter Hunziker
المصدر: PLoS ONE, Vol 9, Iss 8, p e103445 (2014)
PLoS ONEمصطلحات موضوعية: Movement disorders, Gene Expression, lcsh:Medicine, medicine.disease_cause, Biochemistry, Ion Channels, Animals, Genetically Modified, Gene Order, Medicine and Health Sciences, lcsh:Science, Zebrafish, Musculoskeletal System, Genetics, Mutation, Multidisciplinary, Movement Disorders, biology, Muscles, Fishes, Neurodegenerative Diseases, Animal Models, Phenotype, Cell biology, Biomechanical Phenomena, Neurology, Osteichthyes, Vertebrates, medicine.symptom, Anatomy, Locomotion, Research Article, musculoskeletal diseases, Myotonia Congenita, Recombinant Fusion Proteins, Genetic Vectors, Muscle disorder, Research and Analysis Methods, Muscle Fibers, Model Organisms, Chloride Channels, medicine, Animals, Humans, Actin, Swimming, CLCN1, Myotonia congenita, lcsh:R, Organisms, Biology and Life Sciences, Proteins, biology.organism_classification, medicine.disease, Actins, Disease Models, Animal, biology.protein, lcsh:Q
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::e9e0505057d2bc6319fc228eb055a6c7Test
http://europepmc.org/articles/PMC4118878?pdf=renderTest -
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المؤلفون: Jean-Marc Burgunder
المصدر: IUBMB life. 55(6)
مصطلحات موضوعية: Cysteine Endopeptidases, Proteasome Endopeptidase Complex, Multienzyme Complexes, Clinical Biochemistry, Nerve Degeneration, Genetics, Disease Progression, Humans, Neurodegenerative Diseases, Cell Biology, Molecular Biology, Biochemistry
الوصول الحر: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::57167d1fe378260aaf4e07f3653b4183Test
https://pubmed.ncbi.nlm.nih.gov/12938729Test